日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Altered transition metal homeostasis in Niemann-Pick disease, type C1

尼曼-匹克病C1型中过渡金属稳态的改变

Hung, Ya Hui; Faux, Noel G; Killilea, David W; Yanjanin, Nicole; Firnkes, Sally; Volitakis, Irene; Ganio, George; Walterfang, Mark; Hastings, Caroline; Porter, Forbes D; Ory, Daniel S; Bush, Ashley I

Efficacy of N-acetylcysteine in phenotypic suppression of mouse models of Niemann-Pick disease, type C1.

N-乙酰半胱氨酸对尼曼-匹克病 C1 型小鼠模型表型抑制的功效

Fu Rao, Wassif Christopher A, Yanjanin Nicole M, Watkins-Chow Dawn E, Baxter Laura L, Incao Art, Liscum Laura, Sidhu Rohini, Firnkes Sally, Graham Mark, Ory Daniel S, Porter Forbes D, Pavan William J

PROCEEDINGS OF THE PHYSIOLOGICAL SOCIETY: December 12, 1914

生理学会会刊:1914年12月12日

Frankel, Adam; Xu, Miao; Liu, Ke; Swaroop, Manju; Porter, Forbes D; Sidhu, Rohini; Firnkes, Sally; Ory, Daniel S; Marugan, Juan J; Xiao, Jingbo; Southall, Noel; Pavan, William J; Davidson, Cristin; Walkley, Steven U; Remaley, Alan T; Baxa, Ulrich; Sun, Wei; McKew, John C; Austin, Christopher P; Zheng, Wei; Jones, Christopher G; Moniodis, Jessie; Zulak, Katherine G; Scaffidi, Adrian; Plummer, Julie A; Ghisalberti, Emilio L; Barbour, Elizabeth L; Bohlmann, Jörg; Barker, Kylie D; Barkovits, Katalin; Wilks, Angela; Loseva, Olga; Jemth, Ann-Sofie; Bryant, Helen E; Schüler, Herwig; Lehtiö, Lari; Karlberg, Tobias; Helleday, Thomas; Frias, Janice A; Richman, Jack E; Erickson, Jasmine S; Wackett, Lawrence P; Ye, Bin; Zhang, Xiao; Shephard, Freya; Kim, Hong B; Palmer, Ian R; McHarg, Selina; Fowler, Gregory J S; O'Neill, Luke A J; Kiss-Toth, Endre; Qwarnstrom, Eva E; Berlin, Nathaniel I