日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Taperin bundles F-actin at stereocilia pivot points enabling optimal lifelong mechanosensitivity.

Taperin 将 F-肌动蛋白束固定在立体纤毛的枢轴点,从而实现最佳的终生机械敏感性

Belyantseva Inna A, Liu Chang, Dragich Abigail K, Miyoshi Takushi, Inagaki Sayaka, Imtiaz Ayesha, Tona Risa, Zuluaga-Osorio Karen Sofia, Hadi Shadan, Wilson Elizabeth, Morozko Eva, Olszewski Rafal, Yousaf Rizwan, Sokolova Yuliya, Riordan Gavin P, Aston S Andrew, Rehman Atteeq U, Fenollar Ferrer Cristina, Wisniewski Jan, Gu Shoujun, Nayak Gowri, Goodyear Richard J, Li Jinan, Krey Jocelyn F, Wafa Talah, Faridi Rabia, Adadey Samuel Mawuli, Drummond Meghan, Perrin Benjamin, Winkler Dennis C, Starost Matthew F, Cheng Hui, Fitzgerald Tracy, Richardson Guy P, Dong Lijin, Barr-Gillespie Peter G, Hoa Michael, Frolenkov Gregory I, Friedman Thomas B, Zhao Bo

Gene Therapy Restores Balance and Auditory Functions in a Mouse Model of Usher Syndrome

基因疗法恢复了 Usher 综合征小鼠模型的平衡和听觉功能

Isgrig, Kevin; Shteamer, Jack W; Belyantseva, Inna A; Drummond, Meghan C; Fitzgerald, Tracy S; Vijayakumar, Sarath; Jones, Sherri M; Griffith, Andrew J; Friedman, Thomas B; Cunningham, Lisa L; Chien, Wade W

Ototoxicity and Platinum Uptake Following Cyclic Administration of Platinum-Based Chemotherapeutic Agents

铂类化疗药物周期性给药后的耳毒性和铂吸收

Gersten, Benjamin K; Fitzgerald, Tracy S; Fernandez, Katharine A; Cunningham, Lisa L

Tmc2 expression partially restores auditory function in a mouse model of DFNB7/B11 deafness caused by loss of Tmc1 function

在由Tmc1功能丧失引起的DFNB7/B11耳聋小鼠模型中,Tmc2表达可部分恢复听觉功能。

Nakanishi, Hiroshi; Kurima, Kiyoto; Pan, Bifeng; Wangemann, Philine; Fitzgerald, Tracy S; Géléoc, Gwenaëlle S; Holt, Jeffrey R; Griffith, Andrew J

Gene Therapy Restores Hair Cell Stereocilia Morphology in Inner Ears of Deaf Whirler Mice

基因疗法恢复了聋小鼠内耳毛细胞纤毛形态

Chien, Wade W; Isgrig, Kevin; Roy, Soumen; Belyantseva, Inna A; Drummond, Meghan C; May, Lindsey A; Fitzgerald, Tracy S; Friedman, Thomas B; Cunningham, Lisa L

ILDR1 null mice, a model of human deafness DFNB42, show structural aberrations of tricellular tight junctions and degeneration of auditory hair cells

ILDR1基因敲除小鼠是人类耳聋DFNB42的模型,其三细胞紧密连接的结构异常以及听觉毛细胞的退化是其特征。

Morozko, Eva L; Nishio, Ayako; Ingham, Neil J; Chandra, Rashmi; Fitzgerald, Tracy; Martelletti, Elisa; Borck, Guntram; Wilson, Elizabeth; Riordan, Gavin P; Wangemann, Philine; Forge, Andrew; Steel, Karen P; Liddle, Rodger A; Friedman, Thomas B; Belyantseva, Inna A

Sound preconditioning therapy inhibits ototoxic hearing loss in mice

声音预处理疗法可抑制小鼠的耳毒性听力损失

Airoldi, Irma; Di Carlo, Emma; Banelli, Barbara; Moserle, Lidia; Cocco, Claudia; Pezzolo, Annalisa; Sorrentino, Carlo; Rossi, Edoardo; Romani, Massimo; Amadori, Alberto; Pistoia, Vito; González-Terán, Bárbara; Cortés, José R; Manieri, Elisa; Matesanz, Nuria; Verdugo, Ángeles; Rodríguez, María E; González-Rodríguez, Águeda; Valverde, Ángela M; Martín, Pilar; Davis, Roger J; Sabio, Guadalupe; Ory, Benjamin; Ramsey, Matthew R; Wilson, Catherine; Vadysirisack, Douangsone D; Forster, Nicole; Rocco, James W; Rothenberg, S Michael; Ellisen, Leif W; Roy, Soumen; Ryals, Matthew M; Van den Bruele, Astrid Botty; Fitzgerald, Tracy S; Cunningham, Lisa L