Polyglutamine expansion affects huntingtin conformation in multiple Huntington's disease models
多聚谷氨酰胺扩增影响多种亨廷顿病模型中的亨廷顿蛋白构象
期刊:Scientific Reports
影响因子:3.9
doi:10.1038/s41598-017-05336-7
Daldin, Manuel; Fodale, Valentina; Cariulo, Cristina; Azzollini, Lucia; Verani, Margherita; Martufi, Paola; Spiezia, Maria Carolina; Deguire, Sean M; Cherubini, Marta; Macdonald, Douglas; Weiss, Andreas; Bresciani, Alberto; Vonsattel, Jean-Paul Gerard; Petricca, Lara; Marsh, J Lawrence; Gines, Silvia; Santimone, Iolanda; Marano, Massimo; Lashuel, Hilal A; Squitieri, Ferdinando; Caricasole, Andrea