日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Human-induced pluripotent stem cell-based hepatic modeling of lipid metabolism-associated TM6SF2-E167K variant

基于人诱导多能干细胞的脂质代谢相关TM6SF2-E167K变体肝脏模型

Faccioli, Lanuza A P; Sun, Yiyue; Animasahun, Olamide; Motomura, Takashi; Liu, Zhenghao; Kurihara, Takeshi; Hu, Zhiping; Yang, Bo; Cetin, Zeliha; Baratta, Annalisa M; Shankaran, Ajay; Nenwani, Minal; Altay, Leyla Nurcihan; Huang, Linqi; Meurs, Noah; Franks, Jonathan; Stolz, Donna; Gavlock, Dillon C; Miedel, Mark T; Ostrowska, Alina; Florentino, Rodrigo M; Fox, Ira J; Nagrath, Deepak; Soto-Gutierrez, Alejandro

PNPLA3-I148M genetic variant rewires lipid metabolism to drive programmed cell death in human hepatocytes

PNPLA3-I148M基因变异重塑脂质代谢,从而驱动人类肝细胞程序性细胞死亡

Florentino, Rodrigo M; Animasahun, Olamide; Haep, Nils; Nenwani, Minal; Omoloja, Kehinde; Altay, Leyla Nurcihan; Achreja, Abhinav; Morita, Kazutoyo; Motomura, Takashi; Diaz-Aragon, Ricardo; Faccioli, Lanuza Ap; Sun, Yiyue; Liu, Zhenghao; Hu, Zhiping; Yang, Bo; Wuchu, Fulei; Shankaran, Ajay; Paserba, Miya; Baratta, Annalisa M; Arazov, Shohrat; Kocas-Kilicarslan, Zehra N; Meurs, Noah; Behari, Jaideep; Tafaleng, Edgar N; Franks, Jonathan; Ostrowska, Alina; Tomiyama, Takahiro; Yugawa, Kyohei; Morinaga, Akinari; Wang, Zi; Takeishi, Kazuki; Gavlock, Dillon C; Miedel, Mark; Taylor, D Lansing; Fox, Ira J; Yoshizumi, Tomoharu; Nagrath, Deepak; Soto-Gutierrez, Alejandro

Variants in autophagy genes MTMR12 and FAM134A are putative modifiers of the hepatic phenotype in α1-antitrypsin deficiency

自噬基因MTMR12和FAM134A的变异可能是α1-抗胰蛋白酶缺乏症肝脏表型的潜在修饰因子。

Tafaleng, Edgar N; Li, Jie; Wang, Yan; Hidvegi, Tunda; Soto-Gutierrez, Alex; Locke, Adam E; Nicholas, Thomas J; Wang, Yung-Chun; Pak, Stephen; Cho, Michael H; Silverman, Edwin K; Silverman, Gary A; Jin, Sheng Chih; Fox, Ira J; Perlmutter, David H

Mechanism and Effect of HNF4α Decrease in a Rat Model of Cirrhosis and Liver Failure

HNF4α 降低在肝硬化和肝衰竭大鼠模型中的机制和影响

Melis, Marta; Marino, Rebecca; Tian, Jianmin; Johnson, Carla; Sethi, Rahil; Oertel, Michael; Fox, Ira J; Locker, Joseph

Resolution of hepatic fibrosis after ZFN-mediated gene editing in the PiZ mouse model of human α1-antitrypsin deficiency

在PiZ小鼠模型(人类α1-抗胰蛋白酶缺乏症)中,ZFN介导的基因编辑可缓解肝纤维化。

Li, Yanfeng; Guha, Chandan; Asp, Patrik; Wang, Xia; Tchaikovskya, Tatyana L; Kim, Kenneth; Mendel, Matthew; Cost, Gregory J; Perlmutter, David H; Roy-Chowdhury, Namita; Fox, Ira J; Conway, Anthony; Roy-Chowdhury, Jayanta

A non-human primate model of acute liver failure suitable for testing liver support systems

适用于测试肝脏支持系统的非人灵长类动物急性肝衰竭模型

Kalsi, Ranjeet S; Ostrowska, Alina; Olson, Adam; Quader, Mubina; Deutsch, Melvin; Arbujas-Silva, Norma J; Symmonds, Jen; Soto-Gutierrez, Alejandro; Crowley, John J; Reyes-Mugica, Miguel; Sanchez-Guerrero, Giselle; Jaeschke, Hartmut; Amiot, Bruce P; Cascalho, Marilia; Nyberg, Scott L; Platt, Jeffrey L; Tafaleng, Edgar N; Fox, Ira J

Synthetic human livers for modeling metabolic diseases

用于模拟代谢疾病的合成人肝

Tafaleng, Edgar N; Malizio, Michelle R; Fox, Ira J; Soto-Gutierrez, Alejandro

Host conditioning and rejection monitoring in hepatocyte transplantation in humans

人类肝细胞移植中的宿主预处理和排斥反应监测

Soltys, Kyle A; Setoyama, Kentaro; Tafaleng, Edgar N; Soto Gutiérrez, Alejandro; Fong, Jason; Fukumitsu, Ken; Nishikawa, Taichiro; Nagaya, Masaki; Sada, Rachel; Haberman, Kimberly; Gramignoli, Roberto; Dorko, Kenneth; Tahan, Veysel; Dreyzin, Alexandra; Baskin, Kevin; Crowley, John J; Quader, Mubina A; Deutsch, Melvin; Ashokkumar, Chethan; Shneider, Benjamin L; Squires, Robert H; Ranganathan, Sarangarajan; Reyes-Mugica, Miguel; Dobrowolski, Steven F; Mazariegos, George; Elango, Rajavel; Stolz, Donna B; Strom, Stephen C; Vockley, Gerard; Roy-Chowdhury, Jayanta; Cascalho, Marilia; Guha, Chandan; Sindhi, Rakesh; Platt, Jeffrey L; Fox, Ira J

Clinical Hepatocyte Transplantation: What Is Next?

临床肝细胞移植:下一步是什么?

Squires, James E; Soltys, Kyle A; McKiernan, Patrick; Squires, Robert H; Strom, Stephen C; Fox, Ira J; Soto-Gutierrez, Alejandro

Induced pluripotent stem cells model personalized variations in liver disease resulting from α1-antitrypsin deficiency

诱导多能干细胞模型模拟由α1-抗胰蛋白酶缺乏引起的肝脏疾病的个体化变异

Tafaleng, Edgar N; Chakraborty, Souvik; Han, Bing; Hale, Pamela; Wu, Wanquan; Soto-Gutierrez, Alejandro; Feghali-Bostwick, Carol A; Wilson, Andrew A; Kotton, Darrell N; Nagaya, Masaki; Strom, Stephen C; Roy-Chowdhury, Jayanta; Stolz, Donna B; Perlmutter, David H; Fox, Ira J