日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

A High-Calorie Diet Aggravates Mitochondrial Dysfunction and Triggers Severe Liver Damage in Wilson Disease Rats

高热量饮食会加重威尔逊病大鼠的线粒体功能障碍并引发严重的肝损伤

Claudia Einer, Christin Leitzinger, Josef Lichtmannegger, Carola Eberhagen, Tamara Rieder, Sabine Borchard, Ralf Wimmer, Gerald Denk, Bastian Popper, Frauke Neff, Elena V Polishchuk, Roman S Polishchuk, Stefanie M Hauck, Christine von Toerne, Jennifer-Christin Müller, Uwe Karst, Bipin S Baral, Alan

Low catalytic activity is insufficient to induce disease pathology in triosephosphate isomerase deficiency

低催化活性不足以诱发磷酸三糖异构酶缺乏症的疾病病理

Joanna Segal, Michael Mülleder, Antje Krüger, Thure Adler, Manuela Scholze-Wittler, Lore Becker, Julia Calzada-Wack, Lillian Garrett, Sabine M Hölter, Birgit Rathkolb, Jan Rozman, Ildiko Racz, Ralf Fischer, Dirk H Busch, Frauke Neff, Martin Klingenspor, Thomas Klopstock, Nana-Maria Grüning, Steve Mi

The heterozygous R155C VCP mutation: Toxic in humans! Harmless in mice?

杂合 R155C VCP 突变:对人类有毒!对小鼠无害?

Christoph S Clemen, Lilli Winter, Karl-Heinz Strucksberg, Carolin Berwanger, Matthias Türk, Cornelia Kornblum, Alexandra Florin, Juan Antonio Aguilar-Pimentel, Oana Veronica Amarie, Lore Becker, Lillian Garrett, Wolfgang Hans, Kristin Moreth, Frauke Neff, Laura Pingen, Birgit Rathkolb, Ildikó Rácz, 

Lifetime study in mice after acute low-dose ionizing radiation: a multifactorial study with special focus on cataract risk

小鼠急性低剂量电离辐射后的终生研究:一项特别关注白内障风险的多因素研究

Claudia Dalke, Frauke Neff, Savneet Kaur Bains, Scott Bright, Deborah Lord, Peter Reitmeir, Ute Rößler, Daniel Samaga, Kristian Unger, Herbert Braselmann, Florian Wagner, Matthias Greiter, Maria Gomolka, Sabine Hornhardt, Sarah Kunze, Stefan J Kempf, Lillian Garrett, Sabine M Hölter, Wolfgang Wurst,

Epigenetic alterations in longevity regulators, reduced life span, and exacerbated aging-related pathology in old father offspring mice

长寿调节剂的表观遗传改变,导致老年父亲后代小鼠寿命缩短和衰老相关病理加剧

Kan Xie, Devon P Ryan, Brandon L Pearson, Kristin S Henzel, Frauke Neff, Ramon O Vidal, Magali Hennion, Isabelle Lehmann, Melvin Schleif, Susanne Schröder, Thure Adler, Birgit Rathkolb, Jan Rozman, Anna-Lena Schütz, Cornelia Prehn, Michel E Mickael, Marco Weiergräber, Jerzy Adamski, Dirk H Busch, Ge

Standardized, systemic phenotypic analysis reveals kidney dysfunction as main alteration of Kctd1 I27N mutant mice

标准化系统表型分析表明,肾功能障碍是 Kctd1 I27N 突变小鼠的主要改变

Sudhir Kumar, Birgit Rathkolb, Sibylle Sabrautzki, Stefan Krebs, Elisabeth Kemter, Lore Becker, Johannes Beckers, Raffi Bekeredjian, Robert Brommage, Julia Calzada-Wack, Lillian Garrett, Sabine M Hölter, Marion Horsch, Martin Klingenspor, Thomas Klopstock, Kristin Moreth, Frauke Neff, Jan Rozman, He

Bezafibrate ameliorates diabetes via reduced steatosis and improved hepatic insulin sensitivity in diabetic TallyHo mice

贝扎纤维酸可通过减少脂肪变性和改善糖尿病 TallyHo 小鼠的肝脏胰岛素敏感性来改善糖尿病

Andras Franko, Susanne Neschen, Jan Rozman, Birgit Rathkolb, Michaela Aichler, Annette Feuchtinger, Laura Brachthäuser, Frauke Neff, Marketa Kovarova, Eckhard Wolf, Helmut Fuchs, Hans-Ulrich Häring, Andreas Peter, Martin Hrabě de Angelis0

The endochondral bone protein CHM1 sustains an undifferentiated, invasive phenotype, promoting lung metastasis in Ewing sarcoma

软骨内骨蛋白CHM1维持未分化、侵袭性表型,促进尤文氏肉瘤的肺转移。

Kristina von Heyking,Julia Calzada-Wack,Stefanie Göllner,Frauke Neff,Oxana Schmidt,Tim Hensel,David Schirmer,Annette Fasan,Irene Esposito,Carsten Müller-Tidow,Poul H Sorensen,Stefan Burdach,Günther H S Richter

Extensive phenotypic characterization of a new transgenic mouse reveals pleiotropic perturbations in physiology due to mesenchymal hGH minigene expression

对一种新型转基因小鼠进行广泛的表型表征,揭示了间充质hGH微基因表达引起的生理多效性扰动。

Aimilios Kaklamanos ,Jan Rozman ,Manolis Roulis ,Niki Karagianni ,Maria Armaka ,Moya Wu ,Laura Brachthäuser ,Julia Calzada-Wack ,Marion Horsch ,Johannes Beckers ,Birgit Rathkolb ,Thure Adler ,Frauke Neff ,Eckhard Wolf ,Valerie Gailus-Durner ,Helmut Fuchs ,Martin Hrabe de Angelis ,George Kollias

Chemical Hybridization of Glucagon and Thyroid Hormone Optimizes Therapeutic Impact for Metabolic Disease

胰高血糖素和甲状腺激素的化学杂交优化了代谢疾病的治疗效果

Brian Finan, Christoffer Clemmensen, Zhimeng Zhu, Kerstin Stemmer, Karine Gauthier, Luisa Müller, Meri De Angelis, Kristin Moreth, Frauke Neff, Diego Perez-Tilve, Katrin Fischer, Dominik Lutter, Miguel A Sánchez-Garrido, Peng Liu, Jan Tuckermann, Mohsen Malehmir, Marc E Healy, Achim Weber, Mathias H