日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Complex II assembly drives metabolic adaptation to OXPHOS dysfunction.

复合物 II 的组装驱动代谢适应氧化磷酸化功能障碍

Kugapreethan Roopasingam, Elahee Doomun Sheik Nadeem, Sacharz Joanna, Frazier Ann E, Sharma Tanavi, Low Yau Chung, Nie Shuai, Leeming Michael G, Muellner-Wong Linden, Last Karena, Stait Tegan, De Souza David P, Thorburn David R, McConville Malcolm J, Stroud David A

Atf3 controls transitioning in female mitochondrial cardiomyopathy as identified by spatial and single-cell transcriptomics.

通过空间和单细胞转录组学研究发现,Atf3 控制着女性线粒体心肌病中的转变

Qaqorh Tasneem, Takahashi Yusuke, Sameshima Kohei, Otani Kentaro, Yazawa Issei, Nishida Yuya, Tonai Kohei, Fujihara Yoshitaka, Honda Mizuki, Oki Shinya, Ohkawa Yasuyuki, Thorburn David R, Frazier Ann E, Takeda Atsuhito, Ikeda Yoshihiko, Sakaguchi Heima, Watanabe Takuya, Fukushima Norihide, Tsukamoto Yasumasa, Makita Naomasa, Yamaguchi Osamu, Murayama Kei, Ohtake Akira, Okazaki Yasushi, Kimura Takanari, Kato Hisakazu, Inoue Hijiri, Matsuoka Ken, Takashima Seiji, Shintani Yasunori

Legionella effector LpPIP recruits protein phosphatase 1 to the mitochondria to induce dephosphorylation of outer membrane proteins.

军团菌效应蛋白 LpPIP 将蛋白磷酸酶 1 募集到线粒体,诱导外膜蛋白去磷酸化

Yek Kai-Qi, Hodgson Evie R, Ang Ching-Seng, Palmer Catherine S, Frazier Ann E, Newton Hayley J, Stojanovski Diana

Mitochondrial biology and dysfunction in secondary mitochondrial disease

线粒体生物学及继发性线粒体疾病的功能障碍

Baker, Megan J; Crameri, Jordan J; Thorburn, David R; Frazier, Ann E; Stojanovski, Diana

Modelling Mitochondrial Disease in Human Pluripotent Stem Cells: What Have We Learned?

利用人类多能干细胞模拟线粒体疾病:我们学到了什么?

McKnight, Cameron L; Low, Yau Chung; Elliott, David A; Thorburn, David R; Frazier, Ann E

Correction: Function of hTim8a in complex IV assembly in neuronal cells provides insight into pathomechanism underlying Mohr-Tranebjærg syndrome

更正:hTim8a 在神经元细胞复合物 IV 组装中的功能为 Mohr-Tranebjærg 综合征的发病机制提供了新的见解

Kang, Yilin; Anderson, Alexander J; Jackson, Thomas Daniel; Palmer, Catherine S; De Souza, David P; Fujihara, Kenji M; Stait, Tegan; Frazier, Ann E; Clemons, Nicholas J; Tull, Deidreia; Thorburn, David R; McConville, Malcolm J; Ryan, Michael T; Stroud, David A; Stojanovski, Diana

Mitochondrial energy generation disorders: genes, mechanisms, and clues to pathology

线粒体能量生成障碍:基因、机制和病理线索

Frazier, Ann E; Thorburn, David R; Compton, Alison G

MiD49 and MiD51, new components of the mitochondrial fission machinery

MiD49 和 MiD51 是线粒体分裂机制的新组成部分。

Palmer, Catherine S; Osellame, Laura D; Laine, David; Koutsopoulos, Olga S; Frazier, Ann E; Ryan, Michael T

Structural and functional requirements for activity of the Tim9-Tim10 complex in mitochondrial protein import

线粒体蛋白输入过程中Tim9-Tim10复合物活性的结构和功能要求

Baker, Michael J; Webb, Chaille T; Stroud, David A; Palmer, Catherine S; Frazier, Ann E; Guiard, Bernard; Chacinska, Agnieszka; Gulbis, Jacqueline M; Ryan, Michael T

Shy1 couples Cox1 translational regulation to cytochrome c oxidase assembly

Shy1 将 Cox1 的翻译调控与细胞色素 c 氧化酶的组装联系起来

Mick, David U; Wagner, Karina; van der Laan, Martin; Frazier, Ann E; Perschil, Inge; Pawlas, Magdalena; Meyer, Helmut E; Warscheid, Bettina; Rehling, Peter