日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Deep Visual Proteomics maps proteotoxicity in a genetic liver disease.

深度可视化蛋白质组学绘制遗传性肝病中的蛋白质毒性图谱

Rosenberger Florian A, Mädler Sophia C, Thorhauge Katrine Holtz, Steigerwald Sophia, Fromme Malin, Lebedev Mikhail, Weiss Caroline A M, Oeller Marc, Wahle Maria, Metousis Andreas, Zwiebel Maximilian, Schmacke Niklas A, Detlefsen Sönke, Boor Peter, Fabián Ondřej, Fraňková Soňa, Krag Aleksander, Strnad Pavel, Mann Matthias

Severe alpha-1 antitrypsin deficiency is associated with a higher risk of complications after first decompensation than other aetiologies of cirrhosis

与其他病因引起的肝硬化相比,重度α1-抗胰蛋白酶缺乏症与首次失代偿后更高的并发症风险相关。

Balcar, Lorenz; Fromme, Malin; Kappe, Naomi; Schaefer, Benedikt; Fraňková, Soňa; van Melkebeke, Lukas; Stolk, Jan; Jachs, Mathias; Semmler, Georg; Hofer, Benedikt S; Tergast, Tammo L; Rieland, Hannah; Karl, Anna Sophie; Sperl, Jan; Wagner, Martin; Pons, Mònica; Hofer, Harald; Peck-Radosavljevic, Markus; Trauner, Michael; Reiberger, Thomas; Maasoumy, Benjamin; Zoller, Heinz; van Hoek, Bart; Verbeek, Jef; Strnad, Pavel; Mandorfer, Mattias

Alpha-1 Antitrypsin Inclusions Sequester GRP78 in a Bile Acid-Inducible Manner

α1-抗胰蛋白酶包涵体以胆汁酸诱导的方式螯合GRP78

Spivak, Igor; Guldiken, Nurdan; Usachov, Valentyn; Schaap, Frank; Damink, Steven W M Olde; Bouchecareilh, Marion; Lehmann, Alexandra; Fu, Lei; Mo, Fa-Rong; Ensari, Gökce Kobazi; Hufnagel, Franziska; Fromme, Malin; Preisinger, Christian; Strnad, Pavel

Clinical Utility of Non-Invasive Tests for Liver Fibrosis in People Living With Alpha-1 Antitrypsin Deficiency

非侵入性检测在α1-抗胰蛋白酶缺乏症患者肝纤维化诊断中的临床应用价值

Boeckmans, Joost; Schattenberg, Jörn M; Fromme, Malin; Strnad, Pavel; Hagström, Hannes

Alpha-1 antitrypsin deficiency-associated liver disease: From understudied disorder to the poster child of genetic medicine

α1-抗胰蛋白酶缺乏症相关肝病:从研究不足的疾病到遗传医学的典范

Fromme, Malin; Klebingat, Fabienne; Ellis, Paul; Strnad, Pavel

Biomarkers of hepatocellular synthesis in patients with decompensated cirrhosis

失代偿期肝硬化患者肝细胞合成的生物标志物

Gurbuz, Berivan; Guldiken, Nurdan; Reuken, Philipp; Fu, Lei; Remih, Katharina; Preisinger, Christian; Brůha, Radan; Leníček, Martin; Petrtýl, Jaromír; Reissing, Johanna; Aly, Mahmoud; Fromme, Malin; Zhou, Biaohuan; Karkossa, Isabel; Schubert, Kristin; von Bergen, Martin; Stallmach, Andreas; Bruns, Tony; Strnad, Pavel

The Relationship between Plasma Alpha-1-Antitrypsin Polymers and Lung or Liver Function in ZZ Alpha-1-Antitrypsin-Deficient Patients

ZZ α1-抗胰蛋白酶缺乏症患者血浆α1-抗胰蛋白酶聚合物与肺或肝功能的关系

Sark, Annelot D; Fromme, Malin; Olejnicka, Beata; Welte, Tobias; Strnad, Pavel; Janciauskiene, Sabina; Stolk, Jan