日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

NAC controls nascent chain fate through tunnel sensing and chaperone action

NAC通过隧道感知和分子伴侣作用控制新生链的命运。

Lee, Jae Ho; Rabl, Laurenz; Gamerdinger, Martin; Goyal, Vaishali; Khakzar, Katrin Michaela; Barbosa, Natalia Moreira; Abramovich, Juliana; Morales-Polanco, Fabian; Köhler, Ann-Kathrin; Samatova, Ekaterina; Rodnina, Marina V; Deuerling, Elke; Frydman, Judith

Survey of the human proteostasis network: the ubiquitin-proteasome system

人类蛋白质稳态网络概览:泛素-蛋白酶体系统

Elsasser, Suzanne; Powers, Evan T; Stoeger, Thomas; Sui, Xiaojing; Kurtzbard, Roy D; Martínez-Botía, Patricia; Wangeline, Margaret A; Gama, Alejandro Rodriguez; Huttlin, Edward L; Elia, Lisa P; Kelly, Jeffery W; Gestwicki, Jason E; Frydman, Judith; Finkbeiner, Steven; Clerico, Eugenia M; Morimoto, Richard I; Prado, Miguel A; Vertegaal, Alfred C O; Hofmann, Kay; Finley, Daniel

Proteostasis and lysosomal repair deficits in transdifferentiated neurons of Alzheimer's disease

阿尔茨海默病转分化神经元中的蛋白质稳态和溶酶体修复缺陷

Chou, Ching-Chieh; Vest, Ryan; Prado, Miguel A; Wilson-Grady, Joshua; Paulo, Joao A; Shibuya, Yohei; Moran-Losada, Patricia; Lee, Ting-Ting; Luo, Jian; Gygi, Steven P; Kelly, Jeffery W; Finley, Daniel; Wernig, Marius; Wyss-Coray, Tony; Frydman, Judith

Proteostasis and lysosomal repair deficits in transdifferentiated neurons of Alzheimer's disease

阿尔茨海默病转分化神经元中的蛋白质稳态和溶酶体修复缺陷

Chou, Ching-Chieh; Vest, Ryan; Prado, Miguel A; Wilson-Grady, Joshua; Paulo, Joao A; Shibuya, Yohei; Moran-Losada, Patricia; Lee, Ting-Ting; Luo, Jian; Gygi, Steven P; Kelly, Jeffery W; Finley, Daniel; Wernig, Marius; Wyss-Coray, Tony; Frydman, Judith

[Incidence of acquired morbidity and its impact on patients in a pediatric intensive care unit based on the functional status scale]

[基于功能状态评分的儿科重症监护病房患者获得性并发症发生率及其影响]

Frydman, Judith; López, Mara Inés

A lethal mitonuclear incompatibility in complex I of natural hybrids

天然杂交体复合物 I 中致命的线粒体-核不相容性

Moran, Benjamin M; Payne, Cheyenne Y; Powell, Daniel L; Iverson, Erik N K; Donny, Alexandra E; Banerjee, Shreya M; Langdon, Quinn K; Gunn, Theresa R; Rodriguez-Soto, Rebecca A; Madero, Angel; Baczenas, John J; Kleczko, Korbin M; Liu, Fang; Matney, Rowan; Singhal, Kratika; Leib, Ryan D; Hernandez-Perez, Osvaldo; Corbett-Detig, Russell; Frydman, Judith; Gifford, Casey; Schartl, Manfred; Havird, Justin C; Schumer, Molly

Brain malformations and seizures by impaired chaperonin function of TRiC

TRiC分子伴侣功能受损导致脑畸形和癫痫发作

Kraft, Florian; Rodriguez-Aliaga, Piere; Yuan, Weimin; Franken, Lena; Zajt, Kamil; Hasan, Dimah; Lee, Ting-Ting; Flex, Elisabetta; Hentschel, Andreas; Innes, A Micheil; Zheng, Bixia; Julia Suh, Dong Sun; Knopp, Cordula; Lausberg, Eva; Krause, Jeremias; Zhang, Xiaomeng; Trapane, Pamela; Carroll, Riley; McClatchey, Martin; Fry, Andrew E; Wang, Lisa; Giesselmann, Sebastian; Hoang, Hieu; Baldridge, Dustin; Silverman, Gary A; Radio, Francesca Clementina; Bertini, Enrico; Ciolfi, Andrea; Blood, Katherine A; de Sainte Agathe, Jean-Madeleine; Charles, Perrine; Bergant, Gaber; Čuturilo, Goran; Peterlin, Borut; Diderich, Karin; Streff, Haley; Robak, Laurie; Oegema, Renske; van Binsbergen, Ellen; Herriges, John; Saunders, Carol J; Maier, Andrea; Wolking, Stefan; Weber, Yvonne; Lochmüller, Hanns; Meyer, Stefanie; Aleman, Alberto; Polavarapu, Kiran; Nicolas, Gael; Goldenberg, Alice; Guyant, Lucie; Pope, Kathleen; Hehmeyer, Katherine N; Monaghan, Kristin G; Quade, Annegret; Smol, Thomas; Caumes, Roseline; Duerinckx, Sarah; Depondt, Chantal; Van Paesschen, Wim; Rieubland, Claudine; Poloni, Claudia; Guipponi, Michel; Arcioni, Severine; Meuwissen, Marije; Jansen, Anna C; Rosenblum, Jessica; Haack, Tobias B; Bertrand, Miriam; Gerstner, Lea; Magg, Janine; Riess, Olaf; Schulz, Jörg B; Wagner, Norbert; Wiesmann, Martin; Weis, Joachim; Eggermann, Thomas; Begemann, Matthias; Roos, Andreas; Häusler, Martin; Schedl, Tim; Tartaglia, Marco; Bremer, Juliane; Pak, Stephen C; Frydman, Judith; Elbracht, Miriam; Kurth, Ingo

Polyglutamine-mediated ribotoxicity disrupts proteostasis and stress responses in Huntington's disease.

多聚谷氨酰胺介导的核糖毒性会破坏亨廷顿病中的蛋白质稳态和应激反应

Aviner Ranen, Lee Ting-Ting, Masto Vincent B, Li Kathy H, Andino Raul, Frydman Judith

A machine learning approach uncovers principles and determinants of eukaryotic ribosome pausing

机器学习方法揭示真核生物核糖体暂停的原理和决定因素

Aguilar Rangel, Mauricio; Stein, Kevin; Frydman, Judith

Cancers adapt to their mutational load by buffering protein misfolding stress

癌细胞通过缓冲蛋白质错误折叠压力来适应其突变负荷。

Tilk, Susanne; Frydman, Judith; Curtis, Christina; Petrov, Dmitri A