Residual laminin-binding activity and enhanced dystroglycan glycosylation by LARGE in novel model mice to dystroglycanopathy
在新型肌营养不良蛋白病模型小鼠中,LARGE 蛋白的残余层粘连蛋白结合活性和增强的肌营养不良蛋白糖基化作用
期刊:Human Molecular Genetics
影响因子:3.2
doi:10.1093/hmg/ddn387
Kanagawa, Motoi; Nishimoto, Akemi; Chiyonobu, Tomohiro; Takeda, Satoshi; Miyagoe-Suzuki, Yuko; Wang, Fan; Fujikake, Nobuhiro; Taniguchi, Mariko; Lu, Zhongpeng; Tachikawa, Masaji; Nagai, Yoshitaka; Tashiro, Fumi; Miyazaki, Jun-Ichi; Tajima, Youichi; Takeda, Shin'ichi; Endo, Tamao; Kobayashi, Kazuhiro; Campbell, Kevin P; Toda, Tatsushi