日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Targeted deep sequencing identifies mosaicism in patients with immune dysregulation

靶向深度测序可识别免疫失调患者的嵌合现象

Schmitz, Elizabeth G; Paul, Alexander J; Ghosh, Rajarshi; Saucier, Nermina; Kolicheski, Ana; Risma, Samuel I; McDaniels, Kristen P; Liu, Michelle; Lewis, Katie L; de Jesus, Adriana A; Alehashemi, Sara; Fronick, Catrina C; Stein, David; Dominguez, Daniela; Hiraki, Linda T; Lee, Jessica H; Norman, Stephanie; Peng, Christine R; Ward, Brant R; Pettiford, Leah H; Platt, Anna; Lawrence, Monica G; Rocco, Joseph M; Al-Herz, Waleed; Zerbe, Christa S; Atkinson, T Prescott; Peng, Xiao P; Allenspach, Eric J; Hoytema van Konijnenburg, David P; Platt, Craig D; Elkins, Megan; Walter, Jolan E; Bleesing, Jack J; Klion, Amy; Ramaswami, Ramya; Uzel, Gulbu; Lionakis, Michail S; Dissanayake, Dilan; Su, Helen C; Cortese, Irene; Fuss, Ivan J; Bergerson, Jenna R E; Dropulic, Lesia; Sereti, Irini; Lisco, Andrea; Itan, Yuval; Milner, Joshua D; Bogunovic, Dusan; Goldbach-Mansky, Raphaela; Rao, V Koneti; Delmonte, Ottavia M; Notarangelo, Luigi D; Keller, Michael D; Durkee-Shock, Jessica; Cohen, Jeffrey I; Similuk, Morgan N; Holland, Steven M; Griffith, Malachi; Griffith, Obi L; Vogel, Tiphanie P; Canna, Scott; Freeman, Alexandra F; Walkiewicz, Magdalena A; Cooper, Megan A

Evaluating the efficacy and safety of pozelimab in patients with CD55 deficiency with hyperactivation of complement, angiopathic thrombosis, and protein-losing enteropathy disease: an open-label phase 2 and 3 study

评估 pozelimab 在伴有补体过度激活、血管病性血栓形成和蛋白丢失性肠病的 CD55 缺陷患者中的疗效和安全性:一项开放标签的 2 期和 3 期研究

Ozen, Ahmet; Chongsrisawat, Voranush; Sefer, Asena Pinar; Kolukisa, Burcu; Jalbert, Jessica J; Meagher, Karoline A; Brackin, Taylor; Feldman, Hagit Baris; Baris, Safa; Karakoc-Aydiner, Elif; Ergelen, Rabia; Fuss, Ivan J; Moorman, Heather; Suratannon, Narissara; Suphapeetiporn, Kanya; Perlee, Lorah; Harari, Olivier A; Yancopoulos, George D; Lenardo, Michael J

Nodular regenerative hyperplasia in X-linked agammaglobulinemia: An underestimated and severe complication

X连锁无丙种球蛋白血症中的结节性再生性增生:一种被低估的严重并发症

Nunes-Santos, Cristiane J; Koh, Christopher; Rai, Anjali; Sacco, Keith; Marciano, Beatriz E; Kleiner, David E; Marko, Jamie; Bergerson, Jenna R E; Stack, Michael; Rivera, Maria M; Constantine, Gregory; Strober, Warren; Uzel, Gulbu; Fuss, Ivan J; Notarangelo, Luigi D; Holland, Steven M; Rosenzweig, Sergio D; Heller, Theo

The Role of NLRP3 and IL-1β in the Pathogenesis of Inflammatory Bowel Disease

NLRP3和IL-1β在炎症性肠病发病机制中的作用

Mao, Liming; Kitani, Atsushi; Strober, Warren; Fuss, Ivan J

Tumor growth limited to subcutaneous site vs tumor growth in pulmonary site exhibit differential effects on systemic immunities

局限于皮下部位的肿瘤生长与肺部肿瘤生长对全身免疫的影响不同。

Masuda, Junko; Takayama, Eiji; Strober, Warren; Satoh, Ayano; Morimoto, Yuji; Honjo, Yasuko; Ichinohe, Tatsuo; Tokuno, Shin-Ichi; Ishizuka, Toshiaki; Nakata, Takahiro; Mizutani, Akifumi; Umemura, Naoki; Kitani, Atsushi; Fuss, Ivan J; Shigehiro, Tsukasa; Kawaki, Harumi; Mizuno-Kamiya, Masako; Kondoh, Nobuo; Seno, Masaharu

Nodular regenerative hyperplasia in common variable immunodeficiency

常见变异型免疫缺陷中的结节性再生性增生

Fuss, Ivan J; Friend, Julia; Yang, Zhiqiong; He, Jian Ping; Hooda, Lubna; Boyer, James; Xi, Liqiang; Raffeld, Mark; Kleiner, David E; Heller, Theo; Strober, Warren

Suppression of inflammation in ulcerative colitis by interferon-β-1a is accompanied by inhibition of IL-13 production.

干扰素-β-1a抑制溃疡性结肠炎炎症的同时,也抑制了IL-13的产生

Mannon Peter J, Hornung Ronald L, Yang Zhiqiong, Yi Chuli, Groden Catherine, Friend Julia, Yao Michael, Strober Warren, Fuss Ivan J

Proinflammatory cytokines in the pathogenesis of inflammatory bowel diseases

促炎细胞因子在炎症性肠病发病机制中的作用

Strober, Warren; Fuss, Ivan J

Activation of type I IFN signaling by NOD1 mediates mucosal host defense against Helicobacter pylori infection

NOD1激活I型干扰素信号通路介导黏膜宿主对幽门螺杆菌感染的防御。

Watanabe, Tomohiro; Asano, Naoki; Kitani, Atsushi; Fuss, Ivan J; Chiba, Tsutomu; Strober, Warren

The deubiquitinase CYLD targets Smad7 protein to regulate transforming growth factor β (TGF-β) signaling and the development of regulatory T cells.

去泛素化酶 CYLD 靶向 Smad7 蛋白,以调节转化生长因子 β (TGF-β) 信号传导和调节性 T 细胞的发育

Zhao Yongge, Thornton Angela M, Kinney Matthew C, Ma Chi A, Spinner Jacob J, Fuss Ivan J, Shevach Ethan M, Jain Ashish