日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

The XENONnT dark matter experiment

XENONnT暗物质实验

Aprile, E; Aalbers, J; Abe, K; Ahmed Maouloud, S; Althueser, L; Andrieu, B; Angelino, E; Angevaare, J R; Antochi, V C; Antón Martin, D; Arneodo, F; Balata, M; Baudis, L; Baxter, A L; Bazyk, M; Bellagamba, L; Biondi, R; Bismark, A; Brookes, E J; Brown, A; Bruenner, S; Bruno, G; Budnik, R; Bui, T K; Cai, C; Cardoso, J M R; Cassese, F; Chiarini, A; Cichon, D; Cimental Chavez, A P; Colijn, A P; Conrad, J; Corrieri, R; Cuenca-García, J J; Cussonneau, J P; Dadoun, O; D'Andrea, V; Decowski, M P; De Fazio, B; Gangi, P Di; Diglio, S; Disdier, J M; Douillet, D; Eitel, K; Elykov, A; Farrell, S; Ferella, A D; Ferrari, C; Fischer, H; Flierman, M; Form, S; Front, D; Fulgione, W; Fuselli, C; Gaemers, P; Gaior, R; Rosso, A Gallo; Galloway, M; Gao, F; Gardner, R; Garroum, N; Glade-Beucke, R; Grandi, L; Grigat, J; Guan, H; Guerzoni, M; Guida, M; Hammann, R; Higuera, A; Hils, C; Hoetzsch, L; Hood, N F; Howlett, J; Huhmann, C; Iacovacci, M; Iaquaniello, G; Iven, L; Itow, Y; Jakob, J; Joerg, F; Joy, A; Kara, M; Kavrigin, P; Kazama, S; Kobayashi, M; Koltman, G; Kopec, A; Kuger, F; Landsman, H; Lang, R F; Levinson, L; Li, I; Li, S; Liang, S; Lindemann, S; Lindner, M; Liu, K; Loizeau, J; Lombardi, F; Long, J; Lopes, J A M; Ma, Y; Macolino, C; Mahlstedt, J; Mancuso, A; Manenti, L; Marignetti, F; Marrodán Undagoitia, T; Martella, P; Martens, K; Masbou, J; Masson, D; Masson, E; Mastroianni, S; Mele, E; Messina, M; Michinelli, R; Miuchi, K; Molinario, A; Moriyama, S; Morå, K; Mosbacher, Y; Murra, M; Müller, J; Ni, K; Nisi, S; Oberlack, U; Orlandi, D; Othegraven, R; Paetsch, B; Palacio, J; Parlati, S; Paschos, P; Pellegrini, Q; Peres, R; Peters, C; Pienaar, J; Pierre, M; Plante, G; Pollmann, T R; Qi, J; Qin, J; García, D Ramírez; Rynge, M; Shi, J; Singh, R; Sanchez, L; Santos, J M F Dos; Sarnoff, I; Sartorelli, G; Schreiner, J; Schulte, D; Schulte, P; Schulze Eißing, H; Schumann, M; Scotto Lavina, L; Selvi, M; Semeria, F; Shagin, P; Shi, S; Shockley, E; Silva, M; Simgen, H; Stephen, J; Stern, M; Stillwell, B K; Takeda, A; Tan, P-L; Tatananni, D; Terliuk, A; Thers, D; Toschi, F; Trinchero, G; Tunnell, C; Tönnies, F; Valerius, K; Volta, G; Weinheimer, C; Weiss, M; Wenz, D; Westermann, J; Wittweg, C; Wolf, T; Wu, V H S; Xing, Y; Xu, D; Xu, Z; Yamashita, M; Yang, L; Ye, J; Yuan, L; Zavattini, G; Zhong, M; Zhu, T

Venglustat, an orally administered glucosylceramide synthase inhibitor: Assessment over 3 years in adult males with classic Fabry disease in an open-label phase 2 study and its extension study

Venglustat,一种口服葡糖基神经酰胺合成酶抑制剂:一项开放标签的 II 期研究及其扩展研究,对患有经典法布里病的成年男性进行了为期 3 年的评估。

Deegan, Patrick B; Goker-Alpan, Ozlem; Geberhiwot, Tarekegn; Hopkin, Robert J; Lukina, Elena; Tylki-Szymanska, Anna; Zaher, Atef; Sensinger, Charlotte; Gaemers, Sebastiaan J M; Modur, Vijay; Thurberg, Beth L; Sharma, Jyoti; Najafian, Behzad; Mauer, Michael; DasMahapatra, Pronabesh; Wilcox, William R; Germain, Dominique P

Material radiopurity control in the XENONnT experiment

XENONnT实验中的材料放射性纯度控制

Aprile, E; Abe, K; Agostini, F; Ahmed Maouloud, S; Alfonsi, M; Althueser, L; Angelino, E; Angevaare, J R; Antochi, V C; Antón Martin, D; Arneodo, F; Baudis, L; Baxter, A L; Bellagamba, L; Biondi, R; Bismark, A; Brown, A; Bruenner, S; Bruno, G; Budnik, R; Capelli, C; Cardoso, J M R; Cichon, D; Cimmino, B; Clark, M; Colijn, A P; Conrad, J; Cuenca-García, J J; Cussonneau, J P; D'Andrea, V; Decowski, M P; Gangi, P Di; Pede, S Di; Giovanni, A Di; Stefano, R Di; Diglio, S; Elykov, A; Farrell, S; Ferella, A D; Fischer, H; Fulgione, W; Gaemers, P; Gaior, R; Galloway, M; Gao, F; Glade-Beucke, R; Grandi, L; Grigat, J; Higuera, A; Hils, C; Hiraide, K; Hoetzsch, L; Howlett, J; Iacovacci, M; Itow, Y; Jakob, J; Joerg, F; Kato, N; Kavrigin, P; Kazama, S; Kobayashi, M; Koltman, G; Kopec, A; Landsman, H; Lang, R F; Levinson, L; Li, I; Liang, S; Lindemann, S; Lindner, M; Liu, K; Lombardi, F; Long, J; Lopes, J A M; Ma, Y; Macolino, C; Mahlstedt, J; Mancuso, A; Manenti, L; Manfredini, A; Marignetti, F; Marrodán Undagoitia, T; Martens, K; Masbou, J; Masson, D; Masson, E; Mastroianni, S; Messina, M; Miuchi, K; Mizukoshi, K; Molinario, A; Moriyama, S; Morå, K; Mosbacher, Y; Murra, M; Ni, K; Oberlack, U; Palacio, J; Peres, R; Pienaar, J; Pierre, M; Pizzella, V; Plante, G; Qi, J; Qin, J; Ramírez García, D; Reichard, S; Rocchetti, A; Rupp, N; Sanchez, L; Dos Santos, J M F; Sartorelli, G; Schreiner, J; Schulte, D; Schulze Eißing, H; Schumann, M; Lavina, L Scotto; Selvi, M; Semeria, F; Shagin, P; Shockley, E; Silva, M; Simgen, H; Takeda, A; Tan, P L; Terliuk, A; Therreau, C; Thers, D; Toschi, F; Trinchero, G; Tunnell, C; Tönnies, F; Valerius, K; Volta, G; Wei, Y; Weinheimer, C; Weiss, M; Wenz, D; Westermann, J; Wittweg, C; Wolf, T; Xu, Z; Yamashita, M; Yang, L; Ye, J; Yuan, L; Zavattini, G; Zhang, Y; Zhong, M; Zhu, T; Zopounidis, J P; Laubenstein, M; Nisi, S

Clinical outcomes after 4.5 years of eliglustat therapy for Gaucher disease type 1: Phase 3 ENGAGE trial final results

接受eliglustat治疗4.5年后戈谢病1型患者的临床结果:3期ENGAGE试验的最终结果

Mistry, Pramod K; Lukina, Elena; Ben Turkia, Hadhami; Shankar, Suma P; Baris Feldman, Hagit; Ghosn, Marwan; Mehta, Atul; Packman, Seymour; Lau, Heather; Petakov, Milan; Assouline, Sarit; Balwani, Manisha; Danda, Sumita; Hadjiev, Evgueniy; Ortega, Andres; Foster, Meredith C; Gaemers, Sebastiaan J M; Peterschmitt, M Judith

222 Rn  emanation measurements for the XENON1T experiment

XENON1T实验的222Rn析出测量

Aprile, E; Aalbers, J; Agostini, F; Alfonsi, M; Althueser, L; Amaro, F D; Antochi, V C; Angelino, E; Angevaare, J R; Arneodo, F; Barge, D; Baudis, L; Bauermeister, B; Bellagamba, L; Benabderrahmane, M L; Berger, T; Breur, P A; Brown, A; Brown, E; Bruenner, S; Bruno, G; Budnik, R; Capelli, C; Cardoso, J M R; Cichon, D; Cimmino, B; Clark, M; Coderre, D; Colijn, A P; Conrad, J; Cussonneau, J P; Decowski, M P; Depoian, A; Di Gangi, P; Di Giovanni, A; Di Stefano, R; Diglio, S; Elykov, A; Eurin, G; Ferella, A D; Fulgione, W; Gaemers, P; Gaior, R; Rosso, A Gallo; Galloway, M; Gao, F; Grandi, L; Garbini, M; Hasterok, C; Hils, C; Hiraide, K; Hoetzsch, L; Hogenbirk, E; Howlett, J; Iacovacci, M; Itow, Y; Joerg, F; Kato, N; Kazama, S; Kobayashi, M; Koltman, G; Kopec, A; Landsman, H; Lang, R F; Levinson, L; Lin, Q; Lindemann, S; Lindner, M; Lombardi, F; Lopes, J A M; López Fune, E; Macolino, C; Mahlstedt, J; Manenti, L; Manfredini, A; Marignetti, F; Undagoitia, T Marrodán; Martens, K; Masbou, J; Masson, D; Mastroianni, S; Messina, M; Miuchi, K; Molinario, A; Morå, K; Moriyama, S; Mosbacher, Y; Murra, M; Naganoma, J; Ni, K; Oberlack, U; Odgers, K; Palacio, J; Pelssers, B; Peres, R; Pienaar, J; Pizzella, V; Plante, G; Qin, J; Qiu, H; García, D Ramírez; Reichard, S; Rocchetti, A; Rupp, N; Santos, J M F Dos; Sartorelli, G; Šarčević, N; Scheibelhut, M; Schindler, S; Schreiner, J; Schulte, D; Schumann, M; Lavina, L Scotto; Selvi, M; Semeria, F; Shagin, P; Shockley, E; Silva, M; Simgen, H; Takeda, A; Therreau, C; Thers, D; Toschi, F; Trinchero, G; Tunnell, C; Vargas, M; Volta, G; Wack, O; Wang, H; Wei, Y; Weinheimer, C; Weiss, M; Wenz, D; Westermann, J; Wittweg, C; Wulf, J; Xu, Z; Yamashita, M; Ye, J; Zavattini, G; Zhang, Y; Zhu, T; Zopounidis, J P

Pregnancy outcome in women with Gaucher disease type 1 who had unplanned pregnancies during eliglustat clinical trials

在eliglustat临床试验期间发生意外怀孕的1型戈谢病女性的妊娠结局

Lukina, Elena; Balwani, Manisha; Belmatoug, Nadia; Watman, Nora; Hughes, Derralynn; Gaemers, Sebastiaan J M; Foster, Meredith C; Lewis, Grace; Peterschmitt, M Judith

Outcomes after 8 years of eliglustat therapy for Gaucher disease type 1: Final results from the Phase 2 trial

接受eliglustat治疗8年后,戈谢病1型患者的疗效:II期试验的最终结果

Lukina, Elena; Watman, Nora; Dragosky, Marta; Lau, Heather; Avila Arreguin, Elsa; Rosenbaum, Hanna; Zimran, Ari; Foster, Meredith C; Gaemers, Sebastiaan J M; Peterschmitt, M Judith

Long-term adverse event profile from four completed trials of oral eliglustat in adults with Gaucher disease type 1

已完成的四项口服eliglustat治疗1型戈谢病成人患者的试验的长期不良事件概况

Peterschmitt, M Judith; Freisens, Selena; Underhill, Lisa H; Foster, Meredith C; Lewis, Grace; Gaemers, Sebastiaan J M

Eliglustat maintains long-term clinical stability in patients with Gaucher disease type 1 stabilized on enzyme therapy

Eliglustat 可维持接受酶疗法治疗后病情稳定的 1 型戈谢病患者的长期临床稳定性

Cox, Timothy M; Drelichman, Guillermo; Cravo, Renata; Balwani, Manisha; Burrow, Thomas Andrew; Martins, Ana Maria; Lukina, Elena; Rosenbloom, Barry; Goker-Alpan, Ozlem; Watman, Nora; El-Beshlawy, Amal; Kishnani, Priya S; Pedroso, Maria Lucia; Gaemers, Sebastiaan J M; Tayag, Regina; Peterschmitt, M Judith

Outcomes after 18 months of eliglustat therapy in treatment-naïve adults with Gaucher disease type 1: The phase 3 ENGAGE trial

伊利格鲁司他治疗18个月后,初治1型戈谢病成年患者的结果:3期ENGAGE试验

Mistry, Pramod K; Lukina, Elena; Ben Turkia, Hadhami; Shankar, Suma P; Baris, Hagit; Ghosn, Marwan; Mehta, Atul; Packman, Seymour; Pastores, Gregory; Petakov, Milan; Assouline, Sarit; Balwani, Manisha; Danda, Sumita; Hadjiev, Evgueniy; Ortega, Andres; Gaemers, Sebastiaan J M; Tayag, Regina; Peterschmitt, M Judith