日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

N-terminal Huntingtin Knock-In Mice: Implications of Removing the N-terminal Region of Huntingtin for Therapy

N端亨廷顿蛋白敲入小鼠:去除亨廷顿蛋白N端区域对治疗的意义

Liu, Xudong; Wang, Chuan-En; Hong, Yan; Zhao, Ting; Wang, Guohao; Gaertig, Marta A; Sun, Miao; Li, Shihua; Li, Xiao-Jiang

Age-dependent decrease in chaperone activity impairs MANF expression, leading to Purkinje cell degeneration in inducible SCA17 mice.

年龄依赖性的分子伴侣活性下降会损害 MANF 表达,导致可诱导 SCA17 小鼠的浦肯野细胞退化

Yang Su, Huang Shanshan, Gaertig Marta A, Li Xiao-Jiang, Li Shihua