日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Efficacy and safety of steroid-sparing strategy in the treatment of AIHA associated with KSHV/HHV-8 positive multicentric Castleman disease

类固醇替代疗法治疗伴有KSHV/HHV-8阳性多中心Castleman病的自身免疫性溶血性贫血的疗效和安全性

Dieudonné, Yannick; Gourguechon, Clément; Stammler, Romain; Delestre, Florence; Sorin, Boris; Dunogué, Bertrand; Dumas, Guillaume; Fouquet, Guillemette; Ronchetti, Anne-Marie; Paule, Romain; Meliani, Pascal; Pansu, Nathalie; Buzele, Rodolphe; Noel, Robin; Fadlallah, Jehane; Malphettes, Marion; Corvilain, Emilie; Meignin, Véronique; Guillaud, Constance; Dossier, Antoine; Dion, Jérémie; Gérard, Laurence; Oksenhendler, Eric; Galicier, Lionel; Boutboul, David

Optimizing ADAMTS13 prophylaxis to reduce relapse and organ failure in congenital thrombotic thrombocytopenic purpura

优化ADAMTS13预防以减少先天性血栓性血小板减少性紫癜的复发和器官衰竭

Joly, Bérangère S; Joseph, Adrien; Bouzid, Raïda; Boisseau, Pierre; Kwon, Thérésa; Dossier, Claire; Gouge-Biebuyck, Nathalie; Boyer, Olivia; Tsatsaris, Vassilis; Harambat, Jérôme; Delmas, Yahsou; Moranne, Olivier; Sellier-Leclerc, Anne-Laure; Marie, Manon; Barbet, Christelle; Provôt, François; Benhamou, Ygal; Veyradier, Agnès; Coppo, Paul; Augusto, Jean-François; Azoulay, Elie; Barbay, Virginie; Benhamou, Ygal; Arnaud, Jaccard; Charvet-Rumpler, Anne; Chauveau, Dominique; Choukroun, Gabriel; Coindre, Jean-Philippe; Coppo, Paul; Delmas, Yahsou; Celia, Salanoubat; Dossier, Antoine; Simon, Ville; Frémeaux-Bacchi, Véronique; Galicier, Lionel; Grangé, Steven; Guidet, Bertrand; Halimi, Jean-Michel; Antoine, Neel; Jacobs, Frédéric; Joly, Bérangère; Kanouni, Tarik; Kaplanski, Gilles; Virginie, Rieu; Le Guern, Véronique; Moulin, Bruno; Rebibou, Jean-Michel; Ojeda Uribe, Mario; Parquet, Nathalie; Pène, Frédéric; Perez, Pierre; Poullin, Pascale; Pouteil-Noble, Claire; Presne, Claire; Provôt, Françoi; Laurent, Mesnard; Saheb, Samir; Seguin, Amélie; Servais, Aude; Stépanian, Alain; Veyradier, Agnè; Vigneau, Cécile; Wynckel, Alain; Zunic, Patricia; Krummel, Thierry; Ulrich, Marc; Hertig, Alexandre; Benoît, Suzon; Laurent, Gilardin; Le Quintrec, Moglie; Kwon, Theresa; Chatelet, Valérie; Ducheyron, Damien; Martis, Nihal; Marie, Manon; Ribes, David; Ronchetti, Anne-Marie

Porto-sinusoidal Vascular Disease is Associated with Gastrointestinal Disorders in Common Variable Immunodefiency

门静脉窦血管疾病与常见变异型免疫缺陷患者的胃肠道疾病相关

Corvilain, Emilie; Gérard, Laurence; Fadlallah, Jehane; Galicier, Lionel; Delaval, Laure; Alchidiac, Jessy; Plessier, Aurélie; Boutboul, David; Fieschi, Claire; Oksenhendler, Eric; Rautou, Pierre Emmanuel; Malphettes, Marion

Anti-ADAMTS13 Antibodies Trajectory is Associated With ADAMTS13 Recovery in Immune-Mediated TTP

抗ADAMTS13抗体轨迹与免疫介导的TTP中ADAMTS13的恢复相关。

Robert, Marie; Mageau, Arthur; Benhamou, Ygal; Provôt, François; Fadlallah, Jehane; Galicier, Lionel; Azoulay, Elie; Ait-Oufella, Hafid; Urbina, Tomas; Poullin, Pascale; Wynckel, Alain; Poulain, Coralie; Martis, Nihal; Perez, Pierre; Rieu, Virginie; Delmas, Yahsou; Halimi, Jean-Michel; Barbet, Christelle; Seguin, Amélie; Chatelet, Valérie; Augusto, Jean-François; Legendre, Mathieu; Moranne, Olivier; Philipponnet, Carole; Cador, Bérengère; Bouzid, Raïda; Joly, Bérangère S; Veyradier, Agnès; Coppo, Paul

Multicenter validation of secondary hemophagocytic lymphohistiocytosis diagnostic criteria

继发性噬血细胞性淋巴组织细胞增生症诊断标准的多中心验证

Lachmann, Gunnar; Heeren, Patrick; Schuster, Friederike S; Nyvlt, Peter; Spies, Claudia; Feinkohl, Insa; Schenk, Thomas; Ammouri, Wafa; Debaugnies, France; Galicier, Lionel; Jia, Yuan; Meena, Nikhil; Nagant, Carole; Neth, Olaf; Nierkens, Stefan; San Martin, Juan; Sun, Hao Wei Linda; Wang, Yini; Wang, Zhao; Yoon, Jae-Ho; Brunkhorst, Frank M; La Rosée, Paul; Janka, Gritta; Lachmann, Cornelia

Efficacy and safety of dapsone in adult primary immune thrombocytopenia

氨苯砜治疗成人原发性免疫性血小板减少症的疗效和安全性

Larue, Marion; Moulis, Guillaume; Rueter, Manuela; Audia, Sylvain; Comont, Thibault; Terriou, Louis; Viallard, Jean-François; Pan-Petesch, Brigitte; Royer, Bruno; Bonnotte, Bernard; Galicier, Lionel; Lambotte, Olivier; Lefrere, François; Cheze, Stéphane; Ebbo, Mikael; Duong, Tu-Ahn; Boutin, Emmanuelle; Languille, Laetitia; Mahevas, Matthieu; Godeau, Bertrand; Canoui-Poitrine, Florence; Michel, Marc

Time to redefine HHV-8 MCD and KICS criteria?

是时候重新定义HHV-8 MCD和KICS标准了吗?

Stammler, Romain; Dieudonné, Yannick; Vanjak, Anthony; Oksenhendler, Eric; Galicier, Lionel; Boutboul, David

IgA and IgM-enriched Immunoglobulins in Primary Immunodeficiencies: a Pilot Study

原发性免疫缺陷中富含 IgA 和 IgM 的免疫球蛋白:一项初步研究

Collet, Aurore; Coiffard, Benjamin; Ledoult, Emmanuel; Fieschi, Claire; Cheminant, Morgane; Serris, Alexandra; Suarez, Felipe; Sanges, Sébastien; Neel, Antoine; Nove-Josserand, Raphaële; Stabler, Sarah; El Husseini, Kinan; Huault, Alice; Cougoul, Pierre; Mausservey, Christelle; Cassir, Nadim; Mirgot, Floriane; Meresse, Bertrand; Dendooven, Arnaud; Poizot, Sandrine; Le Scornet, Tanguy; Bravard, Anne-Sophie; Conrad, Anne; Levêque, Manon; Fadlallah, Jehane; Melenotte, Cléa; De La Roque, Chloë Dumas; Tinevez, Claire; Chahla, Wadih Abou; Dubucquoi, Sylvain; Labalette, Myriam; Neven, Bénédicte; Malphettes, Marion; Schleinitz, Nicolas; Galicier, Lionel; Viallard, Jean-François; Gorochov, Guy; Lefèvre, Guillaume

Urogenital Schistosomiasis Mimicking IgG4-RD in a Patient With HIV

泌尿生殖系统血吸虫病在 HIV 感染患者中表现类似 IgG4 相关疾病

Gagey, Guillemette; Sorial, Didier; Rasmussen, Camille; Mechai, Frédéric; Galicier, Lionel; Vérine, Jérôme; Oksenhendler, Eric; Bertinchamp, Rémi; Poullot, Elsa; Boutboul, David

Intronic branchpoint-to-acceptor variants underlying inborn errors of immunity

内含子分支点至受体变异是先天性免疫缺陷的根本原因

Alioua, Najiba; Lambert, Nathalie; Puel, Mathilde; Hanein, Sylvain; Bastard, Paul; Fusaro, Mathieu; Jaffray, Marie; Medel, Bernardita; Khellaf, Lydia; Seeleuthner, Yoann; Perin, Mélodie; Jacques, Corinne; Pasquet, Marlène; Olivier, Laura; Sepulveda, Fernando; Le Voyer, Tom; Cobat, Aurélie; Nitschké, Patrick; Galicier, Lionel; Schleinitz, Nicolas; Oksenhendler, Eric; Malphettes, Marion; Neven, Bénédicte; Moshous, Despina; Suarez, Felipe; Fieschi, Claire; Casanova, Jean-Laurent; de Saint Basile, Geneviève; Dorval, Guillaume; Picard, Capucine; Bustamante, Jacinta; Zhang, Peng; Rosain, Jérémie