日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Chaperone mediated autophagy is deficient in spinal motoneurons of ALS patients with TDP-43 proteinopathy

TDP-43蛋白病ALS患者的脊髓运动神经元中分子伴侣介导的自噬存在缺陷。

Garrigos, Daniel; Martinez-Morga, Marta; Pombero, Ana; García-Lopez, Raquel; Pastor, Diego; Riquelme, Dolores; Blanquer, Miguel; Iniesta, Francisca; Valdor, Rut; Geijo-Barrientos, Emilio; Hargus, Gunnar; Moraleda, José María; Martínez, Salvador

Overexpression of bank vole PrP(I109) in mice induces a spontaneous atypical prion disease with sex-dependent onset, early NfL elevation, and universal prion strain permissiveness

小鼠体内田鼠 PrP(I109) 的过表达可诱发一种自发性非典型朊病毒病,该病具有性别依赖性发病、早期 NfL 水平升高以及对普遍朊病毒株的易感性。

Eraña, Hasier; Vidal, Enric; Fernández-Borges, Natalia; Charco, Jorge M; Díaz-Domínguez, Carlos M; Sampedro-Torres-Quevedo, Cristina; San-Juan-Ansoleaga, Maitena; Fernández-Muñoz, Eva; Galarza-Ahumada, Josu; Pérez-Castro, Miguel Ángel; Gonçalves-Anjo, Nuno; Piñeiro, Patricia; Pirisinu, Laura; Di Bari, Michele Angelo; Giler, Samanta; Raimondi, Ilaria; Espinosa, Juan Carlos; Vanni, Ilaria; D'Agostino, Claudia; Rodríguez-Cuesta, Juan; Pasetto, Laura; Bonetto, Valentina; González-Martín, Nora; Teijeira, Susana; Zou, Wen-Quan; Geijo, Mariví; Torres, Juan María; Chiesa, Roberto; Sánchez-Martín, Manuel A; Nonno, Romolo; Requena, Jesús R; Castilla, Joaquín

Selective Lis1 inactivation disrupts migration and positioning of cortical somatostatin interneurons.

选择性 Lis1 失活会破坏皮质生长抑素中间神经元的迁移和定位。

Pombero A, García-López R, Geijo-Barrientos E, Martínez S

Animal organoids as transformative platforms for viral infections and zoonotic cross-species viral research

动物类器官作为病毒感染和人畜共患跨物种病毒研究的变革性平台

García-Rodríguez, Inés; García-Dorival, Isabel; Alonso, Covadonga; Cuesta-Geijo, Miguel Ángel

Spontaneous generation of diverse recombinant prion strains: sulfated glycan cofactors facilitate strain emergence but do not determine specific strain properties

自发产生多种重组朊病毒株:硫酸化聚糖辅因子促进毒株出现,但不决定毒株的具体特性

Lorenzo, Nuria L; Eraña, Hasier; Vidal, Enric; Charco, Jorge M; Parga, Lucía; Díaz-Domínguez, Carlos M; Veiga, Sonia; Bravo, Susana; Giler, Samanta; Geijo, Mariví; Requena, Jesús R; Castilla, Joaquín

Conservation of strain properties of bank vole-adapted chronic wasting disease in the absence of glycosylation and membrane anchoring

在缺乏糖基化和膜锚定的情况下,田鼠适应性慢性消耗性疾病的菌株特性得以保留

Vidal, Enric; Eraña, Hasier; Charco, Jorge M; Lorenzo, Nuria L; Giler, Samanta; Ordóñez, Montserrat; Fernández-Muñoz, Eva; San-Juan-Ansoleaga, Maitena; Telling, Glenn C; Sánchez-Martín, Manuel A; Geijo, Mariví; Requena, Jesús R; Castilla, Joaquín

Effect of primary structural variation on cervid prion protein in flexibility, stability, and spontaneous misfolding propensity

一级结构变异对鹿朊病毒蛋白的柔性、稳定性和自发错误折叠倾向的影响

Díaz-Domínguez, Carlos M; Eraña, Hasier; Peccati, Francesca; Vidal, Enric; Charco, Jorge M; Sampedro-Torres-Quevedo, Cristina; Pérez-Castro, Miguel A; Lorenzo, Nuria L; Giler, Samanta; Telling, Glenn C; Geijo, Mariví; Requena, Jesús R; Jiménez-Osés, Gonzalo; Castilla, Joaquín

Tuberculosis vaccination: microbiological and immunological summary of a series of experimental challenge studies

结核病疫苗接种:一系列实验性攻毒研究的微生物学和免疫学总结

Juste, Ramon A; Sevilla, Iker A; Minguijon, Esmeralda; Fuertes, Miguel; Elguezabal, Natalia; Geijo, Mariví; Vazquez, Patricia; Serrano, Miriam; Rakel, Arrazuria; Gortazar, Christian; Etxezarreta, Amaia; Molina, Elena; Garrido, Joseba M

Protection and diagnostic interference induced by heat-inactivated, phage-inactivated and live vaccine prototypes against animal tuberculosis

热灭活、噬菌体灭活和活疫苗原型对动物结核病的保护作用和诊断干扰

Fernández-Veiga, Leire; Fuertes, Miguel; Geijo, María V; Elguezabal, Natalia; Serrano-Mestre, Jose L; Vázquez-Iniesta, Lucía; Prados-Rosales, Rafael; Michelet, Lorraine; Boschiroli, Maria Laura; Pérez de Val, Bernat; Jones, Gareth J; Juste, Ramón A; Garrido, Joseba M; Sevilla, Iker A

A Protein Misfolding Shaking Amplification-based method for the spontaneous generation of hundreds of bona fide prions

一种基于蛋白质错误折叠振荡放大法的自发生成数百个真正朊病毒的方法

Eraña, Hasier; Sampedro-Torres-Quevedo, Cristina; Charco, Jorge M; Díaz-Domínguez, Carlos M; Peccati, Francesca; San-Juan-Ansoleaga, Maitena; Vidal, Enric; Gonçalves-Anjo, Nuno; Pérez-Castro, Miguel A; González-Miranda, Ezequiel; Piñeiro, Patricia; Fernández-Veiga, Leire; Galarza-Ahumada, Josu; Fernández-Muñoz, Eva; Perez de Nanclares, Guiomar; Telling, Glenn; Geijo, Mariví; Jiménez-Osés, Gonzalo; Castilla, Joaquín