日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Spinal Cord Phosphoproteome of SCA2 Mouse Model Reveals Alteration of ATXN2-N-Term PRM-SH3-Actin Interactome and of Autophagy

SCA2小鼠模型脊髓磷酸化蛋白质组揭示了ATXN2-N端PRM-SH3-肌动蛋白相互作用组和自噬的改变

Luis-Enrique Almaguer-Mederos,Arvind Reddy Kandi,Nesli-Ece Sen,Júlia Canet-Pons,Luca-Malena Berger,Matthew P Stokes,Kathryn Abell,Jana Key,Suzana Gispert,Georg Auburger

CLPP-Null Eukaryotes with Excess Heme Biosynthesis Show Reduced L-arginine Levels, Probably via CLPX-Mediated OAT Activation

具有过量血红素生物合成的 CLPP-Null 真核生物表现出 L-精氨酸水平降低,可能是通过 CLPX 介导的 OAT 激活实现的

Jana Key, Suzana Gispert, Arvind Reddy Kandi, Daniela Heinz, Andrea Hamann, Heinz D Osiewacz, David Meierhofer, Georg Auburger

Poly(A)-binding protein is an ataxin-2 chaperone that regulates biomolecular condensates

Poly(A)结合蛋白是一种调节生物分子凝聚物的共济失调蛋白-2伴侣

Steven Boeynaems, Yanniv Dorone, Yanrong Zhuang, Victoria Shabardina, Guozhong Huang, Anca Marian, Garam Kim, Anushka Sanyal, Nesli-Ece Şen, Daniel Griffith, Roberto Docampo, Keren Lasker, Iñaki Ruiz-Trillo, Georg Auburger, Alex S Holehouse, Edor Kabashi, Yi Lin, Aaron D Gitler

In Cerebellar Atrophy of 12-Month-Old ATM-Null Mice, Transcriptome Upregulations Concern Most Neurotransmission and Neuropeptide Pathways, While Downregulations Affect Prominently Itpr1, Usp2 and Non-Coding RNA

在 12 月龄 ATM 基因缺失小鼠的小脑萎缩中,转录组上调涉及大多数神经传递和神经肽通路,而下调则显著影响 Itpr1、Usp2 和非编码 RNA

Marina Reichlmeir, Júlia Canet-Pons, Gabriele Koepf, Wasifa Nurieva, Ruth Pia Duecker, Claudia Doering, Kathryn Abell, Jana Key, Matthew P Stokes, Stefan Zielen, Ralf Schubert, Zoltán Ivics, Georg Auburger

TR-FRET-Based Immunoassay to Measure Ataxin-2 as a Target Engagement Marker in Spinocerebellar Ataxia Type 2

基于 TR-FRET 的免疫测定法测量 Ataxin-2 作为脊髓小脑共济失调 2 型中的靶标参与标记

Jessica Bux, Nesli Ece Sen, Isa-Maria Klink, Stefan Hauser, Matthis Synofzik, Ludger Schöls, Georg Auburger, Olaf Riess, Jeannette Hübener-Schmid

Translation Fidelity and Respiration Deficits in CLPP-Deficient Tissues: Mechanistic Insights from Mitochondrial Complexome Profiling

CLPP 缺陷组织中的翻译保真度和呼吸缺陷:来自线粒体复合体分析的机制见解

Jana Key, Suzana Gispert, Gabriele Koepf, Julia Steinhoff-Wagner, Marina Reichlmeir, Georg Auburger

CLPP Depletion Causes Diplotene Arrest; Underlying Testis Mitochondrial Dysfunction Occurs with Accumulation of Perrault Proteins ERAL1, PEO1, and HARS2

CLPP 耗竭导致双线期停滞;潜在的睾丸线粒体功能障碍与 Perrault 蛋白 ERAL1、PEO1 和 HARS2 的积累有关

Jana Key, Suzana Gispert, Lieke Koornneef, Esther Sleddens-Linkels, Aneesha Kohli, Sylvia Torres-Odio, Gabriele Koepf, Shady Amr, Marina Reichlmeir, Patrick N Harter, Andrew Phillip West, Christian Münch, Willy M Baarends, Georg Auburger

Experimental Induction of Intracranial Aneurysms in Rats: A New Model Utilizing a Genetic Modification within the EDNRA Gene

大鼠颅内动脉瘤的实验诱导:利用 EDNRA 基因内遗传修饰的新模型

Tim Lampmann, Valeri Borger, Jürgen Konczalla, Suzana Gispert, Georg Auburger, Hartmut Vatter, Erdem Güresir

Inactivity of Peptidase ClpP Causes Primary Accumulation of Mitochondrial Disaggregase ClpX with Its Interacting Nucleoid Proteins, and of mtDNA

肽酶 ClpP 失活导致线粒体解聚酶 ClpX 及其相互作用的核蛋白和线粒体 DNA 的初级积累

Jana Key, Sylvia Torres-Odio, Nina C Bach, Suzana Gispert, Gabriele Koepf, Marina Reichlmeir, A Phillip West, Holger Prokisch, Peter Freisinger, William G Newman, Stavit Shalev, Stephan A Sieber, Ilka Wittig, Georg Auburger

Loss of Mitochondrial Protease CLPP Activates Type I IFN Responses through the Mitochondrial DNA-cGAS-STING Signaling Axis

线粒体蛋白酶 CLPP 的缺失通过线粒体 DNA-cGAS-STING 信号轴激活 I 型 IFN 反应

Sylvia Torres-Odio, Yuanjiu Lei, Suzana Gispert, Antonia Maletzko, Jana Key, Saeed S Menissy, Ilka Wittig, Georg Auburger, A Phillip West