日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Janus kinase and calcineurin-inhibitor combination in anti-MDA5 dermatomyositis: No significant survival benefit but reassuring safety profile

Janus激酶抑制剂和钙调磷酸酶抑制剂联合治疗抗MDA5皮肌炎:未见显著生存获益,但安全性良好

Pagis, Valentine; Astouati, Quentin; Pacoureau, Lucas; Nguyen, Yann; Bay, Pierre; Roux, Antoine; Gallay, Laure; Cottin, Vincent; Terrier, Benjamin; Meyer, Alain; Cerf, Charles; Neuville, Mathilde; Hervier, Baptiste; Renaud, Arthur; Suzon, Benoit; Schleinitz, Nicolas; Papo, Thomas; Priou, Pascaline; Mekinian, Arsène; Ullmer, Audrey; Oehler, Erwan; Gensous, Noémie; Berezne, Alice; Martin, Luc De Saint; Marhadour, Thierry; Martin, Mickaël; Servettaz, Amélie; Samson, Maxime; Gilardin, Laurent; Charles, Pierre; Woessner, Juliette; Carmoi, Thierry; Dilly, Baptiste; Mauhin, Wladimir; Baillet, Nicolas; Humbert, Sébastien; Thoreau, Benjamin; Lemaitre, Marine; Pendu, Claire Le; Loiseau, Pierre; Quemeneur, Thomas; Blanchard, Elodie; Voermans, Nicol; Launay, David; Nunes, Hilario; Benveniste, Olivier; Uzunhan, Yurdagul; Allenbach, Yves

Optimizing ADAMTS13 prophylaxis to reduce relapse and organ failure in congenital thrombotic thrombocytopenic purpura

优化ADAMTS13预防以减少先天性血栓性血小板减少性紫癜的复发和器官衰竭

Joly, Bérangère S; Joseph, Adrien; Bouzid, Raïda; Boisseau, Pierre; Kwon, Thérésa; Dossier, Claire; Gouge-Biebuyck, Nathalie; Boyer, Olivia; Tsatsaris, Vassilis; Harambat, Jérôme; Delmas, Yahsou; Moranne, Olivier; Sellier-Leclerc, Anne-Laure; Marie, Manon; Barbet, Christelle; Provôt, François; Benhamou, Ygal; Veyradier, Agnès; Coppo, Paul; Augusto, Jean-François; Azoulay, Elie; Barbay, Virginie; Benhamou, Ygal; Arnaud, Jaccard; Charvet-Rumpler, Anne; Chauveau, Dominique; Choukroun, Gabriel; Coindre, Jean-Philippe; Coppo, Paul; Delmas, Yahsou; Celia, Salanoubat; Dossier, Antoine; Simon, Ville; Frémeaux-Bacchi, Véronique; Galicier, Lionel; Grangé, Steven; Guidet, Bertrand; Halimi, Jean-Michel; Antoine, Neel; Jacobs, Frédéric; Joly, Bérangère; Kanouni, Tarik; Kaplanski, Gilles; Virginie, Rieu; Le Guern, Véronique; Moulin, Bruno; Rebibou, Jean-Michel; Ojeda Uribe, Mario; Parquet, Nathalie; Pène, Frédéric; Perez, Pierre; Poullin, Pascale; Pouteil-Noble, Claire; Presne, Claire; Provôt, Françoi; Laurent, Mesnard; Saheb, Samir; Seguin, Amélie; Servais, Aude; Stépanian, Alain; Veyradier, Agnè; Vigneau, Cécile; Wynckel, Alain; Zunic, Patricia; Krummel, Thierry; Ulrich, Marc; Hertig, Alexandre; Benoît, Suzon; Laurent, Gilardin; Le Quintrec, Moglie; Kwon, Theresa; Chatelet, Valérie; Ducheyron, Damien; Martis, Nihal; Marie, Manon; Ribes, David; Ronchetti, Anne-Marie

Cold Agglutinin Syndrome Secondary to Mycoplasma pneumoniae Infection in Adults: Results From a Large French Observational Study (MyCOLD Study)

成人肺炎支原体感染引起的冷凝集素综合征:一项大型法国观察性研究(MyCOLD 研究)的结果

Chevalier, Kevin; Holub, Matthieu; Palich, Romain; Blanckaert, Karine; Gilardin, Laurent; Terriou, Louis; Arnould, Bérangère; Bellaiche, Solal; Deshayes, Samuel; Mérindol, Julie; Rolland, Simon; Valentin, Simon; Amarsy, Rishma; Audia, Sylvain; Baltes, Virginie; Barret, Amaury; Cariou, Pierre-Louis; Cattelan, Jessy; Chassepot, Hortense; Chopin, Dorothée; Clément, Mélissa; Coeffier, Marine; Comont, Thibault; De Monteynard, Soline; Declerck, Charles; Durand, Pauline; Ebbo, Mikael; Galli, Gaël; Godot, Amélie; Hamrouni, Sarra; Kaeuffer, Charlotte; Kahn, Jean-Emmanuel; Lassel, Ludovic; Leautez, Sophie; Lecapitaine, Anne-Lise; Le Moal, Gwenael; Luque Paz, David; Martinot, Martin; Mrozek, Natacha; Pagis, Valentine; Perpoint, Thomas; Salle, Valéry; Viallard, Jean-François; Viguier, Clément; Mahevas, Matthieu; Godeau, Bertrand; Crickx, Etienne; Michel, Marc

Efficacy and Thrombotic Risk of Thrombopoietin Receptor Agonists for Immune Thrombocytopenia Secondary to Systemic Lupus and Antiphospholipid Syndrome: French Experience With 80 Patients

血小板生成素受体激动剂治疗系统性红斑狼疮和抗磷脂综合征继发性免疫性血小板减少症的疗效和血栓风险:法国80例患者的经验

Marques, Cindy; Moulis, Guillaume; Roussotte, Mickaël; Bonnotte, Bernard; Viallard, Jean-François; Graveleau, Julie; Lobbes, Hervé; Costedoat-Chalumeau, Nathalie; Deroux, Alban; Gobert, Delphine; Dossier, Antoine; Gilardin, Laurent; Lambotte, Olivier; Dufrenoy, Mylène; Mahévas, Matthieu; Michel, Marc; Sève, Pascal; Godeau, Bertrand

The temporal gene expression landscape of rhabdomyolysis-induced acute kidney injury reveals the timing of complement activation

横纹肌溶解症诱发的急性肾损伤的基因表达时间图谱揭示了补体激活的时机。

Grunenwald, Anne; Boudhabhay, Idris; Revel, Margot; Poillerat, Victoria; Voilin, Elodie; Majdi, Amine; Chaibi, Khalil; Gaudry, Stephane; Woodruff, Trent M; Crambert, Gilles; Guihaire, Julien; Zaidan, Mohamad; Oniszczuk, Julie; Frimat, Marie; Gnemmi, Viviane; Aletti, Marc; Nielly, Hubert; Gilardin, Laurent; Roumenina, Lubka T

Activity of apremilast in a patient with severe pemphigus vulgaris: case report

阿普米司特治疗重症寻常型天疱疮患者的疗效:病例报告

Delvaux, Cheyenne; Bohelay, Gérôme; Sitbon, Ishaï-Yaacov; Soued, Isaac; Alexandre, Marina; Cucherousset, Joël; Gilardin, Laurent; Diep, Antoine; Caux, Frédéric; Le Roux-Villet, Christelle

Clinical, biological, prognostic characteristics of patients with immune-mediated thrombotic thrombocytopenic purpura and Sjögren's disease

免疫介导的血栓性血小板减少性紫癜和干燥综合征患者的临床、生物学和预后特征

Luciano, Justine; Gilardin, Laurent; Nocturne, Gaétane; Bouzid, Raïda; Veyradier, Agnès; Mariette, Xavier; Coppo, Paul; Bonnet, Isabelle; Joly, Bérangère S

Tocilizumab-treated convalescent COVID-19 patients retain the cross-neutralization potential against SARS-CoV-2 variants

接受托珠单抗治疗的新冠肺炎康复患者仍保留对SARS-CoV-2变种的交叉中和能力。

Camille Chauvin ,Laurine Levillayer ,Mathilde Roumier ,Hubert Nielly ,Claude Roth ,Anupama Karnam ,Srinivasa Reddy Bonam ,Anne Bourgarit ,Clément Dubost ,Aurore Bousquet ,Sébastien Le Burel ,Raphaële Mestiri ,Damien Sene ,Joris Galland ,Marc Vasse ,Matthieu Groh ,Mathilde Le Marchand ,Camille Vassord-Dang ,Jean-François Gautier ,Nhan Pham-Thi ,Christiane Verny ,Bruno Pitard ,Cyril Planchais ,Hugo Mouquet ,Richard Paul ,Etienne Simon-Loriere ,Jagadeesh Bayry ,Laurent Gilardin ,Anavaj Sakuntabhai

The risk of COVID-19 death is much greater and age dependent with type I IFN autoantibodies

存在I型干扰素自身抗体的人,新冠肺炎死亡风险要高得多,且与年龄相关。

Manry, Jérémy; Bastard, Paul; Gervais, Adrian; Le Voyer, Tom; Rosain, Jérémie; Philippot, Quentin; Michailidis, Eleftherios; Hoffmann, Hans-Heinrich; Eto, Shohei; Garcia-Prat, Marina; Bizien, Lucy; Parra-Martínez, Alba; Yang, Rui; Haljasmägi, Liis; Migaud, Mélanie; Särekannu, Karita; Maslovskaja, Julia; de Prost, Nicolas; Tandjaoui-Lambiotte, Yacine; Luyt, Charles-Edouard; Amador-Borrero, Blanca; Gaudet, Alexandre; Poissy, Julien; Morel, Pascal; Richard, Pascale; Cognasse, Fabrice; Troya, Jesús; Trouillet-Assant, Sophie; Belot, Alexandre; Saker, Kahina; Garçon, Pierre; Rivière, Jacques G; Lagier, Jean-Christophe; Gentile, Stéphanie; Rosen, Lindsey B; Shaw, Elana; Morio, Tomohiro; Tanaka, Junko; Dalmau, David; Tharaux, Pierre-Louis; Sene, Damien; Stepanian, Alain; Mégarbane, Bruno; Triantafyllia, Vasiliki; Fekkar, Arnaud; Heath, James R; Franco, José Luis; Anaya, Juan-Manuel; Solé-Violán, Jordi; Imberti, Luisa; Biondi, Andrea; Bonfanti, Paolo; Castagnoli, Riccardo; Delmonte, Ottavia M; Zhang, Yu; Snow, Andrew L; Holland, Steven M; Biggs, Catherine M; Moncada-Vélez, Marcela; Arias, Andrés Augusto; Lorenzo, Lazaro; Boucherit, Soraya; Anglicheau, Dany; Planas, Anna M; Haerynck, Filomeen; Duvlis, Sotirija; Ozcelik, Tayfun; Keles, Sevgi; Bousfiha, Ahmed A; El Bakkouri, Jalila; Ramirez-Santana, Carolina; Paul, Stéphane; Pan-Hammarström, Qiang; Hammarström, Lennart; Dupont, Annabelle; Kurolap, Alina; Metz, Christine N; Aiuti, Alessandro; Casari, Giorgio; Lampasona, Vito; Ciceri, Fabio; Barreiros, Lucila A; Dominguez-Garrido, Elena; Vidigal, Mateus; Zatz, Mayana; van de Beek, Diederik; Sahanic, Sabina; Tancevski, Ivan; Stepanovskyy, Yurii; Boyarchuk, Oksana; Nukui, Yoko; Tsumura, Miyuki; Vidaur, Loreto; Tangye, Stuart G; Burrel, Sonia; Duffy, Darragh; Quintana-Murci, Lluis; Klocperk, Adam; Kann, Nelli Y; Shcherbina, Anna; Lau, Yu-Lung; Leung, Daniel; Coulongeat, Matthieu; Marlet, Julien; Koning, Rutger; Reyes, Luis Felipe; Chauvineau-Grenier, Angélique; Venet, Fabienne; Monneret, Guillaume; Nussenzweig, Michel C; Arrestier, Romain; Boudhabhay, Idris; Baris-Feldman, Hagit; Hagin, David; Wauters, Joost; Meyts, Isabelle; Dyer, Adam H; Kennelly, Sean P; Bourke, Nollaig M; Halwani, Rabih; Sharif-Askari, Fatemeh Saheb; Dorgham, Karim; Sallette, Jérôme; Sedkaoui, Souad Mehlal; AlKhater, Suzan; Rigo-Bonnin, Raúl; Morandeira, Francisco; Roussel, Lucie; Vinh, Donald C; Erikstrup, Christian; Condino-Neto, Antonio; Prando, Carolina; Bondarenko, Anastasiia; Spaan, András N; Gilardin, Laurent; Fellay, Jacques; Lyonnet, Stanislas; Bilguvar, Kaya; Lifton, Richard P; Mane, Shrikant; Anderson, Mark S; Boisson, Bertrand; Béziat, Vivien; Zhang, Shen-Ying; Andreakos, Evangelos; Hermine, Olivier; Pujol, Aurora; Peterson, Pärt; Mogensen, Trine H; Rowen, Lee; Mond, James; Debette, Stéphanie; de Lamballerie, Xavier; Burdet, Charles; Bouadma, Lila; Zins, Marie; Soler-Palacin, Pere; Colobran, Roger; Gorochov, Guy; Solanich, Xavier; Susen, Sophie; Martinez-Picado, Javier; Raoult, Didier; Vasse, Marc; Gregersen, Peter K; Piemonti, Lorenzo; Rodríguez-Gallego, Carlos; Notarangelo, Luigi D; Su, Helen C; Kisand, Kai; Okada, Satoshi; Puel, Anne; Jouanguy, Emmanuelle; Rice, Charles M; Tiberghien, Pierre; Zhang, Qian; Casanova, Jean-Laurent; Abel, Laurent; Cobat, Aurélie

The risk of COVID-19 death is much greater and age-dependent with type I IFN autoantibodies

存在I型干扰素自身抗体的人,新冠肺炎死亡风险要高得多,且与年龄相关。

Manry, Jeremy; Bastard, Paul; Gervais, Adrian; Le Voyer, Tom; Rosain, Jérémie; Philippot, Quentin; Michailidis, Eleftherios; Hoffmann, Hans-Heinrich; Eto, Shohei; Garcia-Prat, Marina; Bizien, Lucy; Parra-Martínez, Alba; Yang, Rui; Haljasmägi, Liis; Migaud, Mélanie; Särekannu, Karita; Maslovskaja, Julia; de Prost, Nicolas; Tandjaoui-Lambiotte, Yacine; Luyt, Charles-Edouard; Amador-Borrero, Blanca; Gaudet, Alexandre; Poissy, Julien; Morel, Pascal; Richard, Pascale; Cognasse, Fabrice; Troya, Jesus; Trouillet-Assant, Sophie; Belot, Alexandre; Saker, Kahina; Garçon, Pierre; Rivière, Jacques G; Lagier, Jean-Christophe; Gentile, Stéphanie; Rosen, Lindsey; Shaw, Elana; Morio, Tomohiro; Tanaka, Junko; Dalmau, David; Tharaux, Pierre-Louis; Sene, Damien; Stepanian, Alain; Mégarbane, Bruno; Triantafyllia, Vasiliki; Fekkar, Arnaud; Heath, James; Franco, Jose; Anaya, Juan-Manuel; Solé-Violán, Jordi; Imberti, Luisa; Biondi, Andrea; Bonfanti, Paolo; Castagnoli, Riccardo; Delmonte, Ottavia; Zhang, Yu; Snow, Andrew; Holland, Steve; Biggs, Catherine; Moncada-Vélez, Marcela; Arias, Andrés; Lorenzo, Lazaro; Boucherit, Soraya; Anglicheau, Dany; Planas, Anna; Haerynck, Filomeen; Duvlis, Sotirija; Nussbaum, Robert; Ozcelik, Tayfun; Keles, Sevgi; Bousfiha, Aziz; El Bakkouri, Jalila; Ramirez-Santana, Carolina; Paul, Stéphane; Pan-Hammarstrom, Qiang; Hammarstrom, Lennart; Dupont, Annabelle; Kurolap, Alina; Metz, Christine; Aiuti, Alessandro; Casari, Giorgio; Lampasona, Vito; Ciceri, Fabio; Barreiros, Lucila; Dominguez-Garrido, Elena; Vidigal, Mateus; Zatz, Mayana; van de Beek, Diederik; Sahanic, Sabina; Tancevski, Ivan; Stepanovskyy, Yurii; Boyarchuk, Oksana; Nukui, Yoko; Tsumura, Miyuki; Vidaur, Loreto; Tangye, Stuart; Burrel, Sonia; Duffy, Darragh; Quintana-Murci, Lluis; Klocperk, Adam; Kann, Nelli; Shcherbina, Anna; Lau, Yu-Lung; Leung, Daniel; Coulongeat, Matthieu; Marlet, Julien; Koning, Rutger; Reyes, Luis; Chauvineau-Grenier, Angélique; Venet, Fabienne; Monneret, Guillaume; Nussenzweig, Michel; Arrestier, Romain; Boudhabhay, Idris; Baris-Feldman, Hagit; Hagin, David; Wauters, Joost; Meyts, Isabelle; Dyer, Adam; Kennelly, Sean; Bourke, Nollaig; Halwani, Rabih; Sharif-Askari, Fatemeh; Dorgham, Karim; Sallette, Jérôme; Mehlal-Sedkaoui, Souad; AlKhater, Suzan; Rigo-Bonnin, Raúl; Morandeira, Francisco; Roussel, Lucie; Vinh, Donald; Erikstrup, Christian; Condino-Neto, Antonio; Prando, Carolina; Bondarenko, Anastasiia; Spaan, András; Gilardin, Laurent; Fellay, Jacques; Lyonnet, Stanislas; Bilguvar, Kaya; Lifton, Richard; Mane, Shrikant; Anderson, Mark; Boisson, Bertrand; Béziat, Vivien; Zhang, Shen-Ying; Andreakos, Evangelos; Hermine, Olivier; Pujol, Aurora; Peterson, Pärt; Mogensen, Trine Hyrup; Rowen, Lee; Mond, James; Debette, Stéphanie; deLamballerie, Xavier; Burdet, Charles; Bouadma, Lila; Zins, Marie; Soler-Palacin, Pere; Colobran, Roger; Gorochov, Guy; Solanich, Xavier; Susen, Sophie; Martinez-Picado, Javier; Raoult, Didier; Vasse, Marc; Gregersen, Peter; Rodríguez-Gallego, Carlos; Piemonti, Lorenzo; Notarangelo, Luigi; Su, Helen; Kisand, Kai; Okada, Satoshi; Puel, Anne; Jouanguy, Emmanuelle; Rice, Charles; Tiberghien, Pierre; Zhang, Qian; Casanova, Jean-Laurent; Abel, Laurent; Cobat, Aurélie