日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Mitochondria from huntington´s disease striatal astrocytes are hypermetabolic and compromise neuronal branching.

亨廷顿病纹状体星形胶质细胞的线粒体代谢亢进,损害神经元分支

López-Molina Laura, Pereda-Velarde Alba, di Franco Nadia, Aerts Imme, Sebastià Elisa, Valls-Roca Laura, Guitart-Mampel Mariona, Garrabou Gloria, Gines Silvia

Polyglutamine expansion affects huntingtin conformation in multiple Huntington's disease models

多聚谷氨酰胺扩增影响多种亨廷顿病模型中的亨廷顿蛋白构象

Daldin, Manuel; Fodale, Valentina; Cariulo, Cristina; Azzollini, Lucia; Verani, Margherita; Martufi, Paola; Spiezia, Maria Carolina; Deguire, Sean M; Cherubini, Marta; Macdonald, Douglas; Weiss, Andreas; Bresciani, Alberto; Vonsattel, Jean-Paul Gerard; Petricca, Lara; Marsh, J Lawrence; Gines, Silvia; Santimone, Iolanda; Marano, Massimo; Lashuel, Hilal A; Squitieri, Ferdinando; Caricasole, Andrea