日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Uncoupled glycerol-3-phosphate shuttle in kidney cancer reveals that cytosolic GPD is essential to support lipid synthesis

肾癌中甘油-3-磷酸穿梭的解偶联表明,胞质GPD对于支持脂质合成至关重要。

Cong-Hui Yao ,Joon Seok Park ,Kiran Kurmi ,Song-Hua Hu ,Giulia Notarangelo ,Joseph Crowley ,Heidi Jacobson ,Sheng Hui ,Arlene H Sharpe ,Marcia C Haigis

Metabolic modulation of mitochondrial mass during CD4+ T cell activation

CD4+ T细胞活化过程中线粒体质量的代谢调节

Kiran Kurmi ,Dan Liang ,Robert van de Ven ,Peter Georgiev ,Brandon Mark Gassaway ,SeongJun Han ,Giulia Notarangelo ,Isaac S Harris ,Cong-Hui Yao ,Joon Seok Park ,Song-Hua Hu ,Jingyu Peng ,Jefte M Drijvers ,Sarah Boswell ,Artem Sokolov ,Stephanie K Dougan ,Peter K Sorger ,Steven P Gygi ,Arlene H Sharpe ,Marcia C Haigis

Neonatal alloimmune neutropenia: diagnosis and management of 31 Italian patients

新生儿同种免疫性中性粒细胞减少症:31例意大利患者的诊断和治疗

Cattaneo, Alessandra; Liguori, Manuela; Trombetta, Elena; Ceriotti, Ferruccio; Pugni, Lorenza; Ronchi, Andrea; Carracchia, Giulia; Notarangelo, Lucia D; Ferrua, Francesca; Barzaghi, Federica; Giovanettoni, Chiara; Zuccotti, Gianvincenzo; Cirillo, Emilia; Pignata, Claudio; Meroni, Federica; Maietta, Anna; Farruggia, Piero; Porretti, Laura

Oncometabolite d-2HG alters T cell metabolism to impair CD8+ T cell function

癌代谢物 d-2HG 改变 T 细胞代谢,损害 CD8+ T 细胞功能

Giulia Notarangelo, Jessica B Spinelli, Elizabeth M Perez, Gregory J Baker, Kiran Kurmi, Ilaria Elia, Sylwia A Stopka, Gerard Baquer, Jia-Ren Lin, Alexandra J Golby, Shakchhi Joshi, Heide F Baron, Jefte M Drijvers, Peter Georgiev, Alison E Ringel, Elma Zaganjor, Samuel K McBrayer, Peter K Sorger, Ar

Tumor cells dictate anti-tumor immune responses by altering pyruvate utilization and succinate signaling in CD8+ T cells

肿瘤细胞通过改变CD8+ T细胞中丙酮酸的利用和琥珀酸的信号传导来调控抗肿瘤免疫反应。

Ilaria Elia ,Jared H Rowe ,Sheila Johnson ,Shakchhi Joshi ,Giulia Notarangelo ,Kiran Kurmi ,Sarah Weiss ,Gordon J Freeman ,Arlene H Sharpe ,Marcia C Haigis

SIRT4 is an early regulator of branched-chain amino acid catabolism that promotes adipogenesis

SIRT4 是促进脂肪生成的支链氨基酸分解代谢的早期调节剂

Elma Zaganjor, Haejin Yoon, Jessica B Spinelli, Elizabeth R Nunn, Gaëlle Laurent, Paulina Keskinidis, Suganja Sivaloganathan, Shakchhi Joshi, Giulia Notarangelo, Stacy Mulei, Mathew T Chvasta, Sarah A Tucker, Krystle Kalafut, Robert A H van de Ven, Clary B Clish, Marcia C Haigis

Defective glycosylation and multisystem abnormalities characterize the primary immunodeficiency XMEN disease

糖基化缺陷和多系统异常是原发性免疫缺陷 XMEN 疾病的特征

Juan C Ravell, Mami Matsuda-Lennikov, Samuel D Chauvin, Juan Zou, Matthew Biancalana, Sally J Deeb, Susan Price, Helen C Su, Giulia Notarangelo, Ping Jiang, Aaron Morawski, Chrysi Kanellopoulou, Kyle Binder, Ratnadeep Mukherjee, James T Anibal, Brian Sellers, Lixin Zheng, Tingyan He, Alex B George, 

Mitochondrial Reprogramming Underlies Resistance to BCL-2 Inhibition in Lymphoid Malignancies

线粒体重编程是淋巴系统恶性肿瘤对 BCL-2 抑制产生抗性的基础

Romain Guièze, Vivian M Liu, Daniel Rosebrock, Alexis A Jourdain, María Hernández-Sánchez, Aina Martinez Zurita, Jing Sun, Elisa Ten Hacken, Kaitlyn Baranowski, Philip A Thompson, Jin-Mi Heo, Zachary Cartun, Ozan Aygün, J Bryan Iorgulescu, Wandi Zhang, Giulia Notarangelo, Dimitri Livitz, Shuqiang Li

T Cell Activation Depends on Extracellular Alanine

T细胞活化依赖于细胞外丙氨酸

Noga Ron-Harel ,Jonathan M Ghergurovich ,Giulia Notarangelo ,Martin W LaFleur ,Yoshiki Tsubosaka ,Arlene H Sharpe ,Joshua D Rabinowitz ,Marcia C Haigis

Magnesium transporter 1 (MAGT1) deficiency causes selective defects in N- linked glycosylation and expression of immune-response genes

镁转运蛋白1 (MAGT1) 缺乏会导致N-连接糖基化和免疫应答基因表达的选择性缺陷

Mami Matsuda-Lennikov ,Matthew Biancalana ,Juan Zou ,Juan C Ravell ,Lixin Zheng ,Chrysi Kanellopoulou ,Ping Jiang ,Giulia Notarangelo ,Huie Jing ,Evan Masutani ,Andrew J Oler ,Lisa Renee Olano ,Benjamin L Schulz ,Michael J Lenardo