日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Anandamide Is a Potential Blood Biomarker of Hermansky-Pudlak Syndrome Pulmonary Fibrosis

花生四烯酸乙醇胺是赫曼斯基-普德拉克综合征肺纤维化的潜在血液生物标志物

Cinar, Resat; Basu, Abhishek; Arif, Muhammad; Park, Joshua K; Zawatsky, Charles N; Zuo, Ben Long G; Zuo, Mei Xing G; O'Brien, Kevin J; Behan, Molly; Introne, Wendy; Iyer, Malliga R; Gahl, William A; Malicdan, May Christine V; Gochuico, Bernadette R

A phase 1 study evaluating the safety, tolerability, and pharmacokinetics of the porcupine inhibitor, AZD5055

一项评估豪猪蛋白酶抑制剂 AZD5055 的安全性、耐受性和药代动力学的 1 期研究

Zhou, Xiao-Hong; Prothon, Susanne; L, Engin; Ferrari, Nicola; Hezaveh, Kebria; Liu, Zhi; Nemes, Szilard; Almquist, Joachim; Williams, Michael L; Sobande, Olami; Gottfridsson, Christer; Gochuico, Bernadette R; Platt, Adam; Brohawn, Zach; Belvisi, Maria G; Goldwater, Ronald; Hornberg, Ellinor; Owen, Caroline A

Impairment of Renal Function in Hermansky-Pudlak Syndrome

Hermansky-Pudlak综合征的肾功能损害

Yokoyama, Tadafumi; O'Brien, Kevin J; Franklin, Tesiya M; Zuo, Ben Long G; Zuo, Mei Xing G; Merideth, Melissa A; Introne, Wendy J; Gochuico, Bernadette R

Insights into the renal pathophysiology in Hermansky-Pudlak syndrome-1 from urinary extracellular vesicle proteomics and a new mouse model.

通过尿液细胞外囊泡蛋白质组学和新的小鼠模型,深入了解 Hermansky-Pudlak 综合征-1 的肾脏病理生理学

Maynard Dawn M, Gochuico Bernadette R, Pri Chen Hadass, Bleck Christopher K E, Zerfas Patricia M, Introne Wendy J, Gahl William A, Malicdan May C V

Ectopic Expansion of Pulmonary Vasculature in Fibrotic Lung Disease and Lung Adenocarcinoma Marked by Proangiogenic COL15A1+ Endothelial Cells.

纤维化肺病和肺腺癌中肺血管异位扩张,以促血管生成 COL15A1+ 内皮细胞为标志

Engelbrecht Eric, Kooistra Tristan, Burg Nathalie, Hariri Lida, Nguyen Trong, Brazee Patricia, Hla Timothy, Gochuico Bernadette R, Knipe Rachel S

Elevated blood anandamide levels in acute COVID-19 pneumonia with respiratory failure

急性 COVID-19 肺炎伴呼吸衰竭患者血液中花生四烯酸乙醇胺(anandamide)水平升高

Basu, Abhishek; Pommerolle, Lenny; Arif, Muhammad; Meliton, Angelo Y; Udofia, Inemesit; Wu, David; Mutlu, Gökhan M; Gochuico, Bernadette R; Summer, Ross; Adegunsoye, Ayodeji; Burnham, Ellen L; Cinar, Resat

Type 2 innate immunity promotes the development of pulmonary fibrosis in Hermansky-Pudlak syndrome

型先天免疫促进 Hermansky-Pudlak 综合征肺纤维化的发展

Parand Sorkhdini, Kiran Klubock-Shukla, Selena Sheth, Dongqin Yang, Alina Xiaoyu Yang, Carmelissa Norbrun, Wendy J Introne, Bernadette R Gochuico, Yang Zhou

Quantification of Proteus syndrome-associated lung disease

普罗特斯综合征相关肺病的定量分析

Ours, Christopher A; Buser, Anna; Hodges, Mia B; Chen, Marcus Y; Sapp, Julie C; Gochuico, Bernadette R; Biesecker, Leslie G

Anandamide is an Early Blood Biomarker of Hermansky-Pudlak Syndrome Pulmonary Fibrosis

花生四烯酸乙醇胺是赫曼斯基-普德拉克综合征肺纤维化的早期血液生物标志物

Cinar, Resat; Basu, Abhishek; Arif, Muhammad; Park, Joshua K; Zawatsky, Charles N; Zuo, Ben Long G; Zuo, Mei Xing G; O'Brien, Kevin J; Behan, Molly; Introne, Wendy; Iyer, Malliga R; Gahl, William A; Malicdan, May Christine V; Gochuico, Bernadette R

Investigating Determinants and Evaluating Deep Learning Training Approaches for Visual Acuity in Foveal Hypoplasia

研究影响黄斑发育不全患者视力的决定因素并评估深度学习训练方法

Malechka, Volha V; Duong, Dat; Bordonada, Keyla D; Turriff, Amy; Blain, Delphine; Murphy, Elizabeth; Introne, Wendy J; Gochuico, Bernadette R; Adams, David R; Zein, Wadih M; Brooks, Brian P; Huryn, Laryssa A; Solomon, Benjamin D; Hufnagel, Robert B