日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

A Refined Method for Micro-Scale Blood Cystine Measurement in Preclinical Cystinosis Models

一种用于临床前胱氨酸病模型中微量血液胱氨酸测量的改进方法

De Leo, Ester; Cairoli, Sara; Rega, Laura Rita; Colucci, Manuela; Taranta, Anna; Goffredo, Bianca Maria; Emma, Francesco; Bellomo, Francesco

Use of gastroscopy in the management of pediatric toxic ingestions: insights from a decade of experience - a retrospective study

胃镜在儿童中毒管理中的应用:十年经验的启示——一项回顾性研究

Marano, Marco; Di Meglio, Lavinia; Pisani, Mara; Goffredo, Bianca Maria; Olita, Carla; Faraci, Simona; Rea, Francesca; Perdichizzi, Salvatore; Zampini, Giorgio; David, Piero; Torroni, Filippo

A Rare Intruder: Neonatal Meningoencephalitis by Edwardsiella tarda Requiring Systemic and Intrathecal Antibiotics and Repeated Neurosurgery

罕见入侵者:由迟缓爱德华氏菌引起的新生儿脑膜脑炎,需要全身和鞘内抗生素治疗以及反复神经外科手术

De Rose, Domenico Umberto; Martini, Ludovica; Campi, Francesca; Longo, Daniela; Guarnera, Alessia; Lucignani, Giulia; Conti, Marta; Santisi, Alessandra; Nucci, Carlotta Ginevra; Esposito, Giacomo; Romani, Lorenza; Bernaschi, Paola; Goffredo, Bianca Maria; Scarpelli, Gianfranco; Lancella, Laura; Dotta, Andrea; Ronchetti, Maria Paola

Prenatal Elexacaftor/Tezacaftor/Ivacaftor for Fetal Meconium Ileus: First Italian Case and Narrative Overview of the Emerging Evidence

产前使用Elexacaftor/Tezacaftor/Ivacaftor治疗胎儿胎粪性肠梗阻:首例意大利病例及新兴证据概述

Boni, Alessandra; Vassallo, Chiara; Ciciriello, Fabiana; Cristiani, Luca; Mancini, Alessandro; Zucaro, Luigi; Graziano, Sonia; Goffredo, Bianca Maria; Alghisi, Federico; Raponi, Massimiliano; Fabietti, Isabella; On Behalf Of Opbg Cf Pregnancy And Fetal Therapy Multidisciplinary Group

Measurement of Anti-TNF Biologics in Serum Samples of Pediatric Patients: Comparison of Enzyme-Linked Immunosorbent Assay (ELISA) with a Rapid and Automated Fluorescence-Based Lateral Flow Immunoassay

儿童患者血清样本中抗TNF生物制剂的测定:酶联免疫吸附试验(ELISA)与快速自动化荧光侧向层析免疫测定法的比较

Rossi, Chiara; Simeoli, Raffaele; Angelino, Giulia; Cairoli, Sara; Bracci, Fiammetta; Knafelz, Daniela; Romeo, Erminia Francesca; Faraci, Simona; Tarantino, Giusyda; Mancini, Alessandro; Vitale, Alessia; Vici, Carlo Dionisi; Manzoni, Silvia Magni; De Angelis, Paola; Goffredo, Bianca Maria

Development and Validation of a New LC-MS/MS Method for Simultaneous Quantification of Ivacaftor, Tezacaftor and Elexacaftor Plasma Levels in Pediatric Cystic Fibrosis Patients

开发和验证一种新的LC-MS/MS方法,用于同时定量分析儿童囊性纤维化患者血浆中伊伐卡托、替扎卡托和依来卡托的浓度

Mancini, Alessandro; Simeoli, Raffaele; Cristiani, Luca; Cairoli, Sara; Ciciriello, Fabiana; Boni, Alessandra; Alghisi, Federico; Rossi, Chiara; Antonetti, Giacomo; Vici, Carlo Dionisi; Fiocchi, Alessandro Giovanni; Cutrera, Renato; Goffredo, Bianca Maria

Use of lorazepam for analgosedation during mechanical ventilation in pediatric intensive care

在儿科重症监护室中,使用劳拉西泮进行机械通气镇痛镇静

Healy, Paul; Marano, Marco; Montibeller, Marcello; Goffredo, Bianca Maria; Pontrelli, Giuseppe; Della Pasqua, Oscar

Ketogenic Diet and Progression of Kidney Disease in Animal Models of Nephropathic Cystinosis.

生酮饮食与肾病性胱氨酸病动物模型肾脏疾病进展的关系

Bellomo Francesco, Pugliese Sara, Cairoli Sara, Krohn Patrick, De Stefanis Cristiano, Raso Roberto, Rega Laura Rita, Taranta Anna, De Leo Ester, Ciolfi Andrea, Cicolani Nicolò, Petrini Stefania, Luciani Alessandro, Goffredo Bianca Maria, Porzio Ottavia, Devuyst Olivier, Dionisi-Vici Carlo, Emma Francesco

Pharmacokinetic Evaluation of Oral Viscous Budesonide in Paediatric Patients with Eosinophilic Oesophagitis in Repaired Oesophageal Atresia

口服粘稠布地奈德治疗食管闭锁修复术后儿童嗜酸性食管炎的药代动力学评价

Simeoli, Raffaele; Lava, Sebastiano A G; Di Deo, Alessandro; Roversi, Marco; Cairoli, Sara; Tambucci, Renato; Rea, Francesca; Malamisura, Monica; Angelino, Giulia; Biondi, Isabella; Simonetti, Alessandra; De Angelis, Paola; Dionisi Vici, Carlo; Rossi, Paolo; Pontrelli, Giuseppe; Della Pasqua, Oscar; Goffredo, Bianca Maria

Father-to-daughter transmission in late-onset OTC deficiency: an underestimated mechanism of inheritance of an X-linked disease

晚发型鸟氨酸氨甲酰转移酶缺乏症的父女遗传:一种被低估的X连锁疾病遗传机制

Siri, Barbara; Olivieri, Giorgia; Lepri, Francesca Romana; Poms, Martin; Goffredo, Bianca Maria; Commone, Anna; Novelli, Antonio; Häberle, Johannes; Dionisi-Vici, Carlo