日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Concerns regarding the safety and efficacy of ES-Cu-Captisol for Menkes disease. Reply

对 ES-Cu-Captisol 治疗 Menkes 病的安全性和有效性存在担忧。回复

Gohil, Vishal M; Petris, Michael J; Palau, Francesc

A First-In-Class Broad Spectrum Inhibitor of Copper Exporting P(1B)-type ATPases

首创的铜输出P(1B)型ATP酶广谱抑制剂

Shanbhag, Vinit C; Anakpeba-Dinguyella, Samuel; Gudekar, Nikita; Conrad, Kristyn; Azubuogu, Chiemerie; Probst, Corinna; Ralle, Martina; Mediavilla, María G; Cricco, Julia A; Garza, Natalie M; Gohil, Vishal M; Peck, Scott; Kumar, Siddhartha; Natarajan, Amarnath; Horadigala-Gamage, Madujika A; Meloni, Gabriele; Singh, Kamal; Petris, Michael J

Elesclomol-copper therapy improves neurodevelopment in two children with Menkes disease

艾司洛莫尔-铜疗法改善了两名患有门克斯病的儿童的神经发育。

Godoy-Molina, Elena; Serrano, Natalia L; Jiménez-González, Aquilina; Villaronga, Miquel; Marqués Pérez-Bryan, Rosa M; Varela-Fernández, Rubén; Lotz-Esquivel, Stephanie; Hevia Tuñón, Alba; Trivedi, Prachi P; Horn, Nina; Standing, Joseph F; Mangas-Sanjuan, Víctor; Capdevila, Mercè; Mateos, Aurora; Broun, Denis; Lutsenko, Svetlana; Medina-Rivera, Ines; Artuch, Rafael; Jou, Cristina; Roldán, Mònica; Arango-Sancho, Pedro; Saez-Villafañe, Mónica; Ortiz-de-Urbina, Juan J; Pieras-López, Angela; Duero, Marta; Farré, Rosa; Pijuan, Jordi; Hoenicka, Janet; Sacchettini, James C; Petris, Michael J; Gohil, Vishal M; Palau, Francesc

Nanomaterial-induced mitochondrial biogenesis enhances intercellular mitochondrial transfer efficiency

纳米材料诱导的线粒体生物合成增强了细胞间线粒体转移效率

Soukar, John; Singh, Kanwar Abhay; Aviles, Ari; Hargett, Sarah; Kaur, Harman; Foster, Samantha; Roy, Shounak; Zhao, Feng; Gohil, Vishal M; Singh, Irtisha; Gaharwar, Akhilesh K

Proteolytic regulation of mitochondrial magnesium channel by m-AAA protease and prohibitin complex.

m-AAA蛋白酶和prohibitin复合物对线粒体镁通道的蛋白水解调节

Joshi Alaumy, Stanfield Rachel A, Spletter Andrew T, Gohil Vishal M

Elesclomol rescues mitochondrial copper deficiency in disease models without triggering cuproptosis

Elesclomol 可在不诱导铜凋亡的情况下,挽救疾病模型中的线粒体铜缺乏症。

Zulkifli, Mohammad; Maremanda, Krishna P; Okonkwo, Adriana U; Farid, Ifrah; Gohil, Vishal M

Mitochondrial dysfunction and lipid dysregulation in yeast lacking phosphatidylserine

缺乏磷脂酰丝氨酸的酵母中线粒体功能障碍和脂质代谢紊乱

Joshi, Alaumy; Baker, Zakery N; Stanfield, Rachel A; Kalafatis, Dimitris T; Pagliarini, David J; Gohil, Vishal M

Mechanism of Action and Translational Potential of (S)-Meclizine in Preemptive Prophylaxis Against Stroke

(S)-美克洛嗪在预防卒中中的作用机制及转化潜力

Lee, Jeong Hyun; Gohil, Vishal M; Heidari, Pedram; Seidel, Jessica L; Zulkifli, Mohammad; Wei, Ying; Ji, Yuhua; Daneshmand, Ali; Mahmood, Umar; Clish, Clary B; Mootha, Vamsi K; Ayata, Cenk

Mitochondrial copper in human genetic disorders

人类遗传疾病中的线粒体铜

Garza, Natalie M; Swaminathan, Abhinav B; Maremanda, Krishna P; Zulkifli, Mohammad; Gohil, Vishal M

Mitochondrial phospholipid metabolism in health and disease

线粒体磷脂代谢在健康和疾病中的作用

Joshi, Alaumy; Richard, Travis H; Gohil, Vishal M