日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Factor H-related 1 and heparan sulfate architecture contribute to complement dysregulation in C3 glomerulopathy.

因子 H 相关 1 和硫酸乙酰肝素结构导致 C3 肾小球病中的补体失调

Slagle Amanda K, Ghiringhelli Borsa Nicolo, Wang Kai, Taylor Amanda O, Meyer Nicole C, Jones Michael B, Walls William D, Nelson Angela F M, Roberts Sarah M, Sun Mingyao, Goicoechea de Jorge Elena, Rodriguez de Cordoba Santiago, Jalal Diana I, Nester Carla M, Zhang Yuzhou, Smith Richard J H

Development and Characterization of Novel ELISAs for the Specific Quantification of the Factor H-Related Proteins 2, 3, 4, and 5

开发和表征用于特异性定量因子H相关蛋白2、3、4和5的新型ELISA方法

van Rossum, Mara; Veuskens, Bert R J; Brouwer, Mieke C; van Mierlo, Gerard; Lucientes-Continente, Laura; Goicoechea de Jorge, Elena; Uzonyi, Barbara; Matola, Alexandra T; Józsi, Mihály; Müller, Günter; Meter-Arkema, Anita M; Poppelaars, Felix; Pauly, Diana; Pouw, Richard B; Toonen, Erik J M

The Factor H protein family: The switchers of the complement alternative pathway

因子H蛋白家族:补体旁路途径的转换者

Lucientes-Continente, Laura; Márquez-Tirado, Bárbara; Goicoechea de Jorge, Elena

Clinical Profiles and Patterns of Kidney Disease Progression in C3 Glomerulopathy

C3肾小球病患者的临床特征和肾脏疾病进展模式

Caravaca-Fontán, Fernando; Cavero, Teresa; Díaz-Encarnación, Montserrat; Cabello, Virginia; Ariceta, Gema; Quintana, Luis F; Marco, Helena; Barros, Xoana; Ramos, Natalia; Rodríguez-Mendiola, Nuria; Cruz, Sonia; Fernández-Juárez, Gema; Rodríguez, Adela; Pérez de José, Ana; Rabasco, Cristina; Rodado, Raquel; Fernández, Loreto; Pérez-Gómez, Vanessa; Ávila, Ana; Bravo, Luis; Espinosa, Natalia; Allende, Natalia; Sanchez de la Nieta, Maria Dolores; Rodríguez, Eva; Rivas, Begoña; Melgosa, Marta; Huerta, Ana; Miquel, Rosa; Mon, Carmen; Fraga, Gloria; de Lorenzo, Alberto; Draibe, Juliana; González, Fayna; Shabaka, Amir; López-Rubio, Maria Esperanza; Fenollosa, María Ángeles; Martín-Penagos, Luis; Da Silva, Iara; Titos, Juana Alonso; Rodríguez de Córdoba, Santiago; Goicoechea de Jorge, Elena; Praga, Manuel

Development and validation of a nomogram to predict kidney survival at baseline in patients with C3 glomerulopathy

开发和验证用于预测C3肾小球病患者基线肾脏存活率的列线图

Caravaca-Fontán, Fernando; Rivero, Marta; Cavero, Teresa; Díaz-Encarnación, Montserrat; Cabello, Virginia; Ariceta, Gema; Quintana, Luis F; Marco, Helena; Barros, Xoana; Ramos, Natalia; Rodríguez-Mendiola, Nuria; Cruz, Sonia; Fernández-Juárez, Gema; Rodríguez, Adela; Pérez de José, Ana; Rabasco, Cristina; Rodado, Raquel; Fernández, Loreto; Pérez-Gómez, Vanessa; Ávila, Ana; Bravo, Luis; Espinosa, Natalia; Allende, Natalia; Sanchez de la Nieta, Maria Dolores; Rodríguez, Eva; Olea, Teresa; Melgosa, Marta; Huerta, Ana; Miquel, Rosa; Mon, Carmen; Fraga, Gloria; de Lorenzo, Alberto; Draibe, Juliana; González, Fayna; Shabaka, Amir; López-Rubio, Maria Esperanza; Fenollosa, María Ángeles; Martín-Penagos, Luis; Da Silva, Iara; Alonso Titos, Juana; Rodríguez de Córdoba, Santiago; Goicoechea de Jorge, Elena; Praga, Manuel

Mycophenolate Mofetil in C3 Glomerulopathy and Pathogenic Drivers of the Disease

吗替麦考酚酯在C3肾小球病及其致病驱动因素中的作用

Caravaca-Fontán, Fernando; Díaz-Encarnación, Montserrat M; Lucientes, Laura; Cavero, Teresa; Cabello, Virginia; Ariceta, Gema; Quintana, Luis F; Marco, Helena; Barros, Xoana; Ramos, Natalia; Rodríguez-Mendiola, Nuria; Cruz, Sonia; Fernández-Juárez, Gema; Rodríguez, Adela; Pérez de José, Ana; Rabasco, Cristina; Rodado, Raquel; Fernández, Loreto; Pérez Gómez, Vanessa; Ávila, Ana I; Bravo, Luis; Lumbreras, Javier; Allende, Natalia; Sanchez de la Nieta, Maria Dolores; Rodríguez, Eva; Olea, Teresa; Melgosa, Marta; Huerta, Ana; Miquel, Rosa; Mon, Carmen; Fraga, Gloria; de Lorenzo, Alberto; Draibe, Juliana; Cano-Megías, Marta; González, Fayna; Shabaka, Amir; López-Rubio, Maria Esperanza; Fenollosa, María Ángeles; Martín-Penagos, Luis; Da Silva, Iara; Alonso Titos, Juana; Rodríguez de Córdoba, Santiago; Goicoechea de Jorge, Elena; Praga, Manuel

Factor H Competitor Generated by Gene Conversion Events Associates with Atypical Hemolytic Uremic Syndrome

由基因转换事件产生的H因子竞争者与非典型溶血性尿毒综合征相关

Goicoechea de Jorge, Elena; Tortajada, Agustín; García, Sheila Pinto; Gastoldi, Sara; Merinero, Héctor Martín; García-Fernández, Jesús; Arjona, Emilia; Cao, Mercedes; Remuzzi, Giuseppe; Noris, Marina; Rodríguez de Córdoba, Santiago

A hybrid CFHR3-1 gene causes familial C3 glomerulopathy

CFHR3-1 杂合基因导致家族性 C3 肾小球病

Malik, Talat H; Lavin, Peter J; Goicoechea de Jorge, Elena; Vernon, Katherine A; Rose, Kirsten L; Patel, Mitali P; de Leeuw, Marcel; Neary, John J; Conlon, Peter J; Winn, Michelle P; Pickering, Matthew C

Acute presentation and persistent glomerulonephritis following streptococcal infection in a patient with heterozygous complement factor H-related protein 5 deficiency

一名患有杂合子补体因子H相关蛋白5缺陷的患者,在链球菌感染后出现急性发作和持续性肾小球肾炎。

Vernon, Katherine A; Goicoechea de Jorge, Elena; Hall, Angela E; Fremeaux-Bacchi, Veronique; Aitman, Timothy J; Cook, H Terence; Hangartner, Robert; Koziell, Ania; Pickering, Matthew C