Changes in sputum viscoelastic properties and airway inflammation in primary ciliary dyskinesia are comparable to cystic fibrosis on elexacaftor/tezacaftor/ivacaftor therapy
原发性纤毛运动障碍患者的痰液粘弹性改变和气道炎症与接受依来卡托/替扎卡托/伊伐卡托治疗的囊性纤维化患者相似。
期刊:European Respiratory Journal
影响因子:21
doi:10.1183/13993003.00616-2025
Nussstein, Hannah; Urbantat, Ruth M; Fentker, Kerstin; Loewe, Aditi; Duerr, Julia; Haji, Mohamed; Doellinger, Felix; Stahl, Mirjam; Graeber, Simon Y; Gradzielski, Michael; Röhmel, Jobst; Mertins, Philipp; Schaupp, Laura; Mall, Marcus A