日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Acute Pulmonary Exacerbation Phenotypes in Patients with Cystic Fibrosis

囊性纤维化患者的急性肺部加重表型

Carter, Suzanne C; Franciosi, Alessandro N; O'Shea, Kate M; O'Carroll, Orla M; Sharma, Ashutosh; Bell, Aoife; Keogan, Brian; O'Reilly, Paul; Coughlan, Suzie; Law, Sheonagh M; Gray, Robert D; Hisert, Katherine B; Singh, Pradeep K; Cooke, Gordon; Grogan, Brenda; De Gascun, Cillian F; Gallagher, Charles G; Nicholson, Trevor T; Quon, Bradley S; McKone, Edward F

Ivacaftor modifies cystic fibrosis neutrophil phenotype in subjects with R117H residual function CFTR mutations

伊伐卡托可改变携带R117H残余功能CFTR突变患者的囊性纤维化中性粒细胞表型

Hardisty, Gareth R; Law, Sheonagh M; Carter, Suzanne; Grogan, Brenda; Singh, Pradeep K; McKone, Edward F; Gray, Robert D

CFTR Modulator Therapy Enhances Peripheral Blood Monocyte Contributions to Immune Responses in People With Cystic Fibrosis.

CFTR调节剂疗法可增强囊性纤维化患者外周血单核细胞对免疫反应的贡献

Hisert Katherine B, Birkland Timothy P, Schoenfelt Kelly Q, Long Matthew E, Grogan Brenda, Carter Suzanne, Liles W Conrad, McKone Edward F, Becker Lev, Manicone Anne M, Gharib Sina A

Ivacaftor decreases monocyte sensitivity to interferon-γ in people with cystic fibrosis

伊伐卡托可降低囊性纤维化患者单核细胞对干扰素-γ的敏感性

Hisert, Katherine B; Birkland, Timothy P; Schoenfelt, Kelly Q; Long, Matthew E; Grogan, Brenda; Carter, Suzanne; Liles, W Conrad; McKone, Edward F; Becker, Lev; Manicone, Anne M

Ivacaftor-induced sweat chloride reductions correlate with increases in airway surface liquid pH in cystic fibrosis

伊伐卡托引起的汗液氯化物减少与囊性纤维化患者气道表面液体pH值的升高相关

Abou Alaiwa, Mahmoud H; Launspach, Jan L; Grogan, Brenda; Carter, Suzanne; Zabner, Joseph; Stoltz, David A; Singh, Pradeep K; McKone, Edward F; Welsh, Michael J

Restoring Cystic Fibrosis Transmembrane Conductance Regulator Function Reduces Airway Bacteria and Inflammation in People with Cystic Fibrosis and Chronic Lung Infections

恢复囊性纤维化跨膜传导调节因子功能可减少囊性纤维化和慢性肺部感染患者的气道细菌和炎症

Hisert, Katherine B; Heltshe, Sonya L; Pope, Christopher; Jorth, Peter; Wu, Xia; Edwards, Rachael M; Radey, Matthew; Accurso, Frank J; Wolter, Daniel J; Cooke, Gordon; Adam, Ryan J; Carter, Suzanne; Grogan, Brenda; Launspach, Janice L; Donnelly, Seamas C; Gallagher, Charles G; Bruce, James E; Stoltz, David A; Welsh, Michael J; Hoffman, Lucas R; McKone, Edward F; Singh, Pradeep K

Acute administration of ivacaftor to people with cystic fibrosis and a G551D-CFTR mutation reveals smooth muscle abnormalities

对患有囊性纤维化和 G551D-CFTR 突变的患者进行伊伐卡托急性给药,可发现平滑肌异常。

Adam, Ryan J; Hisert, Katherine B; Dodd, Jonathan D; Grogan, Brenda; Launspach, Janice L; Barnes, Janel K; Gallagher, Charles G; Sieren, Jered P; Gross, Thomas J; Fischer, Anthony J; Cavanaugh, Joseph E; Hoffman, Eric A; Singh, Pradeep K; Welsh, Michael J; McKone, Edward F; Stoltz, David A

Ivacaftor-Induced Proteomic Changes Suggest Monocyte Defects May Contribute to the Pathogenesis of Cystic Fibrosis

伊伐卡托诱导的蛋白质组学变化提示单核细胞缺陷可能与囊性纤维化的发病机制有关

Hisert, Katherine B; Schoenfelt, Kelly Q; Cooke, Gordon; Grogan, Brenda; Launspach, Jan L; Gallagher, Charles G; Donnelly, Seamas C; Welsh, Michael J; Singh, Pradeep K; McKone, Edward F; Becker, Lev