日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Distinct neuronal alterations distinguish two subtypes of sporadic Creutzfeldt-Jakob disease with shared dysfunctional pathways.

散发性克雅氏病的两个亚型具有不同的神经元改变,但它们都存在共同的功能障碍通路。

Williams Katie, Groveman Bradley R, Foliaki Simote T, Race Brent, Hay Arielle, Walters Ryan O, Thomas Tina, Zanusso Gianluigi, Carroll James A, Haigh Cathryn L

Oligosaccharyltransferase (OST) complex inhibition effectively treats rodent and human prions

寡糖基转移酶(OST)复合物抑制剂可有效治疗啮齿动物和人类朊病毒感染。

Beauchemin, Kathryn S; Kun, Judit; Groveman, Bradley; Williams, Katie; Salerno, Francesca; Francomacaro, Lisa M; Robison, Patrick; Haigh, Cathryn L; Supattapone, Surachai

Brain-Only Versus GI-Only Synucleinopathy: A Comprehensive Autopsy Study With Both IHC and SAA

仅累及脑部与仅累及胃肠道的突触核蛋白病:一项结合免疫组化和血清淀粉样蛋白A的综合尸检研究

Orru, Christina D; Beach, Thomas G; Adler, Charles H; Shill, Holly A; Driver-Dunckley, Erika; Mehta, Shyamal H; Atri, Alireza; Lorenzini, Ileana; Qiji, Sanaria H; Intorcia, Anthony J; Hughson, Andrew G; Groveman, Bradley R; King, Samantha; Alam, Parvez; Parveen, Sabiha; Vascellari, Sarah; Caughey, Byron; Serrano, Geidy E

Prion-induced ferroptosis is facilitated by RAC3.

RAC3 促进朊病毒诱导的铁死亡

Peng Hao, Pfeiffer Susanne, Varynskyi Borys, Qiu Marina, Srinark Chanikarn, Jin Xiang, Zhang Xin, Williams Katie, Groveman Bradley R, Foliaki Simote T, Race Brent, Thomas Tina, Chen Chengxuan, Müller Constanze, Kovács Krisztina, Arzberger Thomas, Momma Stefan, Haigh Cathryn L, Schick Joel A

Infecting human brain organoids with FFI or sCJD preserves prion traits regardless of host genotype

用FFI或sCJD感染人脑类器官,无论宿主基因型如何,都能保留朊病毒的特征。

Groveman, B R; Foliaki, S T; Williams, K; Orrù, C D; Race, B; Zanusso, G; Haigh, C L

Lack of Transmission of Chronic Wasting Disease Prions to Human Cerebral Organoids

慢性消耗性疾病朊病毒无法传播至人类脑类器官

Bradley R Groveman, Katie Williams, Brent Race, Simote Foliaki, Tina Thomas, Andrew G Hughson, Ryan O Walters, Wenquan Zou, Cathryn L Haigh

Limbic system synaptic dysfunctions associated with prion disease onset

与朊病毒疾病发病相关的边缘系统突触功能障碍

Simote T Foliaki, Bradley R Groveman, Emmett A Dews, Katie Williams, Hadil El Soufi, Benjamin Schwarz, Jacqueline M Leung, Christine A Schneider, Cindi L Schwartz, Eric Bohrnsen, Cole D Kimzey, Brent Race, Cathryn L Haigh

Sensitive detection of pathological seeds of α-synuclein, tau and prion protein on solid surfaces

对固体表面上α-突触核蛋白、tau蛋白和朊病毒蛋白的病理种子进行灵敏检测

Orrú, Christina D; Groveman, Bradley R; Hughson, Andrew G; Barrio, Tomás; Isiofia, Kachi; Race, Brent; Ferreira, Natalia C; Gambetti, Pierluigi; Schneider, David A; Masujin, Kentaro; Miyazawa, Kohtaro; Ghetti, Bernardino; Zanusso, Gianluigi; Caughey, Byron

Diagnosis and treatment of growth hormone deficiency in children on the ketogenic diet: A case series

生酮饮食治疗儿童生长激素缺乏症的诊断和治疗:病例系列研究

Groveman, Sue; Klepper, Joerg; Liesenkötter, Klaus-Peter; Grimberg, Adda; Bergqvist, A G Christina

Sodium hypochlorite inactivation of human CJD prions

次氯酸钠对人类克雅氏病朊病毒的灭活作用

Groveman, Bradley R; Race, Brent; Hughson, Andrew G; Haigh, Cathryn L