日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Upregulated beta-defensin-1 in murine and human biliary atresia associates with human native liver survival

小鼠和人类胆道闭锁中β-防御素-1表达上调与人类天然肝脏存活率相关

Slavetinsky, Christoph; Basenach, Jule; Damm, Pascal; Bertolini, Caterina; Holweg, Maximilian; Hartleif, Steffen; Hilberath, Johannes; Singer, Stephan; Petersen, Claus; Fuchs, Jörg; Sturm, Ekkehard

Endoscopic retrograde cholangiopancreatography as a diagnostic key tool for biliary atresia: feasibility, safety and accuracy in neonates with cholestatic liver disease

内镜逆行胰胆管造影术作为胆道闭锁诊断的关键工具:在胆汁淤积性肝病新生儿中的可行性、安全性和准确性

Hartleif, Steffen; Esser, Michael; Fuchs, Jörg; Götz, Martin; Graepler, Florian; Hilberath, Johannes; Illhardt, Toni; Kirschner, Hans-Joachim; Malek, Nisar P; Manger, Andreas; Schäfer, Jürgen; Schempf, Ulrike; Singer, Stephan; Slavetinsky, Christoph; Stüker, Dietmar; Tsiflikas, Ilias; Wichmann, Dörte; Sturm, Ekkehard; Werner, Christoph R

Paediatric acute liver failure: A prospective, nationwide, population-based surveillance study in Germany

德国一项前瞻性、全国性、基于人群的儿童急性肝衰竭监测研究

Lenz, Dominic; Abdulaziz, Muhammad; Peters, Bianca; Wagner, Matias; Schlieben, Lea D; Corman, Victor M; Baumann, Ulrich; Bufler, Philip; Dattner, Tal; Ganschow, Rainer; Genzel, Kristin; Hammann, Nicole; Hartleif, Steffen; Hegen, Bianca; Henning, Stephan; Hoerning, André; Jankofsky, Martin; Junge, Norman; Kathemann, Simone; Knoppke, Birgit; Kohl-Sobania, Martina; Laass, Martin; Lainka, Elke; Lurz, Eberhard; Melter, Michael; Müller, Hanna; Pilic, Denisa; Ries, Markus; Schiefele, Lisa; Schwerd, Tobias; Sturm, Ekkehard; Wegner, Mechtild; Urschitz, Michael S; Garbade, Sven F; Wenning, Daniel; Drosten, Christian; Fichtner, Alexander; Kölker, Stefan; Hoffmann, Georg F; Prokisch, Holger; Staufner, Christian

Incidence, management and outcomes in hepatic artery complications after paediatric liver transplantation: protocol of the retrospective, international, multicentre HEPATIC Registry

儿童肝移植术后肝动脉并发症的发生率、处理和预后:回顾性、国际、多中心 HEPATIC 注册研究方案

Li, Weihao; van der Doef, Hubert P J; Wildhaber, Barbara E; Marra, Paolo; Bravi, Michela; Pinelli, Domenico; Minetto, Julia; Dip, Marcelo; Sierre, Sergio; de Santibañes, Martin; Ardiles, Victoria; Uno, Jimmy Walker; Hardikar, Winita; Bates, Sue; Goh, Lynette; Aldrian, Denise; Seisenbacher, Jonathan; Vogel, Georg F; Neto, Joao Seda; Antunes da Fonseca, Eduardo; Magalhães Costa, Carolina; Ferreira, Cristina T; Nader, Luiza S; Farina, Marco A; Dajani, Khaled Z; Parente, Alessandro; Bigam, David L; Liang, Ting-Bo; Bai, Xueli; Zhang, Wei; Gonsorčíková, Lucie; Froněk, Jiří; Bohuš, Šimon; Franchi-Abella, Stéphanie; Gonzales, Emmanuel; Guérin, Florent; Junge, Norman; Baumann, Ulrich; Richter, Nicolas; Hartleif, Steffen; Sturm, Ekkehard; Rajakannu, Muthukumarassamy; Palaniappan, Kumar; Rela, Mohamed; Pawaria, Arti; Rajakrishnan, Haritha; Surendran, Sudhindran; Kumar, Mukesh; Agarwal, Shaleen; Gupta, Subhash; Asthana, Sonal; Bandewar, Vaishnavi; Raichurkar, Karthik; Spada, Marco; Monti, Lidia; Alterio, Tommaso; Yanagi, Yusuke; Uchida, Hajime; Komine, Ryuji; Evans, Helen; Carr-Boyd, Peter; Duncan, David; Stefanowicz, Marek; Latka-Grot, Julita; Kolesnik, Adam; Broering, Dieter C; Raptis, Dimitri A; Ann H Marquez, Kris; Mali, Vidyadhar; Aw, Marion; Beretta, Marisa; Van der Schyff, Francisca; Quintero-Bernabeu, Jesús; Mercadal-Hally, Maria; Larrarte K, Mauricio; Andres, Ane M; Hernandez-Oliveros, Francisco; Frauca, Esteban; Casswall, Thomas; Jorns, Carl; Delle, Martin; Gupte, Girish; Sharif, Khalid; McGuirk, Simon; Superina, Riccardo; Caicedo, Juan Carlos; Jaramillo, Catalina; Bitterfeld, Leandra; Kastenberg, Zachary; Shah, Amit A; Domenick, Bryanna; Acord, Michael R; Mazariegos, George V; Soltys, Kyle; DiNorcia, Joseph; Antala, Swanti; Florman, Sander S; Buchholz, Bettina M; Herden, Uta; Fischer, Lutz; Dierckx, Rudi A J O; Hartog, Hermien; Bokkers, Reinoud P H

Genotype-phenotype relationships of truncating mutations, p.E297G and p.D482G in bile salt export pump deficiency

胆汁酸输出泵缺陷中截断突变 p.E297G 和 p.D482G 的基因型-表型关系

Felzen, Antonia; van Wessel, Daan B E; Gonzales, Emmanuel; Thompson, Richard J; Jankowska, Irena; Shneider, Benjamin L; Sokal, Etienne; Grammatikopoulos, Tassos; Kadaristiana, Agustina; Jacquemin, Emmanuel; Spraul, Anne; Lipiński, Patryk; Czubkowski, Piotr; Rock, Nathalie; Shagrani, Mohammad; Broering, Dieter; Nicastro, Emanuele; Kelly, Deirdre; Nebbia, Gabriella; Arnell, Henrik; Fischler, Björn; Hulscher, Jan B F; Serranti, Daniele; Arikan, Cigdem; Polat, Esra; Debray, Dominique; Lacaille, Florence; Goncalves, Cristina; Hierro, Loreto; Muñoz Bartolo, Gema; Mozer-Glassberg, Yael; Azaz, Amer; Brecelj, Jernej; Dezsőfi, Antal; Calvo, Pier Luigi; Grabhorn, Enke; Hartleif, Steffen; van der Woerd, Wendy J; Kamath, Binita M; Wang, Jian-She; Li, Liting; Durmaz, Özlem; Kerkar, Nanda; Jørgensen, Marianne Hørby; Fischer, Ryan; Jimenez-Rivera, Carolina; Alam, Seema; Cananzi, Mara; Laverdure, Noemie; Ferreira, Cristina Targa; Guerrero, Felipe Ordoñez; Wang, Heng; Sency, Valerie; Kim, Kyung Mo; Chen, Huey-Ling; de Carvalho, Elisa; Fabre, Alexandre; Bernabeu, Jesus Quintero; Zellos, Aglaia; Alonso, Estella M; Sokol, Ronald J; Suchy, Frederick J; Loomes, Kathleen M; McKiernan, Patrick J; Rosenthal, Philip; Turmelle, Yumirle; Horslen, Simon; Schwarz, Kathleen; Bezerra, Jorge A; Wang, Kasper; Hansen, Bettina E; Verkade, Henkjan J

Multisystem inflammation and susceptibility to viral infections in human ZNFX1 deficiency

人类 ZNFX1 缺乏症可导致多系统炎症和病毒感染易感性

Vavassori, Stefano; Chou, Janet; Faletti, Laura Eva; Haunerdinger, Veronika; Opitz, Lennart; Joset, Pascal; Fraser, Christopher J; Prader, Seraina; Gao, Xianfei; Schuch, Luise A; Wagner, Matias; Hoefele, Julia; Maccari, Maria Elena; Zhu, Ying; Elakis, George; Gabbett, Michael T; Forstner, Maria; Omran, Heymut; Kaiser, Thomas; Kessler, Christina; Olbrich, Heike; Frosk, Patrick; Almutairi, Abduarahman; Platt, Craig D; Elkins, Megan; Weeks, Sabrina; Rubin, Tamar; Planas, Raquel; Marchetti, Tommaso; Koovely, Danil; Klämbt, Verena; Soliman, Neveen A; von Hardenberg, Sandra; Klemann, Christian; Baumann, Ulrich; Lenz, Dominic; Klein-Franke, Andreas; Schwemmle, Martin; Huber, Michael; Sturm, Ekkehard; Hartleif, Steffen; Häffner, Karsten; Gimpel, Charlotte; Brotschi, Barbara; Laube, Guido; Güngör, Tayfun; Buckley, Michael F; Kottke, Raimund; Staufner, Christian; Hildebrandt, Friedhelm; Reu-Hofer, Simone; Moll, Solange; Weber, Achim; Kaur, Hundeep; Ehl, Stephan; Hiller, Sebastian; Geha, Raif; Roscioli, Tony; Griese, Matthias; Pachlopnik Schmid, Jana

Safety and Tolerance of Donor-Derived Mesenchymal Stem Cells in Pediatric Living-Donor Liver Transplantation: The MYSTEP1 Study

儿童活体肝移植中供体来源间充质干细胞的安全性和耐受性:MYSTEP1 研究

Hartleif, Steffen; Schumm, Michael; Döring, Michaela; Mezger, Markus; Lang, Peter; Dahlke, Marc H; Riethmüller, Joachim; Königsrainer, Alfred; Handgretinger, Rupert; Nadalin, Silvio; Sturm, Ekkehard