日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Plastin 3 rescues cell surface translocation and activation of TrkB in spinal muscular atrophy

Plastin 3 挽救脊髓性肌萎缩症中的细胞表面易位和 TrkB 的激活

Luisa Hennlein, Hanaa Ghanawi #, Florian Gerstner #, Eduardo Palominos García, Ezgi Yildirim, Lena Saal-Bauernschubert, Mehri Moradi, Chunchu Deng, Teresa Klein, Silke Appenzeller, Markus Sauer, Michael Briese, Christian Simon, Michael Sendtner, Sibylle Jablonka

Nifedipine Ameliorates Cellular Differentiation Defects of Smn-Deficient Motor Neurons and Enhances Neuromuscular Transmission in SMA Mice

硝苯地平改善 Smn 缺陷运动神经元的细胞分化缺陷并增强 SMA 小鼠的神经肌肉传递

Rocio Tejero, Mohammad Alsakkal, Luisa Hennlein, Ana M Lopez-Cabello, Sibylle Jablonka, Lucia Tabares

Impaired dynamic interaction of axonal endoplasmic reticulum and ribosomes contributes to defective stimulus-response in spinal muscular atrophy

轴突内质网和核糖体的动态相互作用受损导致脊髓性肌萎缩症的刺激反应缺陷

Chunchu Deng, Sebastian Reinhard, Luisa Hennlein, Janna Eilts, Stefan Sachs, Sören Doose, Sibylle Jablonka, Markus Sauer, Mehri Moradi, Michael Sendtner

Therapy development for spinal muscular atrophy: perspectives for muscular dystrophies and neurodegenerative disorders

脊髓性肌萎缩症的治疗研发:对肌营养不良症和神经退行性疾病的展望

Jablonka, Sibylle; Hennlein, Luisa; Sendtner, Michael

Loss of full-length hnRNP R isoform impairs DNA damage response in motoneurons by inhibiting Yb1 recruitment to chromatin

全长 hnRNP R 亚型的缺失会抑制 Yb1 募集到染色质,从而损害运动神经元的 DNA 损伤反应

Hanaa Ghanawi, Luisa Hennlein, Abdolhossein Zare, Jakob Bader, Saeede Salehi, Daniel Hornburg, Changhe Ji, Rajeeve Sivadasan, Carsten Drepper, Felix Meissner, Matthias Mann, Sibylle Jablonka, Michael Briese, Michael Sendtner

Interaction of 7SK with the Smn complex modulates snRNP production

7SK 与 Smn 复合物的相互作用调节 snRNP 的产生

Changhe Ji, Jakob Bader, Pradhipa Ramanathan, Luisa Hennlein, Felix Meissner, Sibylle Jablonka, Matthias Mann, Utz Fischer, Michael Sendtner, Michael Briese

Dynamic remodeling of ribosomes and endoplasmic reticulum in axon terminals of motoneurons

运动神经元轴突末端核糖体和内质网的动态重塑

Chunchu Deng, Mehri Moradi, Sebastian Reinhard, Changhe Ji, Sibylle Jablonka, Luisa Hennlein, Patrick Lüningschrör, Sören Doose, Markus Sauer, Michael Sendtner