日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Hyperactivation of mTORC1 signaling mediates folliculin deficiency-induced pulmonary cyst formation in Birt-Hogg-Dubé syndrome

在Birt-Hogg-Dubé综合征中,mTORC1信号通路过度激活介导了滤泡蛋白缺乏引起的肺囊肿形成。

Cao, Ke; Chen, Hui; Chu, Ling; Wang, Hong-Jun; Zhang, Jianhua; Luo, Yongfeng; Chiu, Joanne; Khabibullin, Damir; Alesi, Nicola; Thornton, Matthew E; Grubbs, Brendan H; Ataya, Ali; Gupta, Nishant; McCormack, Francis X; Wikenheiser-Brokamp, Kathryn A; Henske, Elizabeth P; Shi, Wei

A Mitochondrial Plasma Proteomic Signature Identifies Metastatic Chromophobe Renal Cell Carcinoma

线粒体血浆蛋白质组学特征可识别转移性嫌色细胞肾细胞癌

Steiner, Clara; Han, Tiegang; Safi, Steven; Bzeih, Wafaa; Mansour, Hadi; Saad, Eddy; Williams, Jessica F; Hirsch, Michelle S; Giri, Vinay K; Ascione, Liliana; Elon, Yehonatan; Dicker, Adam P; Tang, Yan; Choueiri, Toni K; Henske, Elizabeth P; Xu, Wenxin

Tumor-Intrinsic and Microenvironmental Determinants of Impaired Antitumor Immunity in Chromophobe Renal Cell Carcinoma

嗜铬细胞肾细胞癌中肿瘤内在和微环境因素导致抗肿瘤免疫受损

Labaki, Chris; Saad, Eddy; Madsen, Katrine N; Hobeika, Charbel; Bi, Kevin; Alchoueiry, Michel; Camp, Sabrina; Hou, Yue; Bakouny, Ziad; Matar, Sayed; El Ahmar, Nourhan; Nyman, Jackson; Zhang, Long; Priolo, Carmen; Rout, Rishabh; Daou, Melissa; Khabibullin, Damir; Salem, Samer; Schindler, Nicholas; Saliby, Renée Maria; Meli, Kevin; Wells, J Connor; Pimenta, Erica; Takemura, Kosuke; Park, Jihye; Eid, Marc; Semaan, Karl; Fu, Jingxin; Denize, Thomas; El Hajj Chehade, Razane; Machaalani, Marc; Nawfal, Rashad; Khatoun, Wassim Daoud; Saleh, Mustafa; El Masri, Jad; Haddad, Nina Rossa; Xu, Wenxin; McGregor, Bradley A; Hirsch, Michelle S; Xie, Wanling; Heng, Daniel Y C; McDermott, David F; Signoretti, Sabina; Van Allen, Eliezer M; Shukla, Sachet A; Choueiri, Toni K; Henske, Elizabeth P; Braun, David A

Modulation of infiltrating CD206(+) macrophages restricts progression of pulmonary lymphangioleiomyomatosis.

调节浸润的 CD206(+) 巨噬细胞可限制肺淋巴管肌瘤病的进展。

Liu Heng-Jia, Diesler Remi, Chami Joelle, Wu Boxiang, Du Heng, Jin Yue, Daou Melissa, Alesi Nicola, Khabibullin Damir, Leroux Caroline, Cottin Vincent, Cantley Lloyd G, Rudloff Udo, Henske Elizabeth P

Novel treatment strategies for lymphangioleiomyomatosis: a narrative review

淋巴管肌瘤病的新型治疗策略:叙述性综述

Elia, Davide; Harari, Sergio; Fan, Lu; Diesler, Rémi; Henske, Elizabeth P

Heterogeneous origins and functions of lung mesenchymal stromal cells

肺间充质基质细胞的异质性起源和功能

Peng, Danyi; Cao, Ke; Yang, Ruili; Luo, Yongfeng; Chen, Hui; Madala, Satish K; Thornton, Matthew E; Grubbs, Brendan H; Henske, Elizabeth P; Majka, Susan M; Shi, Wei

Targeting FSP1 to induce ferroptosis in chromophobe renal cell carcinoma.

靶向 FSP1 诱导嗜铬细胞肾癌细胞发生铁死亡。

Salem Samer, Han Tiegang, Alchoueiry Michel, Mahmoud Nadine, Bzeih Wafaa, Chami Joelle, Khabibullin Damir, Mansour Hadi, Tang Yan, Ho Thai H, Ubellacker Jessalyn M, Priolo Carmen, Henske Elizabeth P

The Bi-steric Inhibitor RMC-5552 Reduces mTORC1 Signaling and Growth in Lymphangioleiomyomatosis.

双位阻抑制剂 RMC-5552 可降低淋巴管肌瘤病中的 mTORC1 信号传导和生长

Evans Jilly F, Ledwell Owen A, Tang Yan, Rue Ryan, Mukhitov Alexander R, Diesler Rémi, Lin Susan M, Vanka Kanth Swaroop, Basil Maria C, Cantu Edward, Henske Elizabeth P, Krymskaya Vera P

Extracellular vesicles modulate integrin signaling and subcellular energetics to promote pulmonary lymphangioleiomyomatosis metastasis

细胞外囊泡调节整合素信号传导和亚细胞能量代谢,从而促进肺淋巴管肌瘤病转移

Kalvala, Anil Kumar; Silwal, Ashok; Patel, Bhaumik; Kasetti, Apoorva; Shetty, Kirti Rajendra; Markiewski, Jan; Cho, Jun-Hung; Lara, Gerard; Daugherity, Elizabeth; Diesler, Rémi; Pooladanda, Venkatesh; Rueda, Bo R; Henske, Elizabeth Petri; Yu, Jane J; Markiewski, Maciej; Karbowniczek, Magdalena

52: Spatial transcriptomic mapping reveals immune-inflamed niches in sarcomatoid chromophobe renal cell carcinoma

52:空间转录组图谱揭示肉瘤样嫌色细胞肾细胞癌中的免疫炎症微环境

Kunachowicz, Dominika; Król-Kulikowska, Magdalena; Raczycka, Wiktoria; Sleziak, Jakub; Błażejewska, Marta; Kulbacka, Julita; Tang, Yan; Han, Tiegang; Mansour, Hadi; Hirsch, Michelle S; Collins, Katrina; Henske, Elizabeth P