日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Stabilizing a Native Fold of Alpha-Synuclein with Short Helix-Constrained Peptides

利用短螺旋约束肽稳定α-突触核蛋白的天然折叠

Meade, Richard M; Allen, Scott G; Lopez, Amy J; Williams, Christopher; Thomas-Wright, Iona; Heon-Roberts, Rachel; Carey-Wood, Mara; Tang, T M Simon; Sero, Julia E; Hunt, Vicky L; Wade-Martins, Richard; Crump, Matthew P; Mason, Jody M

Formation of seeding-competent α-synuclein aggregates in parkin-deficient iPSC-derived human neurons.

在缺乏帕金蛋白的iPSC衍生的人类神经元中形成具有播种能力的α-突触核蛋白聚集体

Schmidt Sissel Ida, Okarmus Justyna, Madsen Daniel Aghaie, Hansen Julie Schmidt, Gregersen Emil, Gram Hjalte, Winkelmann Lucas S, Oliveira Anderson Souza, Heon-Roberts Rachel, Ryan Brent J, Freude Kristine, Blaabjerg Morten, Jensen Poul Henning, Meyer Morten

CRISPRi: a way to integrate iPSC-derived neuronal models

CRISPRi:一种整合iPSC衍生神经元模型的方法

Franks, Sarah N J; Heon-Roberts, Rachel; Ryan, Brent J

Post-translational proteomics platform identifies neurite outgrowth impairments in Parkinson's disease GBA-N370S dopamine neurons

翻译后蛋白质组学平台揭示帕金森病GBA-N370S多巴胺神经元神经突生长受损

Helle Bogetofte ,Brent J Ryan ,Pia Jensen ,Sissel I Schmidt ,Dana L E Vergoossen ,Mike B Barnkob ,Lisa N Kiani ,Uroosa Chughtai ,Rachel Heon-Roberts ,Maria Claudia Caiazza ,William McGuinness ,Ricardo Márquez-Gómez ,Jane Vowles ,Fiona S Bunn ,Janine Brandes ,Peter Kilfeather ,Jack P Connor ,Hugo J R Fernandes ,Tara M Caffrey ,Morten Meyer ,Sally A Cowley ,Martin R Larsen ,Richard Wade-Martins

Post-translational proteomics platform identifies neurite outgrowth impairments in Parkinson's disease GBA-N370S dopamine neurons

翻译后蛋白质组学平台揭示帕金森病GBA-N370S多巴胺神经元神经突生长受损

Helle Bogetofte,Brent J Ryan,Pia Jensen,Sissel I Schmidt,Dana L E Vergoossen,Mike B Barnkob,Lisa N Kiani,Uroosa Chughtai,Rachel Heon-Roberts,Maria Claudia Caiazza,William McGuinness,Ricardo Márquez-Gómez,Jane Vowles,Fiona S Bunn,Janine Brandes,Peter Kilfeather,Jack P Connor,Hugo J R Fernandes,Tara M Caffrey,Morten Meyer,Sally A Cowley,Martin R Larsen,Richard Wade-Martins  0

Mitochondrial dysfunction and mitophagy defects in LRRK2-R1441C Parkinson's disease models

LRRK2-R1441C 帕金森病模型中的线粒体功能障碍和线粒体自噬缺陷

Matthew G Williamson, Marta Madureira, William McGuinness, Rachel Heon-Roberts, Elliot D Mock, Kalina Naidoo, Kaitlyn M L Cramb, Maria-Claudia Caiazza, Ana B Malpartida, Martha Lavelle, Katrina Savory, Stewart W Humble, Ryan Patterson, John B Davis, Natalie Connor-Robson, Brent J Ryan, Richard Wade-

Glucosamine amends CNS pathology in mucopolysaccharidosis IIIC mouse expressing misfolded HGSNAT

葡萄糖胺可改善表达错误折叠 HGSNAT 的粘多糖贮积症 IIIC 小鼠的中枢神经系统病理

Xuefang Pan #, Mahsa Taherzadeh #, Poulomee Bose, Rachel Heon-Roberts, Annie L A Nguyen, TianMeng Xu, Camila Pará, Yojiro Yamanaka, David A Priestman, Frances M Platt, Shaukat Khan, Nidhi Fnu, Shunji Tomatsu, Carlos R Morales, Alexey V Pshezhetsky

Identification of bioactive metabolites in human iPSC-derived dopaminergic neurons with PARK2 mutation: Altered mitochondrial and energy metabolism

PARK2突变的人类iPSC衍生多巴胺能神经元中生物活性代谢物的鉴定:线粒体和能量代谢的改变

Okarmus, Justyna; Havelund, Jesper F; Ryding, Matias; Schmidt, Sissel I; Bogetofte, Helle; Heon-Roberts, Rachel; Wade-Martins, Richard; Cowley, Sally A; Ryan, Brent J; Færgeman, Nils J; Hyttel, Poul; Meyer, Morten