Discovery of Autophagy Modulators that Increase I1061T NPC1 Expression and Promote Cholesterol Efflux in Niemann-Pick Type C Patient-Derived Fibroblasts
发现可增加 I1061T NPC1 表达并促进尼曼-匹克 C 型患者来源成纤维细胞胆固醇外流的自噬调节剂
期刊:ACS Chemical Biology
影响因子:3.8
doi:10.1021/acschembio.6c00039
Salkovski, Maryna; Arrieche Suarez, Andrea; Gao, Qiwen; Hippman, Ryan S; Petros, Zoe A; Korkmaz-Vaisys, Melissa A; Gerlach, Erica M; Alvarado-Cartagena, Yaneris M; Nguyen, Thu T A; Pavlinov, Ivan; Ilnytska, Olga; Storch, Judith; Cologna, Stephanie M; Aldrich, Leslie N
成纤维细胞
NPC1
代谢
Autophagy
细胞生物学
自噬