日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Click Chemistry Enables [(89)Zr]Zr-DOTA Radioimmunoconjugation for Theranostic (89)Zr-immunoPET

点击化学实现[(89)Zr]Zr-DOTA放射免疫偶联,用于治疗诊断(89)Zr免疫PET

Imura, Ryota; Jang, Jaewoong; Ozeki, Atsuko Nakanishi; Takahashi, Hiroyuki; Ida, Hiroyuki; Wada, Youichiro; Kumakura, Yoshitaka; Akimitsu, Nobuyoshi

Adverse Events in Pediatric Inpatients: The Japan Adverse Event Study

儿科住院患者不良事件:日本不良事件研究

Sakuma, Mio; Ohta, Yoshinori; Takeuchi, Jiro; Yuza, Yuki; Ida, Hiroyuki; Bates, David W; Morimoto, Takeshi

Allele frequency of pathogenic variants causing acid sphingomyelinase deficiency and Gaucher disease in the general Japanese population

日本普通人群中导致酸性鞘磷脂酶缺乏症和戈谢病的致病变异等位基因频率

Sako, Shuhei; Oishi, Kimihiko; Ida, Hiroyuki; Imagawa, Eri

Venglustat combined with imiglucerase for neurological disease in adults with Gaucher disease type 3: the LEAP trial

Venglustat联合imiglucerase治疗成人戈谢病3型神经系统疾病:LEAP试验

Schiffmann, Raphael; Cox, Timothy M; Dedieu, Jean-François; Gaemers, Sebastiaan J M; Hennermann, Julia B; Ida, Hiroyuki; Mengel, Eugen; Minini, Pascal; Mistry, Pramod; Musholt, Petra B; Scott, David; Sharma, Jyoti; Peterschmitt, M Judith

Erratum: Hematopoietic stem cell gene therapy ameliorates CNS involvement in murine model of GM1-gangliosidosis

更正:造血干细胞基因疗法可改善GM1神经节苷脂病小鼠模型的中枢神经系统受累情况。

Tsunogai, Toshiki; Ohashi, Toya; Shimada, Yohta; Higuchi, Takashi; Kimura, Ayaka; Watabe, Ayako M; Kato, Fusao; Ida, Hiroyuki; Kobayashi, Hiroshi

Hematopoietic stem cell gene therapy ameliorates CNS involvement in murine model of GM1-gangliosidosis.

造血干细胞基因治疗可改善GM1神经节苷脂病小鼠模型的中枢神经系统受累情况

Tsunogai Toshiki, Ohashi Toya, Shimada Yohta, Higuchi Takashi, Kimura Ayaka, Watabe Ayako M, Kato Fusao, Ida Hiroyuki, Kobayashi Hiroshi

An observational study to investigate the relationship between plasma glucosylsphingosine (lyso-Gb1) concentration and treatment outcomes of patients with Gaucher disease in Japan

一项观察性研究旨在探讨日本戈谢病患者血浆葡萄糖鞘氨醇(lyso-Gb1)浓度与治疗结果之间的关系

Ida, Hiroyuki; Watanabe, Yuko; Sagara, Rieko; Inoue, Yoichi; Fernandez, Jovelle

The role of native T1 values on the evaluation of cardiac manifestation in Japanese Fabry disease patients

原生T1值在日本法布里病患者心脏表现评估中的作用

Anan, Ikuko; Sakuma, Toru; Fukuro, Eiko; Morimoto, Satoshi; Nojiri, Ayumi; Kawai, Makoto; Sakurai, Ken; Kobayashi, Masahisa; Kobayashi, Hiroshi; Ida, Hiroyuki; Ohashi, Toya; Yoshimura, Michihiro; Eto, Yoshikatsu; Hongo, Kenichi

Re-Evaluations of Zr-DFO Complex Coordination Chemistry for the Estimation of Radiochemical Yields and Chelator-to-Antibody Ratios of (89)Zr Immune-PET Tracers

重新评估 Zr-DFO 复合物配位化学在 (89)Zr 免疫 PET 示踪剂放射化学产率和螯合剂与抗体比率估算中的应用

Imura, Ryota; Ida, Hiroyuki; Sasaki, Ichiro; Ishioka, Noriko S; Watanabe, Shigeki

Long-term safety and effectiveness of velaglucerase alfa in Gaucher disease: 6-year interim analysis of a post-marketing surveillance in Japan

维拉葡糖苷酶α治疗戈谢病的长期安全性和有效性:日本上市后监测的6年中期分析

Sagara, Rieko; Ishigaki, Masahide; Otsuka, Manami; Murayama, Kei; Ida, Hiroyuki; Fernandez, Jovelle