日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Dissection of metabolic reprogramming in polycystic kidney disease reveals coordinated rewiring of bioenergetic pathways

多囊肾病代谢重编程的解剖揭示了生物能量通路的协调重组

Christine Podrini, Isaline Rowe, Roberto Pagliarini, Ana S H Costa, Marco Chiaravalli, Ivano Di Meo, Hyunho Kim, Gianfranco Distefano, Valeria Tiranti, Feng Qian, Diego di Bernardo, Christian Frezza, Alessandra Boletta

2-Deoxy-d-Glucose Ameliorates PKD Progression

2-脱氧-D-葡萄糖可改善 PKD 进展

Marco Chiaravalli, Isaline Rowe, Valeria Mannella, Giacomo Quilici, Tamara Canu, Veronica Bianchi, Antonia Gurgone, Sofia Antunes, Patrizia D'Adamo, Antonio Esposito, Giovanna Musco, Alessandra Boletta

Defective glucose metabolism in polycystic kidney disease identifies a new therapeutic strategy

多囊肾病的葡萄糖代谢缺陷确定了一种新的治疗策略

Isaline Rowe, Marco Chiaravalli, Valeria Mannella, Valeria Ulisse, Giacomo Quilici, Monika Pema, Xuewen W Song, Hangxue Xu, Silvia Mari, Feng Qian, York Pei, Giovanna Musco, Alessandra Boletta

Polycystin-1 binds Par3/aPKC and controls convergent extension during renal tubular morphogenesis

多囊蛋白-1 与 Par3/aPKC 结合并控制肾小管形态发生过程中的收敛延伸

Maddalena Castelli, Manila Boca, Marco Chiaravalli, Harini Ramalingam, Isaline Rowe, Gianfranco Distefano, Thomas Carroll, Alessandra Boletta

Nephrocystin-1 forms a complex with polycystin-1 via a polyproline motif/SH3 domain interaction and regulates the apoptotic response in mammals

肾囊素-1 通过多脯氨酸基序/SH3 结构域相互作用与多囊蛋白-1 形成复合物,并调节哺乳动物的凋亡反应

Claas Wodarczyk, Gianfranco Distefano, Isaline Rowe, Massimiliano Gaetani, Barbara Bricoli, Mordi Muorah, Andrea Spitaleri, Valeria Mannella, Piero Ricchiuto, Monika Pema, Maddalena Castelli, Ariel E Casanova, Luca Mollica, Manuela Banzi, Manila Boca, Corinne Antignac, Sophie Saunier, Giovanna Musco

Polycystin-1 regulates extracellular signal-regulated kinase-dependent phosphorylation of tuberin to control cell size through mTOR and its downstream effectors S6K and 4EBP1

多囊蛋白-1通过mTOR及其下游效应物S6K和4EBP1调节细胞外信号调节激酶依赖性块茎蛋白磷酸化以控制细胞大小

Gianfranco Distefano, Manila Boca, Isaline Rowe, Claas Wodarczyk, Li Ma, Klaus B Piontek, Gregory G Germino, Pier Paolo Pandolfi, Alessandra Boletta

A novel mouse model reveals that polycystin-1 deficiency in ependyma and choroid plexus results in dysfunctional cilia and hydrocephalus

一种新型小鼠模型揭示了室管膜和脉络丛中多囊蛋白-1的缺乏会导致纤毛功能障碍和脑积水

Claas Wodarczyk, Isaline Rowe, Marco Chiaravalli, Monika Pema, Feng Qian, Alessandra Boletta