日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Developmental venous anomalies are a genetic primer for cerebral cavernous malformations

发育性静脉异常是脑海绵状血管畸形的遗传引物

Daniel A Snellings, Romuald Girard, Rhonda Lightle, Abhinav Srinath, Sharbel Romanos, Ying Li, Chang Chen, Aileen A Ren, Mark L Kahn, Issam A Awad, Douglas A Marchuk

PIK3CA and CCM mutations fuel cavernomas through a cancer-like mechanism

PIK3CA 和 CCM 突变通过类似癌症的机制促进海绵状血管瘤的发生发展。

Aileen A Ren # ,Daniel A Snellings # ,Yourong S Su ,Courtney C Hong ,Marco Castro ,Alan T Tang ,Matthew R Detter ,Nicholas Hobson ,Romuald Girard ,Sharbel Romanos ,Rhonda Lightle ,Thomas Moore ,Robert Shenkar ,Christian Benavides ,M Makenzie Beaman ,Helge Müller-Fielitz ,Mei Chen ,Patricia Mericko ,Jisheng Yang ,Derek C Sung ,Michael T Lawton ,J Michael Ruppert ,Markus Schwaninger ,Jakob Körbelin ,Michael Potente ,Issam A Awad ,Douglas A Marchuk ,Mark L Kahn

Longitudinal transcriptomics define the stages of myeloid activation in the living human brain after intracerebral hemorrhage

纵向转录组学定义了脑出血后活体人脑中髓系细胞活化的各个阶段

Michael H Askenase ,Brittany A Goods ,Hannah E Beatty ,Arthur F Steinschneider ,Sofia E Velazquez ,Artem Osherov ,Margaret J Landreneau ,Shaina L Carroll ,Tho B Tran ,Victor S Avram ,Riley S Drake ,G James Gatter ,Jordan A Massey ,Saravanan S Karuppagounder ,Rajiv R Ratan ,Charles C Matouk ,Kevin N Sheth ,Wendy C Ziai ,Adrian R Parry-Jones ,Issam A Awad ,Mario Zuccarello ,Richard E Thompson ,Jesse Dawson ,Daniel F Hanley ,J Christopher Love ,Alex K Shalek ,Lauren H Sansing

Abortive intussusceptive angiogenesis causes multi-cavernous vascular malformations

套叠性血管生成失败导致多发性海绵状血管畸形

Wenqing Li, Virginia Tran, Iftach Shaked, Belinda Xue, Thomas Moore, Rhonda Lightle, David Kleinfeld, Issam A Awad, Mark H Ginsberg

Leukocyte dynamics after intracerebral hemorrhage in a living patient reveal rapid adaptations to tissue milieu

活体患者脑出血后白细胞动态变化揭示了其对组织微环境的快速适应

Brittany A Goods ,Michael H Askenase ,Erica Markarian ,Hannah E Beatty ,Riley S Drake ,Ira Fleming ,Jonathan H DeLong ,Naomi H Philip ,Charles C Matouk ,Issam A Awad ,Mario Zuccarello ,Daniel F Hanley ,J Christopher Love ,Alex K Shalek ,Lauren H Sansing

Novel Murine Models of Cerebral Cavernous Malformations

小鼠脑海绵状畸形的新型模型

Matthew R Detter, Robert Shenkar, Christian R Benavides, Catherine A Neilson, Thomas Moore, Rhonda Lightle, Nicholas Hobson, Le Shen, Ying Cao, Romuald Girard, Dongdong Zhang, Erin Griffin, Carol J Gallione, Issam A Awad, Douglas A Marchuk

Antibodies in cerebral cavernous malformations react with cytoskeleton autoantigens in the lesional milieu

脑海绵状畸形中的抗体与病变环境中的细胞骨架自身抗原发生反应

Dongdong Zhang, Andrew J Kinloch, Abhinav Srinath, Robert Shenkar, Romuald Girard, Rhonda Lightle, Thomas Moore, Janne Koskimäki, Azam Mohsin, Julián Carrión-Penagos, Sharbel Romanos, Le Shen, Marcus R Clark, Changbin Shi, Issam A Awad

Cerebral cavernous malformations form an anticoagulant vascular domain in humans and mice

脑海绵状畸形在人类和小鼠中形成抗凝血管域

Miguel Alejandro Lopez-Ramirez, Angela Pham, Romuald Girard, Tine Wyseure, Preston Hale, Atsuki Yamashita, Janne Koskimäki, Sean Polster, Laleh Saadat, Ignacio A Romero, Charles T Esmon, Frederic Lagarrigue, Issam A Awad, Laurent O Mosnier, Mark H Ginsberg

The cerebral cavernous malformation disease causing gene KRIT1 participates in intestinal epithelial barrier maintenance and regulation

脑海绵状血管瘤致病基因KRIT1参与肠上皮屏障的维持和调节

Yitang Wang, Ye Li, Jinjing Zou, Sean P Polster, Rhonda Lightle, Thomas Moore, Matthew Dimaano, Tong-Chuan He, Christopher R Weber, Issam A Awad, Le Shen

Endothelial TLR4 and the microbiome drive cerebral cavernous malformations

内皮细胞TLR4和微生物群驱动脑海绵状血管畸形

Alan T Tang ,Jaesung P Choi ,Jonathan J Kotzin ,Yiqing Yang ,Courtney C Hong ,Nicholas Hobson ,Romuald Girard ,Hussein A Zeineddine ,Rhonda Lightle ,Thomas Moore ,Ying Cao ,Robert Shenkar ,Mei Chen ,Patricia Mericko ,Jisheng Yang ,Li Li ,Ceylan Tanes ,Dmytro Kobuley ,Urmo Võsa ,Kevin J Whitehead ,Dean Y Li ,Lude Franke ,Blaine Hart ,Markus Schwaninger ,Jorge Henao-Mejia ,Leslie Morrison ,Helen Kim ,Issam A Awad ,Xiangjian Zheng ,Mark L Kahn