日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Discovery of Sulfonamide Pantothenate Kinase Activators and Elucidation of the Role of Isoform Selectivity in Cellular Pantothenate Kinase Activation

磺胺类泛酸激酶激活剂的发现及同工酶选择性在细胞泛酸激酶激活中的作用阐明

Coker, Ashton L; Tangallapally, Rajendra; Yun, Mi-Kyung; Subramanian, Chitra; Jayasinghe, Thilina; Miller, Karen; Edwards, Anne; Frank, Matthew; Jackowski, Suzanne; Rock, Charles O; White, Stephen W; Lee, Richard E

PCYT2-regulated lipid biosynthesis is critical to muscle health and ageing

PCYT2调控的脂质生物合成对肌肉健康和衰老至关重要。

Cikes, Domagoj; Elsayad, Kareem; Sezgin, Erdinc; Koitai, Erika; Torma, Ferenc; Orthofer, Michael; Yarwood, Rebecca; Heinz, Leonhard X; Sedlyarov, Vitaly; Miranda, Nasser Darwish; Taylor, Adrian; Grapentine, Sophie; Al-Murshedi, Fathiya; Abot, Anne; Weidinger, Adelheid; Kutchukian, Candice; Sanchez, Colline; Cronin, Shane J F; Novatchkova, Maria; Kavirayani, Anoop; Schuetz, Thomas; Haubner, Bernhard; Haas, Lisa; Hagelkruys, Astrid; Jackowski, Suzanne; Kozlov, Andrey V; Jacquemond, Vincent; Knauf, Claude; Superti-Furga, Giulio; Rullman, Eric; Gustafsson, Thomas; McDermot, John; Lowe, Martin; Radak, Zsolt; Chamberlain, Jeffrey S; Bakovic, Marica; Banka, Siddharth; Penninger, Josef M

Proton magnetic resonance spectroscopy detects cerebral metabolic derangement in a mouse model of brain coenzyme a deficiency

质子磁共振波谱法可检测脑辅酶A缺乏症小鼠模型中的脑代谢紊乱。

Li, Yanan; Steinberg, Jeffrey; Coleman, Zane; Wang, Shubo; Subramanian, Chitra; Li, Yimei; Patay, Zoltan; Akers, Walter; Rock, Charles O; Jackowski, Suzanne; Bagga, Puneet

Human pantothenate kinase 4 is a pseudo-pantothenate kinase.

人类泛酸激酶 4 是一种假泛酸激酶

Yao Jiangwei, Subramanian Chitra, Rock Charles O, Jackowski Suzanne

Proposed Therapies for Pantothenate-Kinase-Associated Neurodegeneration

泛酸激酶相关神经退行性疾病的拟议疗法

Jackowski, Suzanne

Excess coenzyme A reduces skeletal muscle performance and strength in mice overexpressing human PANK2

过量的辅酶A会降低过表达人PANK2的小鼠的骨骼肌功能和力量。

Corbin, Deborah R; Rehg, Jerold E; Shepherd, Danielle L; Stoilov, Peter; Percifield, Ryan J; Horner, Linda; Frase, Sharon; Zhang, Yong-Mei; Rock, Charles O; Hollander, John M; Jackowski, Suzanne; Leonardi, Roberta

Correction of a genetic deficiency in pantothenate kinase 1 using phosphopantothenate replacement therapy

利用磷酸泛酸替代疗法纠正泛酸激酶 1 的基因缺陷

Zano, Stephen P; Pate, Caroline; Frank, Matthew; Rock, Charles O; Jackowski, Suzanne

Cancer-associated isocitrate dehydrogenase mutations inactivate NADPH-dependent reductive carboxylation

癌症相关的异柠檬酸脱氢酶突变会使NADPH依赖的还原羧化作用失活。

Leonardi, Roberta; Subramanian, Chitra; Jackowski, Suzanne; Rock, Charles O

The specialized unfolded protein response of B lymphocytes: ATF6α-independent development of antibody-secreting B cells.

B淋巴细胞的特殊未折叠蛋白反应:抗体分泌B细胞的ATF6α非依赖性发育

Aragon Ileana V, Barrington Robert A, Jackowski Suzanne, Mori Kazutoshi, Brewer Joseph W

Compartmentalization of mammalian pantothenate kinases

哺乳动物泛酸激酶的区室化

Alfonso-Pecchio, Adolfo; Garcia, Matthew; Leonardi, Roberta; Jackowski, Suzanne