日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

American College of Rheumatology Guidance Statement for Diagnosis and Management of VEXAS Developed by the International VEXAS Working Group Expert Panel

美国风湿病学会关于VEXAS诊断和治疗的指导声明,由国际VEXAS工作组专家组制定

Mekinian, Arsene; Georgin-Lavialle, Sophie; Ferrada, Marcela A; Savic, Sinisa; Koster, Matthew J; Kosmider, Olivier; Comont, Thibault; Heiblig, Mael; Arostegui, Juan I; Bosco, Annmarie; Bourguiba, Rim; Calvo, Katherine R; Cargo, Catherine; Cattaneo, Chiara; Chasset, François; Coelho, Henrique; Campochiaro, Corrado; Crisafulli, Francesca; Ducharme-Benard, Stephanie; Faria, Raquel; Franceschini, Franco; Frassi, Micol; Groarke, Emma M; Gurnari, Carmelo; Hakobyan, Yervand; Jamilloux, Yvan; Jurcut, Ciprian; Kirino, Yohei; Kulasekararaj, Austin; Kunimoto, Hiroyoshi; Madigan, Lauren M; Mann, Heřman F; Marvisi, Chiara; Milchert, Marcin; Morais, Sara; Sockel, Katja; Muratore, Francesco; Nakajima, Hideaki; Patnaik, Mrinal M; Regadas, Luísa; Robin, Marie; Rutgers, Abraham; Salvarani, Carlo; Sammel, Anthony M; Seebach, Joerg; Sujobert, Pierre; Tomelleri, Alessandro; Urbanski, Geoffrey; Vandergheynst, Frédéric; Vieira, Romana; Viswanatha, David S; Więsik-Szewczyk, Ewa; Diral, Elisa; Terrier, Benjamin; Patel, Bhavisha A; Fenaux, Pierre; Grayson, Peter C; Beck, David B

Clustering reveals diagnostic overlap between Still's disease and a hyperinflammatory subset of seronegative rheumatoid arthritis

聚类分析揭示了斯蒂尔病与血清阴性类风湿关节炎高炎症亚型之间的诊断重叠

Mercier-Guery, Alexandre; El-Jammal, Thomas; El-Nayef, Nour; Massy, Emmanuel; Fournier, Nicolas; Sève, Pascal; Confavreux, Cyrille; Jamilloux, Yvan; Coury, Fabienne

Myeloid neoplasm inspired intensive therapy in VEXAS syndrome: A single-centre experience

髓系肿瘤促使VEXAS综合征患者接受强化治疗:单中心经验

Heiblig, Maël; Plesa, Adriana; Tantot, Juliet; Jamilloux, Yvan; Labussière-Wallet, Hélène; Sujobert, Pierre

EULAR/PReS recommendations for the diagnosis and management of Still's disease, comprising systemic juvenile idiopathic arthritis and adult-onset Still's disease

EULAR/PReS关于斯蒂尔病(包括全身型幼年特发性关节炎和成人斯蒂尔病)诊断和治疗的建议

Fautrel, Bruno; Mitrovic, Stéphane; De Matteis, Arianna; Bindoli, Sara; Antón, Jordi; Belot, Alexandre; Bracaglia, Claudia; Constantin, Tamàs; Dagna, Lorenzo; Di Bartolo, Alessandro; Feist, Eugen; Foell, Dirk; Gattorno, Marco; Georgin-Lavialle, Sophie; Giacomelli, Roberto; Grom, Alexei A; Jamilloux, Yvan; Laskari, Katerina; Lazar, Calin; Minoia, Francesca; Nigrovic, Peter A; Oliveira Ramos, Filipa; Ozen, Seza; Quartier, Pierre; Ruscitti, Piero; Sag, Erdal; Savic, Sinisa; Truchetet, Marie-Elise; Vastert, Sebastiaan J; Wilhelmer, Tanita-Christina; Wouters, Carine; Carmona, Loreto; De Benedetti, Fabrizio

Functional diversity of NLRP3 gain-of-function mutants associated with CAPS autoinflammation

与 CAPS 自身炎症相关的 NLRP3 获得功能突变体的功能多样性

Camille Cosson #, Romane Riou #, Danish Patoli, Tingting Niu, Amaury Rey, Marine Groslambert, Charlotte De Rosny, Elodie Chatre, Omran Allatif, Thomas Henry, Fabienne Venet, Florian Milhavet, Guilaine Boursier, Alexandre Belot, Yvan Jamilloux, Etienne Merlin, Agnès Duquesne, Gilles Grateau, Léa Save

Therapeutic impact of basic critical care echocardiography performed by residents after limited training

住院医师经过有限培训后进行的基础重症监护超声心动图检查的治疗效果

Goudelin, Marine; Evrard, Bruno; Donisanu, Roxana; Gonzalez, Céline; Truffy, Christophe; Orabona, Marie; Galy, Antoine; Lapébie, François-Xavier; Jamilloux, Yvan; Vandeix, Elodie; Belcour, Dominique; Hodler, Charles; Ramirez, Lucie; Gagnoud, Rémi; Chapellas, Catherine; Vignon, Philippe

IFN-γ licenses normal and pathogenic ALPK1/TIFA pathway in human monocytes

IFN-γ 激活人单核细胞中正常的和致病性的 ALPK1/TIFA 通路

Amandine Martin ,Solène Caron ,Mélissa Marcotte ,Pauline Bronnec ,Etienne Garneret ,Nora Martel ,Georgina Maalouf ,Pascal Sève ,David Saadoun ,Yvan Jamilloux ,Thomas Henry

The genome of the simultaneously hermaphroditic snail Lymnaea stagnalis reveals an evolutionary expansion of FMRFamide-like receptors

雌雄同体的椎实螺(Lymnaea stagnalis)的基因组揭示了FMRFamide样受体的进化扩张

Koene, J M; Jackson, D J; Nakadera, Y; Cerveau, N; Madoui, M A; Noel, B; Jamilloux, V; Poulain, J; Labadie, K; Da Silva, C; Davison, A; Feng, Z P; Adema, C M; Klopp, C; Aury, J M; Wincker, P; Coutellec, M A

Quantitative Assessment of Vacuolization of Myeloid Precursors in VEXAS Syndrome

VEXAS综合征中髓系前体细胞空泡化的定量评估

Rabut, Audrey; Jasserand, Ludivine; Richard, Camille; Dumas, Cecile; Mestrallet, Fanélie; Bourbon, Estelle; Gerfaud Valentin, Mathieu; Heiblig, Maël; Eveillard, Marion; Jamilloux, Yvan; Sujobert, Pierre

Recurrent Mutations of the Active Adenylation Domain of UBA1 in Atypical Form of VEXAS Syndrome

非典型VEXAS综合征中UBA1活性腺苷酸化结构域的复发性突变

Faurel, Alyx; Heiblig, Maël; Kosmider, Olivier; Cornillon, Jérôme; Boudou, Laurence; Guyotat, Denis; Martignoles, Jean-Alain; Jamilloux, Yvan; Noyel, Pauline; Daguenet, Elisabeth; Faure, Anne-Camille; Sujobert, Pierre; Flandrin-Gresta, Pascale