日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Evolution of the lipidome uncovers early changes in adrenoleukodystrophy human cortical and spinal organoids.

脂质组的演变揭示了肾上腺脑白质营养不良症人类皮质和脊髓类器官的早期变化。

Ferrer Roberto Montoro, Jaspers Yorrick R J, Coveña Nicki, Breeuwsma Nicole, Dijkstra Inge M E, Kempff Julia, Klinken Jan-Bert van, Wortel Joke, van Weering Jan R T, Engelen Marc, Kemp Stephan, Heine Vivi M

Integrated multi-omics mapping of mitochondrial dysfunction and substrate preference in Barth syndrome cardiac tissue

巴特综合征心脏组织线粒体功能障碍和底物偏好的整合多组学分析

Schomakers, Bauke V; Passadouro, Adriana S; Trętowicz, Maria M; Simpson, Pelle J; Jaspers, Yorrick R J; van Weeghel, Michel; Hu, Iman Man; Lamboo, Cathelijne M E; Cloutier, Denise; Byrne, Barry J; van Klinken, Jan Bert; Janssen, Paul M L; Piersma, Sander R; Jimenez, Connie R; Vaz, Frédéric M; Salomons, Gajja S; van der Velden, Jolanda; Houtkooper, Riekelt H; Mosegaard, Signe

Local accumulation of very long-chain PUFA in plexiform layers associates with retinal dysfunction in a mouse model of peroxisomal ACBD5-deficiency

在过氧化物酶体ACBD5缺陷的小鼠模型中,丛状层中极长链多不饱和脂肪酸的局部积累与视网膜功能障碍相关。

Merz, Julia; Müller, Elisabeth; Darwisch, Warda; Fairless, Richard; Wang, Yixin; Vorwald, Silke; Darwisch, Sharau; Curticean, E Ronald; Shao, Feng; Wacker, Irene; Schröder, Rasmus R; Pitzer, Claudia; Schultz, Christian; van Klinken, Jan-Bert; Vaz, Frederic M; Kratzer, Frank; Schwarz, Kathrin; Okun, Jürgen G; Feng, Yuxi; Hopf, Carsten; Islinger, Markus

Altered lipid profile and reduced neuronal support in human induced pluripotent stem cell-derived astrocytes from adrenoleukodystrophy patients

肾上腺脑白质营养不良症患者的人类诱导性多能干细胞衍生的星形胶质细胞脂质谱发生改变,神经元支持减少

Roberto Montoro Ferrer, Yorrick R J Jaspers, Inge M E Dijkstra, Nicole Breeuwsma, Jan-Bert van Klinken, Cato Romero, Marc Engelen, Stephan Kemp, Vivi M Heine

Four-dimensional lipidomics profiling in X-linked adrenoleukodystrophy using trapped ion mobility mass spectrometry

利用离子阱迁移质谱法对X连锁肾上腺脑白质营养不良进行四维脂质组学分析

Jaspers, Yorrick R J; Meyer, Sven W; Pras-Raves, Mia L; Dijkstra, Inge M E; Wever, Eric J M; Dane, Adrie D; van Klinken, Jan-Bert; Salomons, Gajja S; Houtkooper, Riekelt H; Engelen, Marc; Kemp, Stephan; Van Weeghel, Michel; Vaz, Frédéric M

Western diet triggers cardiac dysfunction in heterozygous Mybpc3-targeted knock-in mice: A two-hit model of hypertrophic cardiomyopathy

西方饮食引发杂合 Mybpc3 靶向敲入小鼠的心脏功能障碍:肥厚性心肌病的两次打击模型

Edgar E Nollet, Sila Algül, Max Goebel, Saskia Schlossarek, Nicole N van der Wel, Judith J M Jans, Mark A van de Wiel, Jaco C Knol, Thang V Pham, Sander R Piersma, Richard de Goeij-de Haas, Jill Hermans, Jan Bert van Klinken, Michel van Weeghel, Riekelt H Houtkooper, Lucie Carrier, Connie R Jimenez,

Angiopoietin-like 4 governs diurnal lipoprotein lipase activity in brown adipose tissue

血管生成素样 4 调控棕色脂肪组织中的昼夜脂蛋白脂肪酶活性

Robin van Eenige, Wietse In Het Panhuis, Milena Schönke, Céline Jouffe, Thomas H Devilee, Ricky Siebeler, Trea C M Streefland, Hetty C M Sips, Amanda C M Pronk, Ruben H P Vorderman, Hailiang Mei, Jan Bert van Klinken, Michel van Weeghel, Nina H Uhlenhaut, Sander Kersten, Patrick C N Rensen, Sander K

Spread of infectious agents through the air in complex spaces

传染性病原体在复杂空间内通过空气传播

Eames, Ian; Flór, Jan-Bert

The effect of mirabegron on energy expenditure and brown adipose tissue in healthy lean South Asian and Europid men

米拉贝隆对健康瘦弱的南亚和欧洲男性能量消耗和棕色脂肪组织的影响

Nahon, Kimberly J; Janssen, Laura G M; Sardjoe Mishre, Aashley S D; Bilsen, Manu P; van der Eijk, Jari A; Botani, Kani; Overduin, Lisanne A; Ruiz, Jonatan R; Burakiewicz, Jedrzej; Dzyubachyk, Oleh; Webb, Andrew G; Kan, Hermien E; Berbée, Jimmy F P; van Klinken, Jan-Bert; van Dijk, Ko Willems; van Weeghel, Michel; Vaz, Frédéric M; Coskun, Tamer; Jazet, Ingrid M; Kooijman, Sander; Martinez-Tellez, Borja; Boon, Mariëtte R; Rensen, Patrick C N

Ethyl Pyruvate Increases Post-Ischemic Levels of Mitochondrial Energy Metabolites: A (13)C-Labeled Cerebral Microdialysis Study

丙酮酸乙酯可增加缺血后线粒体能量代谢物的水平:一项(13)C标记脑微透析研究

Nygaard, Kevin H; Havelund, Jesper F; Nielsen, Troels H; Nordström, Carl-Henrik; Færgeman, Nils J; Poulsen, Frantz R; Gramsbergen, Jan Bert; Forsse, Axel