日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

A Computational Framework for Simulating Patient-Specific TMJ Biomechanics Using a Combined Multibody Dynamics and Finite Element Approach

一种利用多体动力学和有限元方法相结合的计算框架,用于模拟患者特异性颞下颌关节生物力学。

Ahmadi, Farhad; Sun, Shuchun; Zhao, Jichao; Chen, Jian; Wilson, Marshall B; Damon, Brooke; Wu, Yongren; Almpani, Konstantinia; Chung, Rachel; Jani, Priyam; Chen, Peng; Slate, Elizabeth H; Lee, Janice S; Sagl, Benedikt; Yao, Hai

Variability, asymmetry and sexual dimorphism in craniofacial anomalies in Loeys-Dietz syndrome 2: geometric morphometric analysis in mice

Loeys-Dietz综合征2型颅面畸形的变异性、不对称性和性别二态性:小鼠几何形态测量分析

Devine, Katelin R; Lynn, Sarah; Jani, Priyam; Keyvanfar, Cyrus; Lamichhane, Bikash; Hanner, Ashleigh S; Dietrich, Catharine; Chung, Rachel S; Frischmeyer-Guerrerio, Pamela A; Almpani, Konstantinia; Duverger, Olivier; Lee, Janice S

Gain-of-function mutations in ALPK1 cause an NF-κB-mediated autoinflammatory disease: functional assessment, clinical phenotyping and disease course of patients with ROSAH syndrome

ALPK1基因功能获得性突变导致NF-κB介导的自身炎症性疾病:ROSAH综合征患者的功能评估、临床表型和疾病进程

Kozycki, Christina Torres; Kodati, Shilpa; Huryn, Laryssa; Wang, Hongying; Warner, Blake M; Jani, Priyam; Hammoud, Dima; Abu-Asab, Mones S; Jittayasothorn, Yingyos; Mattapallil, Mary J; Tsai, Wanxia Li; Ullah, Ehsan; Zhou, Ping; Tian, Xiaoying; Soldatos, Ariane; Moutsopoulos, Niki; Kao-Hsieh, Marie; Heller, Theo; Cowen, Edward W; Lee, Chyi-Chia Richard; Toro, Camilo; Kalsi, Shelley; Khavandgar, Zohreh; Baer, Alan; Beach, Margaret; Long Priel, Debra; Nehrebecky, Michele; Rosenzweig, Sofia; Romeo, Tina; Deuitch, Natalie; Brenchley, Laurie; Pelayo, Eileen; Zein, Wadih; Sen, Nida; Yang, Alexander H; Farley, Gary; Sweetser, David A; Briere, Lauren; Yang, Janine; de Oliveira Poswar, Fabiano; Schwartz, Ida Vanessa D; Silva Alves, Tamires; Dusser, Perrine; Koné-Paut, Isabelle; Touitou, Isabelle; Titah, Salah Mohamed; van Hagen, Petrus Martin; van Wijck, Rogier T A; van der Spek, Peter J; Yano, Hiromi; Benneche, Andreas; Apalset, Ellen M; Jansson, Ragnhild Wivestad; Caspi, Rachel R; Kuhns, Douglas Byron; Gadina, Massimo; Takada, Hidetoshi; Ida, Hiroaki; Nishikomori, Ryuta; Verrecchia, Elena; Sangiorgi, Eugenio; Manna, Raffaele; Brooks, Brian P; Sobrin, Lucia; Hufnagel, Robert B; Beck, David; Shao, Feng; Ombrello, Amanda K; Aksentijevich, Ivona; Kastner, Daniel L

The Role of Type VI Collagen in Alveolar Bone

VI型胶原蛋白在牙槽骨中的作用

Komori, Taishi; Pham, Hai; Jani, Priyam; Perry, Sienna; Wang, Yan; Kilts, Tina M; Li, Li; Young, Marian F

Loeys-Dietz and Shprintzen-Goldberg syndromes: analysis of TGF-β-opathies with craniofacial manifestations using an innovative multimodality method

Loeys-Dietz综合征和Shprintzen-Goldberg综合征:采用创新的多模态方法分析伴有颅面表现的TGF-β病

Almpani, Konstantinia; Liberton, Denise K; Jani, Priyam; Keyvanfar, Cyrus; Mishra, Rashmi; Curry, Natasha; Orzechowski, Pamela; Frischmeyer-Guerrerio, Pamela A; Lee, Janice S

Fibrin is a critical regulator of neutrophil effector function at the oral mucosal barrier.

纤维蛋白是口腔黏膜屏障中中性粒细胞效应功能的关键调节因子

Silva Lakmali M, Doyle Andrew D, Greenwell-Wild Teresa, Dutzan Nicolas, Tran Collin L, Abusleme Loreto, Juang Lih Jiin, Leung Jerry, Chun Elizabeth M, Lum Andrew G, Agler Cary S, Zuazo Carlos E, Sibree Megan, Jani Priyam, Kram Vardit, Martin Daniel, Moss Kevin, Lionakis Michail S, Castellino Francis J, Kastrup Christian J, Flick Matthew J, Divaris Kimon, Bugge Thomas H, Moutsopoulos Niki M

Quantitative Craniofacial Analysis and Generation of Human Induced Pluripotent Stem Cells for Muenke Syndrome: A Case Report

定量颅面分析及人诱导多能干细胞生成治疗穆恩克综合征:病例报告

Kidwai, Fahad K; Mui, Byron W H; Almpani, Konstantinia; Jani, Priyam; Keyvanfar, Cyrus; Iqbal, Kulsum; Paravastu, Sriram S; Arora, Deepika; Orzechowski, Pamela; Merling, Randall K; Mallon, Barbara; Myneni, Vamsee D; Ahmad, Moaz; Kruszka, Paul; Muenke, Maximilian; Woodcock, Jeremiah; Gilman, Jeffrey W; Robey, Pamela G; Lee, Janice S

Case Report: Rare Presentation of Dentin Abnormalities in Loeys-Dietz Syndrome Type I

病例报告:Loeys-Dietz综合征I型中罕见的牙本质异常表现

Jani, Priyam; Duverger, Olivier; Mishra, Rashmi; Frischmeyer-Guerrerio, Pamela A; Lee, Janice S

The peroxisomal disorder spectrum and Heimler syndrome: Deep phenotyping and review of the literature

过氧化物酶体疾病谱系和海姆勒综合征:深入表型分析及文献综述

Daich Varela, Malena; Jani, Priyam; Zein, Wadih M; D'Souza, Precilla; Wolfe, Lynne; Chisholm, Jennifer; Zalewski, Christopher; Adams, David; Warner, Blake M; Huryn, Laryssa A; Hufnagel, Robert B

OPG-Fc treatment partially rescues low bone mass phenotype in mature Bgn/Fmod deficient mice but is deleterious to the young mouse skeleton

OPG-Fc治疗可部分挽救成年Bgn/Fmod缺陷小鼠的低骨量表型,但对幼鼠骨骼有害。

Kram, Vardit; Jani, Priyam; Kilts, Tina M; Li, Li; Chu, Emily Y; Young, Marian F