日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Genetic deletion of transglutaminase 2 does not rescue the phenotypic deficits observed in R6/2 and zQ175 mouse models of Huntington's disease

转谷氨酰胺酶 2 的基因缺失并不能挽救 R6/2 和 zQ175 亨廷顿氏病小鼠模型中观察到的表型缺陷

Liliana B Menalled, Andrea E Kudwa, Steve Oakeshott, Andrew Farrar, Neil Paterson, Igor Filippov, Sam Miller, Mei Kwan, Michael Olsen, Jose Beltran, Justin Torello, Jon Fitzpatrick, Richard Mushlin, Kimberly Cox, Kristi McConnell, Matthew Mazzella, Dansha He, Georgina F Osborne, Rand Al-Nackkash, Gi

Caspase-6 activity in a BACHD mouse modulates steady-state levels of mutant huntingtin protein but is not necessary for production of a 586 amino acid proteolytic fragment

BACHD 小鼠中的 Caspase-6 活性调节突变亨廷顿蛋白的稳态水平,但对于 586 个氨基酸蛋白水解片段的产生并非必需

Juliette Gafni, Theodora Papanikolaou, Francesco Degiacomo, Jennifer Holcomb, Sylvia Chen, Liliana Menalled, Andrea Kudwa, Jon Fitzpatrick, Sam Miller, Sylvie Ramboz, Pasi I Tuunanen, Kimmo K Lehtimäki, X William Yang, Larry Park, Seung Kwak, David Howland, Hyunsun Park, Lisa M Ellerby

Comprehensive behavioral and molecular characterization of a new knock-in mouse model of Huntington's disease: zQ175

亨廷顿氏病新型敲入小鼠模型 zQ175 的全面行为和分子表征

Liliana B Menalled, Andrea E Kudwa, Sam Miller, Jon Fitzpatrick, Judy Watson-Johnson, Nicole Keating, Melinda Ruiz, Richard Mushlin, William Alosio, Kristi McConnell, David Connor, Carol Murphy, Steve Oakeshott, Mei Kwan, Jose Beltran, Afshin Ghavami, Dani Brunner, Larry C Park, Sylvie Ramboz, David