日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Complementary use of autoantibody detection methods facilitates diagnosis of juvenile autoimmune hepatitis and autoimmune sclerosing cholangitis

辅助使用自身抗体检测方法有助于诊断幼年自身免疫性肝炎和自身免疫性硬化性胆管炎

Kirchner, Theresa; Junge, Norman; Henjes, Nicole; Loges, Stephanie; Yuksel, Muhammed; Janczyk, Wojciech; Lalanne, Claudine; Zachou, Kalliopi; Oo, Ye H; Gournay, Jérôme; Pape, Simon; Drenth, Joost Ph; Renand, Amédée; Dalekos, George N; Muratori, Luigi; Socha, Piotr; Arikan, Cigdem; Ma, Yun; Wedemeyer, Heiner; Baumann, Ulrich; Engel, Bastian; Taubert, Richard

ATP8B1 Deficiency Causes Phosphodiesterase 4-Mediated Glucagon Resistance and Impaired Gluconeogenesis in Mouse and Human Liver.

ATP8B1 缺乏导致小鼠和人类肝脏中磷酸二酯酶 4 介导的胰高血糖素抵抗和糖异生受损

Chang Jung-Chin, Panhuis Wietse In Het, Hsu Shu-Hao, Duijst Suzanne, Ho-Mok Kam S, van der Heiden Jolie F, Ying Zhixiong, Erdmann Joris I, Vogel Georg F, Junge Norman, Hartleben Björn, Koelink Pim J, van Dijk Sebastian G, Peng Weng Chuan, Verhoeven Arthur J, Oude Elferink Ronald P J, Chen Huey-Ling, van de Graaf Stan F J, Paulusma Coen C

Hepatic Form of Dihydrolipoamide Dehydrogenase Deficiency (DLDD): Phenotypic Spectrum, Laboratory Findings, and Therapeutic Approaches in 52 Patients

二氢硫辛酰胺脱氢酶缺乏症(DLDD)肝型:52例患者的表型谱、实验室检查结果和治疗方法

Hammann, Nicole; Staufner, Christian; Schlieben, Lea Dewi; Dezsőfi-Gottl, Antal; Feichtinger, René G; Häberle, Johannes; Junge, Norman; Konstantopoulou, Vassiliki; Kopajtich, Robert; McLin, Valérie; Rymen, Daisy; Slavetinsky, Christoph; Sturm, Ekkehard; Mayr, Johannes A; Wagner, Matias; Kölker, Stefan; Prokisch, Holger; Hoffmann, Georg F; Lenz, Dominic

Amyloid precursor protein as a fibrosis marker in infants with biliary atresia.

淀粉样前体蛋白作为胆道闭锁患儿纤维化的标志物

Kamp Jan C, Madadi-Sanjani Omid, Uecker Marie, Werlein Christopher, Neubert Lavinia, Kübler Joachim F, Obed Mikal, Junge Norman, Welte Tobias, Ruwisch Jannik, Jonigk Danny D, Stolk Jan, Vieten Gertrud, Janciauskiene Sabina

Rectal budesonide: A potential game changer after Kasai hepatoportoenterostomy

直肠布地奈德:葛西氏肝门空肠吻合术后的潜在变革者

Langreen, Stefanie; Pauer, Nathalie; Pfister, Eva D; Junge, Norman; Baumann, Ulrich; Madadi-Sanjani, Omid; Petersen, Claus; Dingemann, Jens; Schukfeh, Nagoud

Update on pediatric liver transplantation in Europe 2022: An ELITA-ESPGHAN report

2022年欧洲儿童肝移植最新进展:ELITA-ESPGHAN报告

Junge, Norman; Karam, Vincent; Hartog, Hermien; Adam, Rene; Cailliez, Valérie; Indolfi, Giuseppe; Samyn, Marianne; Stephenne, Xavier; Pop, Tudor Lucian; Waisbourd-Zinman, Orit; Kohlmaier, Benno; Zellos, Aglaia; Mancell, Sara; Gonzales, Emmanuel; Nicastro, Emanuele; Quintero, Jesus; Richter, Nicolas; Heaton, Nigel; Reding, Raymond; Branchereau, Sophie; Gupte, Girish; Schmelzle, Moritz; Fischer, Lutz; Kalicinski, Piotr; Colledan, Michele; Santamaria, Manuel Lopez; de Kleine, Ruben H; Fitzpatrick, Emer

Primary sclerosing cholangitis in children with inflammatory bowel disease: An ESPGHAN position paper from the Hepatology Committee and the IBD Porto group

儿童炎症性肠病合并原发性硬化性胆管炎:欧洲儿科学会肝病学、肝病学和营养学会肝病委员会及波尔图炎症性肠病小组的立场文件

van Rheenen, Patrick F; Kolho, Kaija-Leena; Russell, Richard K; Aloi, Marina; Deganello, Annamaria; Hussey, Séamus; Junge, Norman; De Laffolie, Jan; Deneau, Mark R; Fitzpatrick, Emer; Griffiths, Anne M; Hojsak, Iva; Nicastro, Emanuele; Nita, Andreia; Pakarinen, Mikko; Ricciuto, Amanda; de Ridder, Lissy; Sonzogni, Aurelio; Tenca, Andrea; Samyn, Marianne; Indolfi, Giuseppe

Paediatric acute liver failure: A prospective, nationwide, population-based surveillance study in Germany

德国一项前瞻性、全国性、基于人群的儿童急性肝衰竭监测研究

Lenz, Dominic; Abdulaziz, Muhammad; Peters, Bianca; Wagner, Matias; Schlieben, Lea D; Corman, Victor M; Baumann, Ulrich; Bufler, Philip; Dattner, Tal; Ganschow, Rainer; Genzel, Kristin; Hammann, Nicole; Hartleif, Steffen; Hegen, Bianca; Henning, Stephan; Hoerning, André; Jankofsky, Martin; Junge, Norman; Kathemann, Simone; Knoppke, Birgit; Kohl-Sobania, Martina; Laass, Martin; Lainka, Elke; Lurz, Eberhard; Melter, Michael; Müller, Hanna; Pilic, Denisa; Ries, Markus; Schiefele, Lisa; Schwerd, Tobias; Sturm, Ekkehard; Wegner, Mechtild; Urschitz, Michael S; Garbade, Sven F; Wenning, Daniel; Drosten, Christian; Fichtner, Alexander; Kölker, Stefan; Hoffmann, Georg F; Prokisch, Holger; Staufner, Christian

Genetic landscape of pediatric acute liver failure of indeterminate origin

儿童不明原因急性肝衰竭的遗传图谱

Lenz, Dominic; Schlieben, Lea D; Shimura, Masaru; Bianzano, Alyssa; Smirnov, Dmitrii; Kopajtich, Robert; Berutti, Riccardo; Adam, Rüdiger; Aldrian, Denise; Baric, Ivo; Baumann, Ulrich; Bozbulut, Neslihan E; Brugger, Melanie; Brunet, Theresa; Bufler, Philip; Burnytė, Birutė; Calvo, Pier L; Crushell, Ellen; Dalgiç, Buket; Das, Anibh M; Dezsőfi, Antal; Distelmaier, Felix; Fichtner, Alexander; Freisinger, Peter; Garbade, Sven F; Gaspar, Harald; Goujon, Louise; Hadzic, Nedim; Hartleif, Steffen; Hegen, Bianca; Hempel, Maja; Henning, Stephan; Hoerning, Andre; Houwen, Roderick; Hughes, Joanne; Iorio, Raffaele; Iwanicka-Pronicka, Katarzyna; Jankofsky, Martin; Junge, Norman; Kanavaki, Ino; Kansu, Aydan; Kaspar, Sonja; Kathemann, Simone; Kelly, Deidre; Kirsaçlioğlu, Ceyda T; Knoppke, Birgit; Kohl, Martina; Kölbel, Heike; Kölker, Stefan; Konstantopoulou, Vassiliki; Krylova, Tatiana; Kuloğlu, Zarife; Kuster, Alice; Laass, Martin W; Lainka, Elke; Lurz, Eberhard; Mandel, Hanna; Mayerhanser, Katharina; Mayr, Johannes A; McKiernan, Patrick; McClean, Patricia; McLin, Valerie; Mention, Karine; Müller, Hanna; Pasquier, Laurent; Pavlov, Martin; Pechatnikova, Natalia; Peters, Bianca; Petković Ramadža, Danijela; Piekutowska-Abramczuk, Dorota; Pilic, Denisa; Rajwal, Sanjay; Rock, Nathalie; Roetig, Agnès; Santer, René; Schenk, Wilfried; Semenova, Natalia; Sokollik, Christiane; Sturm, Ekkehard; Taylor, Robert W; Tschiedel, Eva; Urbonas, Vaidotas; Urreizti, Roser; Vermehren, Jan; Vockley, Jerry; Vogel, Georg-Friedrich; Wagner, Matias; van der Woerd, Wendy; Wortmann, Saskia B; Zakharova, Ekaterina; Hoffmann, Georg F; Meitinger, Thomas; Murayama, Kei; Staufner, Christian; Prokisch, Holger

Detection of polyreactive immunoglobulin G facilitates diagnosis in children with autoimmune hepatitis

检测多反应性免疫球蛋白G有助于诊断儿童自身免疫性肝炎

Engel, Bastian; Diestelhorst, Jana; Hupa-Breier, Katharina Luise; Kirchner, Theresa; Henjes, Nicole; Loges, Stephanie; Yuksel, Muhammed; Janczyk, Wojciech; Lalanne, Claudine; Zachou, Kalliopi; Oo, Ye H; Gournay, Jérôme; Pape, Simon; Drenth, Joost P H; Renand, Amédée; Dalekos, George N; Muratori, Luigi; Socha, Piotr; Ma, Yun; Arikan, Cigdem; Baumann, Ulrich; Manns, Michael P; Wedemeyer, Heiner; Junge, Norman; Jaeckel, Elmar; Taubert, Richard