日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Cortactin loss protects against hemin-induced acute lung injury in sickle cell disease

皮质蛋白的丢失可防止镰状细胞病中血红素诱发的急性肺损伤

Nicole M Jones, Justin R Sysol, Sunit Singla, Patricia Smith, George E Sandusky, Huashan Wang, Viswanathan Natarajan, Steven M Dudek, Roberto F Machado

Sphingosine Kinase 1 Deficiency in Smooth Muscle Cells Protects against Hypoxia-Mediated Pulmonary Hypertension via YAP1 Signaling

平滑肌细胞鞘氨醇激酶 1 缺乏可通过 YAP1 信号传导预防缺氧介导的肺动脉高压

Jiwang Chen, Angelia Lockett, Shuangping Zhao, Long Shuang Huang, Yifan Wang, Weiwen Wu, Ming Tang, Shahzaib Haider, Daniela Velez Rendon, Raheel Khan, Bing Liu, Nicholas Felesena, Justin R Sysol, Daniela Valdez-Jasso, Haiyang Tang, Yang Bai, Viswanathan Natarajan, Roberto F Machado

Micro-RNA-1 is decreased by hypoxia and contributes to the development of pulmonary vascular remodeling via regulation of sphingosine kinase 1

缺氧会导致微小RNA-1减少,并通过调节鞘氨醇激酶1促进肺血管重塑的发展

Justin R Sysol, Jiwang Chen, Sunit Singla, Shuangping Zhao, Suzy Comhair, Viswanathan Natarajan, Roberto F Machado

Nicotinamide Phosphoribosyltransferase Promotes Pulmonary Vascular Remodeling and Is a Therapeutic Target in Pulmonary Arterial Hypertension

烟酰胺磷酸核糖基转移酶促进肺血管重塑,是肺动脉高压的治疗靶点

Jiwang Chen, Justin R Sysol, Sunit Singla, Shuangping Zhao, Aya Yamamura, Daniela Valdez-Jasso, Taimur Abbasi, Krystyna M Shioura, Sakshi Sahni, Vamsi Reddy, Arvind Sridhar, Hui Gao, Jaime Torres, Sara M Camp, Haiyang Tang, Shui Q Ye, Suzy Comhair, Raed Dweik, Paul Hassoun, Jason X-J Yuan, Joe G N G

Hemin Causes Lung Microvascular Endothelial Barrier Dysfunction by Necroptotic Cell Death

血红素通过坏死性细胞死亡导致肺微血管内皮屏障功能障碍

Sunit Singla, Justin R Sysol, Benjamin Dille, Nicole Jones, Jiwang Chen, Roberto F Machado

Loss of lung WWOX expression causes neutrophilic inflammation

肺 WWOX 表达丧失导致中性粒细胞炎症

Sunit Singla, Jiwang Chen, Shruthi Sethuraman, Justin R Sysol, Amulya Gampa, Shuangping Zhao, Roberto F Machado

Deficiency of Akt1, but not Akt2, attenuates the development of pulmonary hypertension

Akt1 缺乏(而非 Akt2 缺乏)可减缓肺动脉高压的发展

Haiyang Tang, Jiwang Chen, Dustin R Fraidenburg, Shanshan Song, Justin R Sysol, Abigail R Drennan, Stefan Offermanns, Richard D Ye, Marcelo G Bonini, Richard D Minshall, Joe G N Garcia, Roberto F Machado, Ayako Makino, Jason X-J Yuan

The sphingosine kinase 1/sphingosine-1-phosphate pathway in pulmonary arterial hypertension

肺动脉高压中的鞘氨醇激酶 1/鞘氨醇-1-磷酸通路

Jiwang Chen, Haiyang Tang, Justin R Sysol, Liliana Moreno-Vinasco, Krystyna M Shioura, Tianji Chen, Irina Gorshkova, Lichun Wang, Long Shuang Huang, Peter V Usatyuk, Saad Sammani, Guofei Zhou, J Usha Raj, Joe G N Garcia, Evgeny Berdyshev, Jason X-J Yuan, Viswanathan Natarajan, Roberto F Machado

Exome sequencing identifies ACSF3 as a cause of combined malonic and methylmalonic aciduria

外显子组测序确定 ACSF3 是导致丙二酸和甲基丙二酸尿症的原因

Jennifer L Sloan, Jennifer J Johnston, Irini Manoli, Randy J Chandler, Caitlin Krause, Nuria Carrillo-Carrasco, Suma D Chandrasekaran, Justin R Sysol, Kevin O'Brien, Natalie S Hauser, Julie C Sapp, Heidi M Dorward, Marjan Huizing; NIH Intramural Sequencing Center Group; Bruce A Barshop, Susan A Berr