日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Hypertrophic cardiomyopathy R403Q mutation in rabbit β-myosin reduces contractile function at the molecular and myofibrillar levels

兔β-肌球蛋白R403Q突变导致肥厚型心肌病,并在分子和肌原纤维水平上降低收缩功能。

Lowey, Susan; Bretton, Vera; Joel, Peteranne B; Trybus, Kathleen M; Gulick, James; Robbins, Jeffrey; Kalganov, Albert; Cornachione, Anabelle S; Rassier, Dilson E

Dysfunctional sarcomere contractility contributes to muscle weakness in ACTA1-related nemaline myopathy (NEM3)

ACTA1相关线状肌病(NEM3)中肌节收缩功能障碍是导致肌肉无力的原因之一。

Joureau, Barbara; de Winter, Josine Marieke; Conijn, Stefan; Bogaards, Sylvia J P; Kovacevic, Igor; Kalganov, Albert; Persson, Malin; Lindqvist, Johan; Stienen, Ger J M; Irving, Thomas C; Ma, Weikang; Yuen, Michaela; Clarke, Nigel F; Rassier, Dilson E; Malfatti, Edoardo; Romero, Norma B; Beggs, Alan H; Ottenheijm, Coen A C

Arginylation of myosin heavy chain regulates skeletal muscle strength.

肌球蛋白重链的精氨酸化调节骨骼肌力量

Cornachione Anabelle S, Leite Felipe S, Wang Junling, Leu Nicolae A, Kalganov Albert, Volgin Denys, Han Xuemei, Xu Tao, Cheng Yu-Shu, Yates John R R 3rd, Rassier Dilson E, Kashina Anna