日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

In vitro reconstitution of heterochromatin compartments reveals the spontaneous formation of tunable liquid-liquid interfaces

体外异染色质区室的重建揭示了可调控液-液界面的自发形成。

Brennan, Lucy D; Kim, Hyeong-Ku; Colmenares, Serafin; Ego, Tatum; Ryu, Je-Kyung; Karpen, Gary

The history and future of bile acid therapies

胆汁酸疗法的历史与未来

Beuers, Ulrich; Banales, Jesus M; Karpen, Saul J; Keitel, Verena; Williamson, Catherine; Trauner, Michael

Erratum to: 'Inhibition of the renal apical sodium dependent bile acid transporter prevents cholemic nephropathy in mice with obstructive cholestasis' [J Hepatol (2024) 80:268-281]

更正:'抑制肾顶端钠依赖性胆汁酸转运体可预防阻塞性胆汁淤积小鼠的胆汁性肾病' [J Hepatol (2024) 80:268-281]

Ghallab, Ahmed; González, Daniela; Strängberg, Ellen; Hofmann, Ute; Myllys, Maiju; Hassan, Reham; Hobloss, Zaynab; Brackhagen, Lisa; Begher-Tibbe, Brigitte; Duda, Julia C; Drenda, Carolin; Kappenberg, Franziska; Reinders, Joerg; Friebel, Adrian; Vucur, Mihael; Turajski, Monika; Seddek, Abdel-Latief; Abbas, Tahany; Abdelmageed, Noha; Morad, Samy A F; Morad, Walaa; Hamdy, Amira; Albrecht, Wiebke; Kittana, Naim; Assali, Mohyeddin; Vartak, Nachiket; van Thriel, Christoph; Sous, Ansam; Nell, Patrick; Villar-Fernandez, Maria; Cadenas, Cristina; Genc, Erhan; Marchan, Rosemarie; Luedde, Tom; Åkerblad, Peter; Mattsson, Jan; Marschall, Hanns-Ulrich; Hoehme, Stefan; Stirnimann, Guido; Schwab, Matthias; Boor, Peter; Amann, Kerstin; Schmitz, Jessica; Bräsen, Jan H; Rahnenführer, Jörg; Edlund, Karolina; Karpen, Saul J; Simbrunner, Benedikt; Reiberger, Thomas; Mandorfer, Mattias; Trauner, Michael; Dawson, Paul A; Lindström, Erik; Hengstler, Jan G

Enteronephrohepatic circulation of bile acids and therapeutic potential of systemic bile acid transporter inhibitors

胆汁酸的肠肾肝循环及全身胆汁酸转运体抑制剂的治疗潜力

Ghallab, Ahmed; Mandorfer, Mattias; Stirnimann, Guido; Geyer, Joachim; Lindström, Erik; Luedde, Tom; van der Merwe, Schalk; Rashidi-Alavijeh, Jassin; Schmidt, Hartmut; Karpen, Saul J; Fickert, Peter; Trauner, Michael; Hengstler, Jan G; Dawson, Paul A

Hierarchical interactions between nucleolar and heterochromatin condensates are mediated by a dual-affinity protein.

核仁和异染色质凝聚体之间的层级相互作用是由双亲和力蛋白介导的。

Rajshekar Srivarsha, Adame-Arana Omar, Bajpai Gaurav, Colmenares Serafin U, Papoi Hannah, Brennan Lucy D, Tsukamoto Shingo, Safran Samuel, Karpen Gary H

Benefits and challenges to therapeutic targeting of bile acid circulation in cholestatic liver disease

胆汁酸循环治疗在胆汁淤积性肝病中的益处和挑战

Trauner, Michael; Karpen, Saul J; Dawson, Paul A

Expanding the HP1a-binding consensus and molecular grammar for heterochromatin assembly

扩展HP1a结合共识和异染色质组装的分子语法

Colmenares, Serafin U; Tsukamoto, Shingo; Hickmann, Collin; Brennan, Lucy D; Khavani, Mohammad; Mofrad, Mohammad R K; Karpen, Gary H

Condition-Specific Growth Charts for Children With Alagille Syndrome

阿拉吉尔综合征患儿的特定生长曲线图

Huysentruyt, Koen; Vandriel, Shannon M; Roelants, Mathieu; Piccoli, David A; Loomes, Kathleen M; Rand, Elizabeth B; Ebel, Noelle H; Feinstein, Jeffrey A; Jankowska, Irena; Czubkowski, Piotr; Gliwicz-Miedzinska, Dorota; Gonzales, Emmanuel M; Jacquemin, Emmanuel; Bouligand, Jérôme; Karpen, Saul J; Romero, Rene; Lin, Henry C; Fischler, Björn; Arnell, Henrik; Li, Li-Ting; Wang, Jian-She; Fawaz, Rima; Nastasio, Silvia; Kim, Kyung Mo; Oh, Seak Hee; D'Antiga, Lorenzo; Nicastro, Emanuele; Fischer, Ryan T; Siew, Susan M; Stormon, Michael; Lertudomphonwanit, Chatmanee; Hardikar, Winita; Shankar, Sahana; Squires, James E; Sundaram, Shikha S; Larson-Nath, Catherine; Kelly, Deirdre A; Hartley, Jane; Bulut, Pinar; Jensen, M Kyle; Jaramillo, Catalina; Roberts, Amin J; Evans, Helen M; Sokal, Étienne M; Demaret, Tanguy; Verkade, Henkjan J; Thompson, Richard J; Hansen, Bettina E; Cole, Tim J; Kamath, Binita M; Debray, Dominique; Lacaille, Florence; Brecelj, Jernej; El-Koofy, Nehal M; Elmonem, Mohamed A; Lee, Way Seah; Sanchez, Maria Camila; Cavalieri, Maria Lorena; Hajinicolaou, Christina; Schwarz, Kathleen B; Carvalho, Elisa; Rock, Nathalie; Karnsakul, Wikrom; Quiros-Tejeira, Ruben E; Alam, Seema; Nebbia, Gabriella; Mozer-Glassberg, Yael; Valentino, Pamela L; Santos-Silva, Ermelinda; Önal, Zerrin; Dezsofi-Gottl, Antal; Melere, Melina; Legarda Tamara, María; Eshun, John; Zellos, Aglaia; Indolfi, Giuseppe; Rogalidou, Maria; Blondet, Niviann; Luigi Calvo, Pier; Beretta, Marisa; Zizzo, Andréanne N; Arikan, Cigdem; Kasahara, Mureo; Kerkar, Nanda; Aqul, Amal A; Wolters, Victorien M; Borges Pinto, Raquel; Quintero Bernabeu, Jesus; Garcia, Jennifer; Wiecek, Sabina; Tzivinikos, Christos; Mujawar, Quais; Jimenez-Rivera, Carolina; Molera Busoms, Cristina; Gonçalves, Cristina; Bujanda, Luis

Stage-dependent effects of systemic ASBT inhibition in a cholestasis-induced cholemic nephropathy mouse model

在胆汁淤积诱导的胆汁性肾病小鼠模型中,全身性ASBT抑制的阶段依赖性效应

Ghallab, Ahmed; Myllys, Maiju; González, Daniela; Friebel, Adrian; Hobloss, Zaynab; Hassan, Reham; Schmidt, Hannah; Siddiqui, Qasim; Zhipeng, Deng; Hendawi, Rama; Begher-Tibbe, Brigitte; Reinders, Joerg; Derksen, Katharina; Hofmann, Ute; Duda, Julia C; Ameis, Lucia; Möllenhoff, Kathrin; Seddek, Abdellatief; Abdelmageed, Noha; Strängberg, Ellen; Åkerblad, Peter; Vucur, Mihael; Luedde, Tom; Stirnimann, Guido; Schwab, Matthias; Abbas, Tahany; Hild, Benedikt; Schmidt, Hartmut; Karpen, Saul J; Simbrunner, Benedikt; Mandorfer, Mattias; Rahnenführer, Jörg; Edlund, Karolina; Hoehme, Stefan; Trauner, Michael; Dawson, Paul A; Lindström, Erik; Hengstler, Jan G

Phenotypic Divergence of JAG1- and NOTCH2-Associated Alagille Syndrome & Disease-Specific NOTCH2 Variant Classification Guidelines

JAG1 和 NOTCH2 相关阿拉吉尔综合征的表型差异及疾病特异性 NOTCH2 变异分类指南

Vandriel, Shannon M; Li, Li-Ting; She, Huiyu; Wang, Jian-She; Loomes, Kathleen M; Piccoli, David A; Jankowska, Irena; Czubkowski, Piotr; Gliwicz-Miedzińska, Dorota; D'Antiga, Lorenzo; Nicastro, Emanuele; Lacaille, Florence; Debray, Dominique; Sokal, Étienne M; Demaret, Tanguy; Fawaz, Rima L; Nastasio, Silvia; Kim, Kyung Mo; Oh, Seak Hee; Fischler, Björn; Arnell, Henrik; Larson-Nath, Catherine; Hardikar, Winita; Shankar, Sahana; Sundaram, Shikha S; Chaidez, Alexander; Bulut, Pinar; Calvo, Pier Luigi; Kasahara, Mureo; Blondet, Niviann; Lurz, Eberhard; Kavallar, Anna-Maria; Gonzales, Emmanuel M; Jacquemin, Emmanuel; Bouligand, Jérôme; Ebel, Noelle H; Feinstein, Jeffrey A; Siew, Susan M; Stormon, Michael O; Karpen, Saul J; Romero, Rene; Jensen, M Kyle; Jaramillo, Catalina; Squires, James E; Bedoyan, Sarah M; Kelly, Deirdre A; Hartley, Jane; Verkade, Henkjan J; Lee, Way Seah; Lertudomphonwanit, Chatmanee; Fischer, Ryan T; Lin, Henry C; Rock, Nathalie; Mozer-Glassberg, Yael; Roberts, Amin J; Evans, Helen M; Karnsakul, Wikrom; Nebbia, Gabriella; Wolters, Victorien M; Valentino, Pamela L; Bernabeu, Jesus Quintero; Aqul, Amal A; Arikan, Cigdem; Tamara, María Legarda; Busoms, Cristina Molera; Sandahl, Thomas Damgaard; Indolfi, Giuseppe; Zizzo, Andréanne N; Zellos, Aglaia; Quiros-Tejeira, Ruben E; Santos-Silva, Ermelinda; Schwarz, Kathleen B; Brecelj, Jernej; Sanchez, Maria Camila; Cavalieri, Maria Lorena; Tzivinikos, Christos; Wiecek, Sabina; Eshun, John; Kerkar, Nanda; Mujawar, Quais; Önal, Zerrin; Gonçalves, Cristina; Garcia, Jennifer; Alam, Seema; Jimenez-Rivera, Carolina; Bujanda, Luis; Thompson, Richard J; Hansen, Bettina E; Spinner, Nancy B; Gilbert, Melissa A; Kamath, Binita M