日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

A novel method for real-time analysis of the complement C3b:FH:FI complex reveals dominant negative CFI variants in age-related macular degeneration

一种实时分析补体 C3b:FH:FI 复合物的新方法揭示了年龄相关性黄斑变性中的显性负性 CFI 变异

Thomas M Hallam, Thomas E Cox, Kate Smith-Jackson, Vicky Brocklebank, April J Baral, Nikolaos Tzoumas, David H Steel, Edwin K S Wong, Victoria G Shuttleworth, Andrew J Lotery, Claire L Harris, Kevin J Marchbank, David Kavanagh

Functional Characterization of Rare Genetic Variants in the N-Terminus of Complement Factor H in aHUS, C3G, and AMD

补体因子 H N 端罕见遗传变异在 aHUS、C3G 和 AMD 中的功能表征

Edwin K S Wong, Thomas M Hallam, Vicky Brocklebank, Patrick R Walsh, Kate Smith-Jackson, Victoria G Shuttleworth, Thomas E Cox, Holly E Anderson, Paul Nigel Barlow, Kevin James Marchbank, Claire L Harris, David Kavanagh

Homodimeric Minimal Factor H: In Vivo Tracking and Extended Dosing Studies in Factor H Deficient Mice

同型二聚体最小因子 H:因子 H 缺乏小鼠体内追踪和延长给药研究

Ola Kamala, Talat H Malik, Thomas M Hallam, Thomas E Cox, Yi Yang, Falguni Vyas, Saimir Luli, Chloe Connelly, Beth Gibson, Kate Smith-Jackson, Harriet Denton, Isabel Y Pappworth, Lei Huang, David Kavanagh, Matthew C Pickering, Kevin J Marchbank

Hyperfunctional complement C3 promotes C5-dependent atypical hemolytic uremic syndrome in mice

补体 C3 功能亢进促进小鼠 C5 依赖性非典型溶血性尿毒症综合征

Kate Smith-Jackson, Yi Yang, Harriet Denton, Isabel Y Pappworth, Katie Cooke, Paul N Barlow, John P Atkinson, M Kathryn Liszewski, Matthew C Pickering, David Kavanagh, H Terence Cook, Kevin J Marchbank