日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Odevixibat after liver transplant in patients with progressive familial intrahepatic cholestasis type 1: A case series

肝移植后接受奥德维西巴治疗进行性家族性肝内胆汁淤积症1型患者:病例系列研究

Vogel, Georg-Friedrich; Kathemann, Simone; Pietrobattista, Andrea; Maggiore, Giuseppe; Aldrian, Denise; Sciveres, Marco; Verkade, Henkjan J; Sokal, Etienne; Jannone, Giulia; Salcedo, Magdalena; Rauschkolb, Peter; Maucksch, Christof; Valcheva, Velichka; Lainka, Elke

Paediatric acute liver failure: A prospective, nationwide, population-based surveillance study in Germany

德国一项前瞻性、全国性、基于人群的儿童急性肝衰竭监测研究

Lenz, Dominic; Abdulaziz, Muhammad; Peters, Bianca; Wagner, Matias; Schlieben, Lea D; Corman, Victor M; Baumann, Ulrich; Bufler, Philip; Dattner, Tal; Ganschow, Rainer; Genzel, Kristin; Hammann, Nicole; Hartleif, Steffen; Hegen, Bianca; Henning, Stephan; Hoerning, André; Jankofsky, Martin; Junge, Norman; Kathemann, Simone; Knoppke, Birgit; Kohl-Sobania, Martina; Laass, Martin; Lainka, Elke; Lurz, Eberhard; Melter, Michael; Müller, Hanna; Pilic, Denisa; Ries, Markus; Schiefele, Lisa; Schwerd, Tobias; Sturm, Ekkehard; Wegner, Mechtild; Urschitz, Michael S; Garbade, Sven F; Wenning, Daniel; Drosten, Christian; Fichtner, Alexander; Kölker, Stefan; Hoffmann, Georg F; Prokisch, Holger; Staufner, Christian

The role of LSR gene variants in early onset intrahepatic cholestasis: a case series with treatment options

LSR基因变异在早发性肝内胆汁淤积症中的作用:病例系列及治疗方案

Ohlsson, Sinja; Zaufel, Alex; Qvartskhava, Natalia; Stock, Friedrich; Hinreiner, Sophie; Baba, Hideo A; Prusinskas, Benas; Kubitz, Ralf; Görg, Boris; Herebian, Diran; Lainka, Elke; Kathemann, Simone

Assessment of Donor-Specific Human Leukocyte Antigen Antibodies Following Pediatric Liver Transplantation: Predictors, Protectors, and Clinical Relevance

儿童肝移植后供体特异性人类白细胞抗原抗体的评估:预测因子、保护因子和临床意义

Kanaan, Evelien; Ohlsson, Sinja; Kathemann, Simone; Prusinskas, Benas; Tsaka, Sofia; Heinemann, Falko M; Heinold, Andreas; Schulze, Maren; Pape, Lars; Lainka, Elke

Genetic landscape of pediatric acute liver failure of indeterminate origin

儿童不明原因急性肝衰竭的遗传图谱

Lenz, Dominic; Schlieben, Lea D; Shimura, Masaru; Bianzano, Alyssa; Smirnov, Dmitrii; Kopajtich, Robert; Berutti, Riccardo; Adam, Rüdiger; Aldrian, Denise; Baric, Ivo; Baumann, Ulrich; Bozbulut, Neslihan E; Brugger, Melanie; Brunet, Theresa; Bufler, Philip; Burnytė, Birutė; Calvo, Pier L; Crushell, Ellen; Dalgiç, Buket; Das, Anibh M; Dezsőfi, Antal; Distelmaier, Felix; Fichtner, Alexander; Freisinger, Peter; Garbade, Sven F; Gaspar, Harald; Goujon, Louise; Hadzic, Nedim; Hartleif, Steffen; Hegen, Bianca; Hempel, Maja; Henning, Stephan; Hoerning, Andre; Houwen, Roderick; Hughes, Joanne; Iorio, Raffaele; Iwanicka-Pronicka, Katarzyna; Jankofsky, Martin; Junge, Norman; Kanavaki, Ino; Kansu, Aydan; Kaspar, Sonja; Kathemann, Simone; Kelly, Deidre; Kirsaçlioğlu, Ceyda T; Knoppke, Birgit; Kohl, Martina; Kölbel, Heike; Kölker, Stefan; Konstantopoulou, Vassiliki; Krylova, Tatiana; Kuloğlu, Zarife; Kuster, Alice; Laass, Martin W; Lainka, Elke; Lurz, Eberhard; Mandel, Hanna; Mayerhanser, Katharina; Mayr, Johannes A; McKiernan, Patrick; McClean, Patricia; McLin, Valerie; Mention, Karine; Müller, Hanna; Pasquier, Laurent; Pavlov, Martin; Pechatnikova, Natalia; Peters, Bianca; Petković Ramadža, Danijela; Piekutowska-Abramczuk, Dorota; Pilic, Denisa; Rajwal, Sanjay; Rock, Nathalie; Roetig, Agnès; Santer, René; Schenk, Wilfried; Semenova, Natalia; Sokollik, Christiane; Sturm, Ekkehard; Taylor, Robert W; Tschiedel, Eva; Urbonas, Vaidotas; Urreizti, Roser; Vermehren, Jan; Vockley, Jerry; Vogel, Georg-Friedrich; Wagner, Matias; van der Woerd, Wendy; Wortmann, Saskia B; Zakharova, Ekaterina; Hoffmann, Georg F; Meitinger, Thomas; Murayama, Kei; Staufner, Christian; Prokisch, Holger

Cell-based BSEP trans-inhibition: A novel, non-invasive test for diagnosis of antibody-induced BSEP deficiency

基于细胞的 BSEP 反式抑制:一种诊断抗体诱导的 BSEP 缺陷的新型非侵入性检测方法

Jan Stindt, Carola Dröge, Elke Lainka, Simone Kathemann, Eva-Doreen Pfister, Ulrich Baumann, Amelie Stalke, Enke Grabhorn, Mohammad Ali Shagrani, Yael Mozer-Glassberg, Jane Hartley, Marianne Wammers, Caroline Klindt, Paulina Philippski, Roman Liebe, Diran Herebian, Ertan Mayatepek, Thomas Berg, Anjo

Progressive familial intrahepatic cholestasis-outcome and time to transplant after biliary diversion according to genetic subtypes

进行性家族性肝内胆汁淤积症——根据遗传亚型分析胆道改道术后的预后和移植时间

Sahloul, Abdulla; Lainka, Elke; Kathemann, Simone; Swoboda, Sandra; Dröge, Carola; Keitel, Verena; Al-Matary, Yahya Saleh; Berger, Michael; Schulze, Maren

Congenital Diarrhea and Cholestatic Liver Disease: Phenotypic Spectrum Associated with MYO5B Mutations

先天性腹泻和胆汁淤积性肝病:与 MYO5B 突变相关的表型谱

Aldrian, Denise; Vogel, Georg F; Frey, Teresa K; Ayyıldız Civan, Hasret; Aksu, Aysel Ünlüsoy; Avitzur, Yaron; Ramos Boluda, Ester; Çakır, Murat; Demir, Arzu Meltem; Deppisch, Caroline; Duba, Hans-Christoph; Düker, Gesche; Gerner, Patrick; Hertecant, Jozef; Hornová, Jarmila; Kathemann, Simone; Koeglmeier, Jutta; Koutroumpa, Arsinoi; Lanzersdorfer, Roland; Lev-Tzion, Raffi; Lima, Rosa; Mansour, Sahar; Meissl, Manfred; Melek, Jan; Miqdady, Mohamad; Montoya, Jorge Hernan; Posovszky, Carsten; Rachman, Yelena; Siahanidou, Tania; Tabbers, Merit; Uhlig, Holm H; Ünal, Sevim; Wirth, Stefan; Ruemmele, Frank M; Hess, Michael W; Huber, Lukas A; Müller, Thomas; Sturm, Ekkehard; Janecke, Andreas R

Role of Tacrolimus C/D Ratio in the First Year After Pediatric Liver Transplantation

他克莫司 C/D 比值在儿童肝移植术后第一年的作用

Prusinskas, Benas; Ohlsson, Sinja; Kathemann, Simone; Pilic, Denisa; Kampmann, Kristina; Büscher, Rainer; Paul, Andreas; Pape, Lars; Hoyer, Peter F; Lainka, Elke

A Retrospective Analysis of Rituximab Treatment for B Cell Depletion in Different Pediatric Indications

利妥昔单抗治疗不同儿科适应症中B细胞耗竭的回顾性分析

Wennmann, Merlin; Kathemann, Simone; Kampmann, Kristina; Ohlsson, Sinja; Büscher, Anja; Holzinger, Dirk; Della Marina, Adela; Lainka, Elke