Enhanced hepatic clearance of hyposialylated platelets explains thrombocytopenia in GNE-related macrothrombocytopenia
低唾液酸化血小板的肝脏清除增强可解释GNE相关性巨血小板减少症中的血小板减少症。
期刊:Blood Advances
影响因子:7.1
doi:10.1182/bloodadvances.2021006830
Noordermeer, Tessa; van Asten, Ivar; Schutgens, Roger E G; Lakerveld, Anke J; Koekman, Cornelis A; Hage, Kay Y; Sebastian, Silvie A E; Huisman, Albert; van den Heuvel, Dave J; Gerritsen, Hans C; Korporaal, Suzanne J A; Bierings, Marc; van der Smagt, Jasper J; van Gijn, Mariëlle E; Urbanus, Rolf T