日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

SLC26A4-AP-2 mu2 interaction regulates SLC26A4 plasma membrane abundance in the endolymphatic sac

SLC26A4-AP-2 mu2 相互作用调节内淋巴囊中的 SLC26A4 质膜丰度

Hyun Jae Lee, Cristina Fenollar-Ferrer, Kevin Isgrig, Ya-Xian Wang, Kerstin Valente, Juleh Eide, Keiji Honda, Wade W Chien, Ronald S Petralia, Lijin Dong, Thomas B Friedman, Juan S Bonifacino, Andrew J Griffith, Isabelle Roux

Early-Onset Hearing Loss in Mouse Models of Alzheimer's Disease and Increased DNA Damage in the Cochlea

阿尔茨海默病小鼠模型中早发性听力损失和耳蜗 DNA 损伤增加

Jae-Hyeon Park, Burcin Duan Sahbaz, Komal Pekhale, Xixia Chu, Mustafa N Okur, Mhamed Grati, Kevin Isgrig, Wade Chien, Elena Chrysostomou, Lauren Sullivan, Deborah L Croteau, Uri Manor, Vilhelm A Bohr

Dual-AAV vector-mediated expression of MYO7A improves vestibular function in a mouse model of Usher syndrome 1B

双 AAV 载体介导的 MYO7A 表达可改善 Usher 综合征 1B 小鼠模型的前庭功能

Samantha C Lau, Mhamed Grati, Kevin Isgrig, Moaz Sinan, Kaitlyn R Calabro, Jianliang Zhu, Yasuko Ishibashi, Zeynep Ozgur, Talah Wafa, Inna A Belyantseva, Tracy Fitzgerald, Thomas B Friedman, Sanford L Boye, Shannon E Boye, Wade W Chien

AAV8BP2 and AAV8 transduce the mammalian cochlear lateral wall and endolymphatic sac with high efficiency

AAV8BP2 和 AAV8 高效传导哺乳动物耳蜗侧壁和内淋巴囊

Kevin Isgrig, Yasuko Ishibashi, Hyun Jae Lee, Jianliang Zhu, Mhamed Grati, Jean Bennett, Andrew J Griffith, Isabelle Roux, Wade W Chien

Refining surgical techniques for efficient posterior semicircular canal gene delivery in the adult mammalian inner ear with minimal hearing loss

改进手术技术,在成年哺乳动物内耳中有效传递后半规管基因,同时最大程度减少听力损失

Jianliang Zhu #, Jin Woong Choi #, Yasuko Ishibashi, Kevin Isgrig, Mhamed Grati, Jean Bennett, Wade Chien

AAV2.7m8 is a powerful viral vector for inner ear gene therapy

AAV2.7m8 是一种用于内耳基因治疗的强大病毒载体

Kevin Isgrig, Devin S McDougald, Jianliang Zhu, Hong Jun Wang, Jean Bennett, Wade W Chien

A CEP290 C-Terminal Domain Complements the Mutant CEP290 of Rd16 Mice In Trans and Rescues Retinal Degeneration

CEP290 C 端结构域在转录过程中补充 Rd16 小鼠的突变 CEP290 并挽救视网膜变性

Suddhasil Mookherjee, Holly Yu Chen, Kevin Isgrig, Wenhan Yu, Suja Hiriyanna, Rivka Levron, Tiansen Li, Peter Colosi, Wade Chien, Anand Swaroop, Zhijian Wu