Local accumulation of very long-chain PUFA in plexiform layers associates with retinal dysfunction in a mouse model of peroxisomal ACBD5-deficiency
在过氧化物酶体ACBD5缺陷的小鼠模型中,丛状层中极长链多不饱和脂肪酸的局部积累与视网膜功能障碍相关。
期刊:Cellular and Molecular Life Sciences
影响因子:6.2
doi:10.1007/s00018-025-05971-8
Merz, Julia; Müller, Elisabeth; Darwisch, Warda; Fairless, Richard; Wang, Yixin; Vorwald, Silke; Darwisch, Sharau; Curticean, E Ronald; Shao, Feng; Wacker, Irene; Schröder, Rasmus R; Pitzer, Claudia; Schultz, Christian; van Klinken, Jan-Bert; Vaz, Frederic M; Kratzer, Frank; Schwarz, Kathrin; Okun, Jürgen G; Feng, Yuxi; Hopf, Carsten; Islinger, Markus