日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Long-Term Dynamics of CSF and Serum Neurofilament Light Chain in Adult Patients With 5q Spinal Muscular Atrophy Treated With Nusinersen

接受诺西那生治疗的5q脊髓性肌萎缩症成年患者脑脊液和血清神经丝轻链的长期动态变化

Cordts, Isabell; Fuetterer, Cornelia; Wachinger, Annika; von Heynitz, Ricarda; Kessler, Tobias; Freigang, Maren; Quinten, Anna Lisa; Bjelica, Bogdan; Brakemeier, Svenja; Hobbiebrunken, Elke; Hagenacker, Tim; Petri, Susanne; Koch, Jan Christoph; Hahn, Andreas; Lingor, Paul; Deschauer, Marcus; Günther, Rene; Weiler, Markus; Haller, Bernhard; Feneberg, Emily

Provision, cough efficacy and treatment satisfaction of mechanical insufflation-exsufflation in a large multicenter cohort of patients with amyotrophic lateral sclerosis

在一项针对肌萎缩侧索硬化症患者的大型多中心队列研究中,机械通气-排气疗法的实施、咳嗽疗效和治疗满意度

Maier, André; Kettemann, Dagmar; Weyen, Ute; Grehl, Torsten; Schulte, Peter Caspar; Steinbach, Robert; Rödiger, Annekathrin; Weydt, Patrick; Petri, Susanne; Wolf, Joachim; Grosskreutz, Julian; Koch, Jan Christoph; Weishaupt, Jochen H; Rosseau, Simone; Norden, Jenny; Körtvélyessy, Peter; Koch, Birgit; Holm, Teresa; Hildebrandt, Barbara; Schumann, Peggy; Walter, Bertram; Riitano, Alessio; Münch, Christoph; Meyer, Thomas; Spittel, Susanne

Serum neurofilament light chain in distinct phenotypes of amyotrophic lateral sclerosis: A longitudinal, multicenter study

肌萎缩侧索硬化症不同表型患者血清神经丝轻链水平:一项纵向多中心研究

Meyer, Thomas; Dreger, Marie; Grehl, Torsten; Weyen, Ute; Kettemann, Dagmar; Weydt, Patrick; Günther, René; Lingor, Paul; Petri, Susanne; Koch, Jan Christoph; Großkreutz, Julian; Rödiger, Annekathrin; Baum, Petra; Hermann, Andreas; Prudlo, Johannes; Boentert, Matthias; Weishaupt, Jochen H; Löscher, Wolfgang N; Dorst, Johannes; Koc, Yasemin; Bernsen, Sarah; Cordts, Isabell; Vidovic, Maximilian; Steinbach, Robert; Metelmann, Moritz; Kleinveld, Vera E; Norden, Jenny; Ludolph, Albert; Walter, Bertram; Schumann, Peggy; Münch, Christoph; Körtvélyessy, Péter; Maier, André

Synchrotron-Based Fourier-Transform Infrared Micro-Spectroscopy of Cerebrospinal Fluid from Amyotrophic Lateral Sclerosis Patients Reveals a Unique Biomolecular Profile

利用同步辐射傅里叶变换红外显微光谱技术对肌萎缩侧索硬化症患者脑脊液进行分析,揭示其独特的生物分子特征。

Dučić, Tanja; Koch, Jan Christoph

Economic evaluation of Motor Neuron Diseases: a nationwide cross-sectional analysis in Germany

运动神经元疾病的经济评价:德国全国横断面分析

Heinrich, Felix; Cordts, Isabell; Günther, René; Stolte, Benjamin; Zeller, Daniel; Schröter, Carsten; Weyen, Ute; Regensburger, Martin; Wolf, Joachim; Schneider, Ilka; Hermann, Andreas; Metelmann, Moritz; Kohl, Zacharias; Linker, Ralf A; Koch, Jan Christoph; Radelfahr, Florentine; Schönfelder, Erik; Gardt, Pavel; Mohajer-Peseschkian, Tara; Osmanovic, Alma; Klopstock, Thomas; Dorst, Johannes; Ludolph, Albert C; Schöffski, Oliver; Boentert, Matthias; Hagenacker, Tim; Deschauer, Marcus; Lingor, Paul; Petri, Susanne; Schreiber-Katz, Olivia

Improvements in Walking Distance during Nusinersen Treatment - A Prospective 3-year SMArtCARE Registry Study

Nusinersen治疗期间步行距离的改善——一项前瞻性3年SMArtCARE注册研究

Pechmann, Astrid; Behrens, Max; Dörnbrack, Katharina; Tassoni, Adrian; Wenzel, Franziska; Stein, Sabine; Vogt, Sibylle; Zöller, Daniela; Bernert, Günther; Hagenacker, Tim; Schara-Schmidt, Ulrike; Walter, Maggie C; Steinbach, Meike; Blaschek, Astrid; Baumann, Matthias; Baumgartner, Manuela; Becker, Benedikt; Flotats-Bastardas, Marina; Friese, Johannes; Günther, Rene; Hahn, Andreas; Küpper, Hanna; Johannsen, Jessika; Kamm, Christoph; Koch, Jan Christoph; Köhler, Cornelia; Kölbel, Heike; Kolzter, Kirsten; von Moers, Arpad; Naegel, Steffen; Neuwirth, Christoph; Petri, Susanne; Rödiger, Annekathrin; Schimmel, Mareike; Schrank, Bertold; Schreiber, Gudrun; Smitka, Martin; Stadler, Christian; Steiner, Elisabeth; Stögmann, Eva; Trollmann, Regina; Türk, Matthias; Weiler, Markus; Stoltenburg, Corinna; Willichowsky, Ekkehard; Zeller, Daniel; Ziegler, Andreas; Lochmüller, Hanns; Kirschner, Janbernd

Small and long RNA transcriptome of whole human cerebrospinal fluid and serum as compared to their extracellular vesicle fractions reveal profound differences in expression patterns and impacts on biological processes.

与细胞外囊泡组分相比,全人脑脊液和血清的小RNA和长RNA转录组揭示了表达模式的显著差异以及对生物过程的影响

Michel Uwe, Shomroni Orr, Müller Barbara, Lange Peter, Salinas Gabriela, Bähr Mathias, Koch Jan Christoph

The Role of Axonal Transport in Glaucoma

轴突运输在青光眼中的作用

Dias, Mariana Santana; Luo, Xiaoyue; Ribas, Vinicius Toledo; Petrs-Silva, Hilda; Koch, Jan Christoph

Use and subjective experience of the impact of motor-assisted movement exercisers in people with amyotrophic lateral sclerosis: a multicenter observational study

肌萎缩侧索硬化症患者使用运动辅助锻炼器及其主观体验:一项多中心观察性研究

Maier, André; Gaudlitz, Marcel; Grehl, Torsten; Weyen, Ute; Steinbach, Robert; Grosskreutz, Julian; Rödiger, Annekathrin; Koch, Jan Christoph; Lengenfeld, Teresa; Weydt, Patrick; Günther, René; Wolf, Joachim; Baum, Petra; Metelmann, Moritz; Dorst, Johannes; Ludolph, Albert C; Kettemann, Dagmar; Norden, Jenny; Koc, Ruhan Yasemin; Walter, Bertram; Hildebrandt, Barbara; Münch, Christoph; Meyer, Thomas; Spittel, Susanne

Increased chitotriosidase 1 concentration following nusinersen treatment in spinal muscular atrophy

脊髓性肌萎缩症患者接受诺西那生治疗后,几丁质酶1浓度升高

Freigang, Maren; Steinacker, Petra; Wurster, Claudia Diana; Schreiber-Katz, Olivia; Osmanovic, Alma; Petri, Susanne; Koch, Jan Christoph; Rostásy, Kevin; Falkenburger, Björn; Ludolph, Albert Christian; Otto, Markus; Hermann, Andreas; Günther, René