日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Lymphopenia drives T cell exhaustion in immunodeficient STING gain-of-function mice

淋巴细胞减少症导致免疫缺陷型STING功能获得性小鼠的T细胞耗竭。

Damien Freytag,Stéphane Giorgiutti,Grégoire Hopsomer,Nadège Wadier,Sabine Depauw,Philippe Mertz,Fabrice Augé,Raphaël Carapito,Isabelle Couillin,Anne-Sophie Korganow,Francesca Pala,Marita Bosticardo,Luigi D Notarangelo,Frédéric Rieux-Laucat,Nicolas Riteau,Peggy Kirstetter,Pauline Soulas-Sprauel

Editorial: Community series in primary immunodeficiencies worldwide, volume II

社论:全球原发性免疫缺陷社区系列,第二卷

Condino-Neto, Antonio; Korganow, Anne-Sophie; Kanegane, Hirokazu

Histologic and molecular features shared between antibody-mediated rejection of kidney allografts and chronic histiocytic intervillositis support common pathogenesis.

抗体介导的肾移植排斥反应与慢性组织细胞性绒毛间炎在组织学和分子特征上存在共同之处,这支持了二者共同的发病机制

Albersammer Léonie, Leon Juliette, Martinovic Jelena, Dagobert Jessy, Lebraud Emilie, Bessières Bettina, Loeuillet Laurence, Eloudzeri Maëva, Vivanti Alexandre J, Dumery Grégoire, Marchaudon Valérie, Antal Cristina, Korganow Anne-Sophie, Quibel Thibaud, Costedoat-Chalumeau Nathalie, Tsatsaris Vassilis, Benachi Alexandra, Zuber Julien, Rabant Marion

Impaired development of memory B cells and antibody responses in humans and mice deficient in PD-1 signaling

PD-1信号通路缺陷的人类和小鼠的记忆B细胞发育和抗体反应受损

Masato Ogishi ,Koji Kitaoka ,Kim L Good-Jacobson ,Darawan Rinchai ,Baihao Zhang ,Jun Wang ,Vincent Gies ,Geetha Rao ,Tina Nguyen ,Danielle T Avery ,Taushif Khan ,Megan E Smithmyer ,Joseph Mackie ,Rui Yang ,Andrés Augusto Arias ,Takaki Asano ,Khoren Ponsin ,Matthieu Chaldebas ,Peng Zhang ,Jessica N Peel ,Jonathan Bohlen ,Romain Lévy ,Simon J Pelham ,Wei-Te Lei ,Ji Eun Han ,Iris Fagniez ,Maya Chrabieh ,Candice Laine ,David Langlais ,Conor Gruber ,Fatima Al Ali ,Mahbuba Rahman ,Caner Aytekin ,Basilin Benson ,Matthew J Dufort ,Clara Domingo-Vila ,Kunihiko Moriya ,Mark Shlomchik ,Gulbu Uzel ,Paul E Gray ,Daniel Suan ,Kahn Preece ,Ignatius Chua ,Satoshi Okada ,Shunsuke Chikuma ,Hiroshi Kiyonari ,Timothy I Tree ,Dusan Bogunovic ,Philippe Gros ,Nico Marr ,Cate Speake ,Richard A Oram ,Vivien Béziat ,Jacinta Bustamante ,Laurent Abel ,Bertrand Boisson ,Anne-Sophie Korganow ,Cindy S Ma ,Matthew B Johnson ,Kenji Chamoto ,Stéphanie Boisson-Dupuis ,Tasuku Honjo ,Jean-Laurent Casanova ,Stuart G Tangye

Defective germinal center selection results in persistence of self-reactive B cells from the primary to the secondary repertoire in Primary Antiphospholipid Syndrome

原发性抗磷脂综合征中,生发中心选择缺陷导致自身反应性B细胞从初级B细胞库持续存在于次级B细胞库中。

Yannick Dieudonné # ,Raquel Lorenzetti # ,Julien Rottura ,Iga Janowska ,Quentin Frenger ,Léa Jacquel ,Olivier Vollmer ,Francesco Carbone ,Zhu Chengsong ,Marine Luka ,Sabine Depauw ,Nadège Wadier ,Stéphane Giorgiutti ,Benoît Nespola ,Agathe Herb ,Reinhard Edmund Voll ,Aurélien Guffroy ,Vincent Poindron ,Mickaël Ménager ,Thierry Martin ,Pauline Soulas-Sprauel ,Marta Rizzi ,Anne-Sophie Korganow ,Vincent Gies

Normal B cells express ZAP70 in chronic lymphocytic leukemia: A link between autoimmunity and lymphoproliferation?

正常 B 细胞在慢性淋巴细胞白血病中表达 ZAP70:自身免疫和淋巴细胞增殖之间存在联系?

Dana Ghergus, Mickaël Martin, Anne-Marie Knapp, Fabien Delmotte, Aurélie Joublin-Delavat, Sophie Jung, Jean-Nicolas Schickel, Isabelle Mendel, Arnaud Dupuis, Bernard Drénou, Hervé Ghesquières, Gilles Salles, Lucile Baseggio, Raoul Herbrecht, Anne-Sophie Korganow, Laurent Vallat, Pauline Soulas-Sprau

The histamine analogue clobenpropit modulates IRF7 phosphorylation and interferon production by targeting CXCR4 in systemic lupus erythematosus models

组胺类似物氯苯那敏通过靶向系统性红斑狼疮模型中的 CXCR4 来调节 IRF7 磷酸化和干扰素产生

Nassima Bekaddour, Nikaïa Smith, Birgit Caspar, Severine Grinberg, Stephane Giorgiutti, Vincent Rodeschini, Stephanie Dupuy, Nicolas Leboulanger, Darragh Duffy, Pauline Soulas-Sprauel, Vincent Gies, Anne-Sophie Korganow, Sébastien Nisole, Jean-Philippe Herbeuval

Recommendations for Transitioning Young People with Primary Immunodeficiency Disorders and Autoinflammatory Diseases to Adult Care

关于将患有原发性免疫缺陷疾病和自身炎症性疾病的年轻人过渡到成人护理的建议

Israni, Muskan; Alderson, Eliska; Mahlaoui, Nizar; Obici, Laura; Rossi-Semerano, Linda; Lachmann, Helen; Avramovič, Mojca Zajc; Guffroy, Aurelien; Dalm, Virgil; Rimmer, Rachel; Solis, Leire; Villar, Carlota; Gennery, Andrew R; Skeffington, Stephanie; Nordin, Julia; Warnatz, Klaus; Korganow, Anne-Sophie; Antón, Jordi; Cattalini, Marco; Berg, Stefan; Soler-Palacin, Pere; Campbell, Mari; Burns, Siobhan O

CXCR4: from B-cell development to B cell-mediated diseases

CXCR4:从B细胞发育到B细胞介导的疾病

Giorgiutti, Stéphane; Rottura, Julien; Korganow, Anne-Sophie; Gies, Vincent

Current Transition Practice for Primary Immunodeficiencies and Autoinflammatory Diseases in Europe: a RITA-ERN Survey

欧洲原发性免疫缺陷和自身炎症性疾病的当前过渡实践:RITA-ERN调查

Israni, Muskan; Nicholson, Bethany; Mahlaoui, Nizar; Obici, Laura; Rossi-Semerano, Linda; Lachmann, Helen; Hayward, Georgia; Avramovič, Mojca Zajc; Guffroy, Aurelien; Dalm, Virgil; Rimmer, Rachel; Solis, Leire; Villar, Carlotta; Gennery, Andrew R; Skeffington, Stephanie; Nordin, Julia; Warnatz, Klaus; Korganow, Anne-Sophie; Antón, Jordi; Cattalini, Marco; Amin, Tania; Berg, Stephan; Soler-Palacin, Pere; Burns, Siobhan O; Campbell, Mari