日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

American College of Rheumatology Guidance Statement for Diagnosis and Management of VEXAS Developed by the International VEXAS Working Group Expert Panel

美国风湿病学会关于VEXAS诊断和治疗的指导声明,由国际VEXAS工作组专家组制定

Mekinian, Arsene; Georgin-Lavialle, Sophie; Ferrada, Marcela A; Savic, Sinisa; Koster, Matthew J; Kosmider, Olivier; Comont, Thibault; Heiblig, Mael; Arostegui, Juan I; Bosco, Annmarie; Bourguiba, Rim; Calvo, Katherine R; Cargo, Catherine; Cattaneo, Chiara; Chasset, François; Coelho, Henrique; Campochiaro, Corrado; Crisafulli, Francesca; Ducharme-Benard, Stephanie; Faria, Raquel; Franceschini, Franco; Frassi, Micol; Groarke, Emma M; Gurnari, Carmelo; Hakobyan, Yervand; Jamilloux, Yvan; Jurcut, Ciprian; Kirino, Yohei; Kulasekararaj, Austin; Kunimoto, Hiroyoshi; Madigan, Lauren M; Mann, Heřman F; Marvisi, Chiara; Milchert, Marcin; Morais, Sara; Sockel, Katja; Muratore, Francesco; Nakajima, Hideaki; Patnaik, Mrinal M; Regadas, Luísa; Robin, Marie; Rutgers, Abraham; Salvarani, Carlo; Sammel, Anthony M; Seebach, Joerg; Sujobert, Pierre; Tomelleri, Alessandro; Urbanski, Geoffrey; Vandergheynst, Frédéric; Vieira, Romana; Viswanatha, David S; Więsik-Szewczyk, Ewa; Diral, Elisa; Terrier, Benjamin; Patel, Bhavisha A; Fenaux, Pierre; Grayson, Peter C; Beck, David B

PAXIS: A Randomized, Double-Blind, Placebo-Controlled, Dose-Finding Phase 2 Study (Part 1) Followed by an Open-Label Period (Part 2) to Assess the Efficacy and Safety of Pacritinib in Patients with VEXAS Syndrome

PAXIS:一项随机、双盲、安慰剂对照、剂量探索性 II 期研究(第一部分)及后续开放标签期(第二部分),旨在评估帕克替尼治疗 VEXAS 综合征患者的疗效和安全性

Beck, David B; Heiblig, Maël; Savic, Sinisa; Ferrada, Marcela A; Mekinian, Arsène; Chowdhury, Onima; Hammond, Danielle; Weeks, Lachelle D; Gurnari, Carmelo; Kirino, Yohei; Georgin-Lavialle, Sophie; Buckley, Sarah A; Garcha, Raman; Harder, Bryan G; Koster, Matthew J

Do Not Anchor on Vasculitis: Pancreatic Cancer Presenting With Isolated Celiac/Superior Mesenteric Artery Thickening

不要将血管炎作为诊断依据:胰腺癌表现为孤立性腹腔动脉/肠系膜上动脉增厚

Own, Maryam; Koster, Matthew J; Warrington, Kenneth J

Epidemiology of Erdheim-Chester disease in the United States: a SEER-based analysis

美国埃尔德海姆-切斯特病的流行病学:基于SEER数据库的分析

Tessier, Steven; Abeykoon, Jithma P; Ruan, Gordon; Bennani, N Nora; Shah, Mithun V; Rech, Karen L; Ravindran, Aishwarya; Ryu, Jay H; Vassallo, Robert; Koster, Matthew J; Davidge-Pitts, Caroline J; Gruber, Lucinda M; Tobin, W Oliver; Sartori-Valinotti, Julio C; Hilal, Talal; Jiang, Liuyan; Moustafa, Muhammad Alhaj; Ahmed, Asra Z; Bach, Corrie R; Young, Jason R; Goyal, Gaurav; Go, Ronald S

Efficacy of MEK inhibitors in Erdheim-Chester disease: impact of MAPK pathway pathogenic variants

MEK抑制剂在Erdheim-Chester病中的疗效:MAPK通路致病变异的影响

Acosta-Medina, Aldo A; Abeykoon, Jithma P; Zanwar, Saurabh; Ruan, Gordon J; Rech, Karen L; Ravindran, Aishwarya; Bennani, N Nora; Davidge-Pitts, Caroline J; Koster, Matthew J; Ryu, Jay H; Shah, Mithun V; Tobin, W Oliver; Vassallo, Robert; Young, Jason R; Go, Ronald S; Goyal, Gaurav

Cluster analysis reveals the clinical spectrum of Erdheim-Chester disease

聚类分析揭示了埃尔德海姆-切斯特病的临床谱。

Tesi, Michelangelo; Pegoraro, Francesco; Peyronel, Francesco; Emile, Jean-François; Catamerò, Francesco; Koster, Matthew J; Goyal, Gaurav; Collin, Matthew; Milne, Paul; Boussouar, Samia; Cohen-Aubart, Fleur; Papo, Matthias; Amoura, Zahir; Estrada-Veras, Juvianee I; O'Brien, Kevin; Razanamahery, Jerome; Goulabchand, Radjiv; Idbaih, Ahmed; de Menthon, Mathilde; Gensous, Noemie; Aouba, Achille; Ledoult, Emmanuel; Le Scornet, Tanguy; Néel, Antoine; Go, Ronald S; Mazor, Roei D; Campochiaro, Corrado; Dagna, Lorenzo; Diamond, Eli L; Vaglio, Augusto; Haroche, Julien

Distinctive clinical features in biopsy-proven nerve large-arteriole vasculitis and microvasculitis

经活检证实的神经大动脉血管炎和微血管炎的独特临床特征

Soontrapa, Pannathat; Pinto, Marcus V; Shouman, Kamal; Mandrekar, Jay; Engelstad, JaNean K; Aragon Pinto, Catarina; Taylor, Sean; Mauermann, Michelle L; Berini, Sarah E; Bosch, E Peter; Rubin, Devon I; Koster, Matthew J; Weyand, Cornelia M; Warrington, Kenneth J; Klein, Christopher J; Dyck, Peter J; Dyck, P James B

Cardiovascular degeneration in Erdheim-Chester disease: prevalence, burden, and outcomes

Erdheim-Chester病的心血管退行性变:患病率、疾病负担和预后

Tawfiq, Reema K; Spears, Grant M; Young, Jason R; Mahowald, Madeline K; Tobin, W Oliver; Patgunarajah, Ubenthira; Ruan, Gordon J; Yi, Dongni; Zanwar, Saurabh; Rech, Karen; Koster, Matthew J; Acosta-Medina, Aldo A; Gruber, Lucinda; Ravindran, Aishwarya; Shah, Mithun Vinod; Bennani, N Nora; Alhaj Moustafa, Muhamad; Hilal, Talal; Sartori Valinotti, Julio C; Vassallo, Robert; Ryu, Jay H; Davidge-Pitts, Caroline; Dasari, Surendra; Witzig, Thomas E; Go, Ronald S; Goyal, Gaurav; Abeykoon, Jithma P

Vasculitis associated with VEXAS syndrome

与VEXAS综合征相关的血管炎

Sullivan, Megan M; Mead-Harvey, Carolyn; Sartori-Valinotti, Julio C; Kalantari, Kambiz; Kusne, Yael N; Patnaik, Mrinal M; Mangaonkar, Abhishek A; Go, Ronald S; Montes, Daniel; Reichard, Kaaren K; Olteanu, Horatiu; Bois, Melanie C; Hines, Alexander S; Warrington, Kenneth J; Koster, Matthew J

Population-Based Performance of Inflammatory Markers in Giant Cell Arteritis

巨细胞动脉炎中炎症标志物的群体表现

Castillejo Becerra, Clara M; Crowson, Cynthia S; Langenfeld, Hannah E; Tajfirouz, Deena; Chodnicki, Kevin D; Koster, Matthew J; Warrington, Kenneth J; Chen, John J